eMedicine Specialties > Pediatrics: General Medicine > Pulmonology

Goodpasture Syndrome: Multimedia

Author: Rudolph P Valentini, MD, Director of Dialysis Services, Associate Professor, Department of Pediatrics, Division of Pediatric Nephrology, Wayne State University and Children's Hospital of Michigan
Contributor Information and Disclosures

Updated: Mar 4, 2009

Multimedia

This image of direct immunofluorescence shows smo...Media file 1: This image of direct immunofluorescence shows smooth linear staining of the basement membrane secondary to immunoglobulin G deposition. This confirms the diagnosis of Goodpasture syndrome. Image courtesy of K. Orr, MD.
This image of direct immunofluorescence shows smo...

This image of direct immunofluorescence shows smooth linear staining of the basement membrane secondary to immunoglobulin G deposition. This confirms the diagnosis of Goodpasture syndrome. Image courtesy of K. Orr, MD.

More on Goodpasture Syndrome

Overview: Goodpasture Syndrome
Differential Diagnoses & Workup: Goodpasture Syndrome
Treatment & Medication: Goodpasture Syndrome
Follow-up: Goodpasture Syndrome
Multimedia: Goodpasture Syndrome
References

References

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  2. Lerner RA, Glassock RJ, Dixon FJ. The role of anti-glomerular basement membrane antibody in the pathogenesis of human glomerulonephritis. J Exp Med. Dec 1 1967;126(6):989-1004. [Medline][Full Text].

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  4. Miklovicova D, Cornelissen M, Cransberg K, Groothoff JW, Dedik L, Schroder CH. Etiology and epidemiology of end-stage renal disease in Dutch children 1987-2001. Pediatr Nephrol. Aug 2005;20(8):1136-42. [Medline].

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Further Reading

Keywords

Goodpasture syndrome, GS, anti–glomerular basement membrane disease, anti-GBM disease, Goodpasture disease, Goodpasture's disease, pulmonary renal syndrome, Goodpasture's syndrome, Wegener granulomatosis, Wegener's granulomatosis, glomerulonephritis, pulmonary hemorrhage, anti-GBM antibody formation, pulmonary renal syndrome of alveolar hemorrhage, small vessel vasculitis, glomerulonephritis, cigarette smoking, end-stage renal disease, ESRD, systemic lupus erythematosus, SLE, Henoch-Schönlein purpura, HSP, respiratory failure, proteinuria, nephrotic syndrome

Contributor Information and Disclosures

Author

Rudolph P Valentini, MD, Director of Dialysis Services, Associate Professor, Department of Pediatrics, Division of Pediatric Nephrology, Wayne State University and Children's Hospital of Michigan
Rudolph P Valentini, MD is a member of the following medical societies: American Academy of Pediatrics, American Society of Nephrology, and American Society of Pediatric Nephrology
Disclosure: Nothing to disclose.

Medical Editor

Girish D Sharma, MD, Associate Professor, Department of Pediatrics, Rush University Medical Center, Rush Children's Hospital; Director of Pediatric Pulmonary Section and Rush Cystic Fibrosis Center
Girish D Sharma, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Chest Physicians, American Thoracic Society, and Royal College of Physicians of Ireland
Disclosure: Nothing to disclose.

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from financial planner; Avanir Pharma Stock Investment from financial planner ; WebMD Salary and stock Employment and investment from financial planner

Managing Editor

Charles Callahan, DO, Professor, Deputy Chief of Clinical Services, Walter Reed Army Medical Center
Charles Callahan, DO is a member of the following medical societies: American Academy of Pediatrics, American College of Chest Physicians, American College of Osteopathic Pediatricians, American Thoracic Society, Association of Military Surgeons of the US, and Christian Medical & Dental Society
Disclosure: Nothing to disclose.

CME Editor

Mary E Cataletto, MD, Associate Director, Division of Pediatric Pulmonology, Winthrop University Hospital; Professor of Clinical Pediatrics, State University of New York at Stony Brook; Director of Children's Sleep Services, Winthrop University Hospital
Mary E Cataletto, MD is a member of the following medical societies: American Academy of Pediatrics and American College of Chest Physicians
Disclosure: Shering Plough Pharmaceuticals Honoraria Consulting

Chief Editor

Michael R Bye, MD, Professor of Clinical Pediatrics, Division of Pulmonary Medicine, Columbia University College of Physicians and Surgeons; Attending Physician, Pediatric Pulmonary Medicine, Morgan Stanley Children's Hospital of New York Presbyterian, Columbia University Medical Center
Michael R Bye, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Chest Physicians, and American Thoracic Society
Disclosure: Merck Honoraria Speaking and teaching

 
 
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