eMedicine Specialties > Pediatrics: General Medicine > Pulmonology

Pulmonary Hypoplasia: Multimedia

Author: Terry Chin, MD, PhD, Associate Professor of Pediatrics, Pediatric Allergy/Immunology/Pulmonology, Department of Pediatrics, University of California Irvine School of Medicine; Associate Director, Miller Children's Hospital at Long Beach Memorial Medical Center
Coauthor(s): Girija Natarajan, MD, Assistant Professor, Division of Neonatology, Children's Hospital of Michigan & Wayne State University; Ibrahim Abdulhamid, MD, Assistant Professor of Pediatrics, Wayne State University; Director of Pediatric Pulmonary Medicine, Clinical Director of Pediatric Sleep Laboratory, Children's Hospital of Michigan
Contributor Information and Disclosures

Updated: Mar 5, 2009

Multimedia

Chest radiograph of a newborn with primary pulmon...Media file 1: Chest radiograph of a newborn with primary pulmonary hypoplasia of the right lung showing shift of the mediastinum to the right hemithorax.
Chest radiograph of a newborn with primary pulmon...

Chest radiograph of a newborn with primary pulmonary hypoplasia of the right lung showing shift of the mediastinum to the right hemithorax.

CT scan of the same patient as in Media file 1 sh...Media file 2: CT scan of the same patient as in Media file 1 showing absence of the right lung. Note branching of the left lower lobe bronchus (horizontal arrow) and absence of airways in the right side (vertical arrow).
CT scan of the same patient as in Media file 1 sh...

CT scan of the same patient as in Media file 1 showing absence of the right lung. Note branching of the left lower lobe bronchus (horizontal arrow) and absence of airways in the right side (vertical arrow).

A posteroanterior radiograph of a 3-month-old inf...Media file 3: A posteroanterior radiograph of a 3-month-old infant with primary pulmonary hypoplasia of the right lung.
A posteroanterior radiograph of a 3-month-old inf...

A posteroanterior radiograph of a 3-month-old infant with primary pulmonary hypoplasia of the right lung.

Lateral view of the same patient as in Media file...Media file 4: Lateral view of the same patient as in Media file 3 showing one dome of the diaphragm.
Lateral view of the same patient as in Media file...

Lateral view of the same patient as in Media file 3 showing one dome of the diaphragm.

Bronchogram of the same patient as in Media file ...Media file 5: Bronchogram of the same patient as in Media file 3 showing absence of the airways in the right side and presence of the left main bronchus and its branches.
Bronchogram of the same patient as in Media file ...

Bronchogram of the same patient as in Media file 3 showing absence of the airways in the right side and presence of the left main bronchus and its branches.

A chest radiograph of a 14-year-old child with pr...Media file 6: A chest radiograph of a 14-year-old child with primary pulmonary hypoplasia of the right side causing secondary scoliosis.
A chest radiograph of a 14-year-old child with pr...

A chest radiograph of a 14-year-old child with primary pulmonary hypoplasia of the right side causing secondary scoliosis.

A chest radiograph of a newborn with achondroplas...Media file 7: A chest radiograph of a newborn with achondroplasia and small chest causing hypoplasia of both lungs.
A chest radiograph of a newborn with achondroplas...

A chest radiograph of a newborn with achondroplasia and small chest causing hypoplasia of both lungs.

A chest radiograph of a newborn with diaphragmati...Media file 8: A chest radiograph of a newborn with diaphragmatic hernia in the right hemithorax shortly after birth.
A chest radiograph of a newborn with diaphragmati...

A chest radiograph of a newborn with diaphragmatic hernia in the right hemithorax shortly after birth.

CT scan of the same child as in Media file 8 show...Media file 9: CT scan of the same child as in Media file 8 showing the presence of abdominal contents in the right hemithorax. Note the presence of the left lower bronchus and its main branches (horizontal arrow) and absence of the right lower lobe bronchus. The liver in the right hemithorax is indicated by the upper arrow.
CT scan of the same child as in Media file 8 show...

CT scan of the same child as in Media file 8 showing the presence of abdominal contents in the right hemithorax. Note the presence of the left lower bronchus and its main branches (horizontal arrow) and absence of the right lower lobe bronchus. The liver in the right hemithorax is indicated by the upper arrow.

A chest radiograph of a 10-month-old child after ...Media file 10: A chest radiograph of a 10-month-old child after repair of a right diaphragmatic hernia showing loss of lung volume in the right hemithorax.
A chest radiograph of a 10-month-old child after ...

A chest radiograph of a 10-month-old child after repair of a right diaphragmatic hernia showing loss of lung volume in the right hemithorax.

MRI of the same patient in Media file 10 showing ...Media file 11: MRI of the same patient in Media file 10 showing loss of right lung volume and smaller right pulmonary artery than the left pulmonary artery (arrow).
MRI of the same patient in Media file 10 showing ...

MRI of the same patient in Media file 10 showing loss of right lung volume and smaller right pulmonary artery than the left pulmonary artery (arrow).

More on Pulmonary Hypoplasia

Overview: Pulmonary Hypoplasia
Differential Diagnoses & Workup: Pulmonary Hypoplasia
Treatment & Medication: Pulmonary Hypoplasia
Follow-up: Pulmonary Hypoplasia
Multimedia: Pulmonary Hypoplasia
References

References

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Further Reading

Keywords

pulmonary hypoplasia, pulmonary aplasia, bronchopulmonary dysplasia, BPD, treatment, diagnosis, underdevelopment of the lung, hypoplastic lung, carina, congenital diaphragmatic hernia, cystic adenomatoid malformation, CAM, prolonged rupture of membranes, fetal renal dysplasias, lung hypoplasia, oligohydramnios, hydrops fetalis, respiratory distress, apnea, ventilatory support, pneumothorax, arthrogryposis, Potter facies, hypertelorism, epicanthus, retrognathia, depressed nasal bridge, abdominal masses, tracheoesophageal fistula, imperforate anus, communicating bronchopulmonary foregut malformation, pleural effusion, asphyxiating thoracic dystrophy, achondroplasia, thanatophoric dwarfism, osteogenesis imperfecta, thoracic neuroblastoma, hydrothorax, urinary tract obstruction, renal dysplasia, tetralogy of Fallot

Contributor Information and Disclosures

Author

Terry Chin, MD, PhD, Associate Professor of Pediatrics, Pediatric Allergy/Immunology/Pulmonology, Department of Pediatrics, University of California Irvine School of Medicine; Associate Director, Miller Children's Hospital at Long Beach Memorial Medical Center
Terry Chin, MD, PhD is a member of the following medical societies: American Academy of Allergy Asthma and Immunology, American Association of Immunologists, American College of Allergy, Asthma and Immunology, American College of Chest Physicians, American Thoracic Society, California Thoracic Society, Clinical Immunology Society, and Western Society for Pediatric Research
Disclosure: Nothing to disclose.

Coauthor(s)

Girija Natarajan, MD, Assistant Professor, Division of Neonatology, Children's Hospital of Michigan & Wayne State University
Girija Natarajan, MD is a member of the following medical societies: American Academy of Pediatrics
Disclosure: Nothing to disclose.

Ibrahim Abdulhamid, MD, Assistant Professor of Pediatrics, Wayne State University; Director of Pediatric Pulmonary Medicine, Clinical Director of Pediatric Sleep Laboratory, Children's Hospital of Michigan
Ibrahim Abdulhamid, MD is a member of the following medical societies: American Academy of Pediatrics, American Academy of Sleep Medicine, and American Thoracic Society
Disclosure: Nothing to disclose.

Medical Editor

Susanna A McColley, MD, Director of Cystic Fibrosis Center; Head, Division of Pulmonary Medicine; Associate Professor, Department of Pediatrics, Children's Memorial Medical Center of Chicago, Northwestern University
Susanna A McColley, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Chest Physicians, American Sleep Disorders Association, and American Thoracic Society
Disclosure: Genentech Honoraria Speaking and teaching; Genentech Consulting fee Consulting; Novartis Consulting fee Consulting; Altus Consulting fee Consulting; Axcan Scandi Consulting fee Consulting; Boston Scientific Consulting fee Consulting

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from financial planner; Avanir Pharma Stock Investment from financial planner ; WebMD Salary and stock Employment and investment from financial planner

Managing Editor

Heidi Connolly, MD, Associate Professor of Pediatrics and Psychiatry, University of Rochester; Director, Pediatric Sleep Medicine Services, Strong Sleep Disorders Center
Heidi Connolly, MD is a member of the following medical societies: American Academy of Pediatrics, American Thoracic Society, and Society of Critical Care Medicine
Disclosure: Nothing to disclose.

CME Editor

Mary E Cataletto, MD, Associate Director, Division of Pediatric Pulmonology, Winthrop University Hospital; Professor of Clinical Pediatrics, State University of New York at Stony Brook; Director of Children's Sleep Services, Winthrop University Hospital
Mary E Cataletto, MD is a member of the following medical societies: American Academy of Pediatrics and American College of Chest Physicians
Disclosure: Shering Plough Pharmaceuticals Honoraria Consulting

Chief Editor

Michael R Bye, MD, Professor of Clinical Pediatrics, Division of Pulmonary Medicine, Columbia University College of Physicians and Surgeons; Attending Physician, Pediatric Pulmonary Medicine, Morgan Stanley Children's Hospital of New York Presbyterian, Columbia University Medical Center
Michael R Bye, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Chest Physicians, and American Thoracic Society
Disclosure: Merck Honoraria Speaking and teaching

 
 
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