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Hypomelanosis of Ito Treatment & Management

  • Author: Manuel Valdebran, MD; Chief Editor: Dirk M Elston, MD  more...
Updated: Apr 18, 2016

Medical Care

No treatment is administered for the cutaneous findings of hypomelanosis of Ito. Cover-up makeup can be used if the patient desires it.

Associated diseases, including the following, require appropriate specialty care:

  • Seizures
  • Mental retardation
  • Hearing abnormalities
  • Tooth deformities
  • Visual problems
  • Orthopedic problems

Diagnosis is important to guide genetic counseling.


Surgical Care

No surgical treatment is required for the cutaneous problems. Consult a surgeon in regard to the associated surgical problems, as the physical examination findings indicate.



Consult a genetic counselor. Consult a neurologist, psychiatrist, orthopedic specialist, dentist, or ophthalmologist, as the features of the history and physical examination indicate.



No limitations on activity are required.



Complications may occur as a result of associated abnormalities.



Genetics counseling may aid in the prevention of hypomelanosis of Ito.


Long-Term Monitoring

Routine outpatient care is sufficient, except when associated abnormalities require additional care.

Contributor Information and Disclosures

Manuel Valdebran, MD Visiting Dermatopathology Fellow, University of California, San Francisco, School of Medicine

Manuel Valdebran, MD is a member of the following medical societies: International Dermoscopy Society, Medical Dermatology Society, Society for Pediatric Dermatology

Disclosure: Nothing to disclose.

Specialty Editor Board

Michael J Wells, MD, FAAD Associate Professor, Department of Dermatology, Texas Tech University Health Sciences Center, Paul L Foster School of Medicine

Michael J Wells, MD, FAAD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, Texas Medical Association

Disclosure: Nothing to disclose.

Christen M Mowad, MD Professor, Department of Dermatology, Geisinger Medical Center

Christen M Mowad, MD is a member of the following medical societies: Alpha Omega Alpha, Noah Worcester Dermatological Society, Pennsylvania Academy of Dermatology, American Academy of Dermatology, Phi Beta Kappa

Disclosure: Nothing to disclose.

Chief Editor

Dirk M Elston, MD Professor and Chairman, Department of Dermatology and Dermatologic Surgery, Medical University of South Carolina College of Medicine

Dirk M Elston, MD is a member of the following medical societies: American Academy of Dermatology

Disclosure: Nothing to disclose.

Additional Contributors

John Louis Ratz, MD, MBA Private Practice Dermatologist, Mohs Surgeon, Tampa, Florida

John Louis Ratz, MD, MBA is a member of the following medical societies: American Academy of Dermatology, American College of Mohs Surgery, American College of Physicians, American Society for Dermatologic Surgery, American Society for Laser Medicine and Surgery, International Society for Dermatologic Surgery, Southern Medical Association

Disclosure: Nothing to disclose.

Sungnack Lee, MD Vice President of Medical Affairs, Professor, Department of Dermatology, Ajou University School of Medicine, Korea

Sungnack Lee, MD is a member of the following medical societies: American Academy of Dermatology

Disclosure: Nothing to disclose.

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Hypomelanosis of Ito on the arm.
Hypomelanosis of Ito highlighted with a Wood lamp.
Hypomelanosis of Ito on the torso.
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