Congenital Patterned Leukodermas Treatment & Management
- Author: Raymond E Boissy, PhD; Chief Editor: William D James, MD more...
Medical Care
- Limited medical treatment is available for abnormalities of the skin, hair, eyes, or ears that result from a paucity or absence of melanocytes. Surgical skin-grafting techniques have been developed, with variable success in establishing pigmentation. Camouflaging involved areas with skin stains or sunless self-tanning agents may be helpful to some patients. The use of sunscreens and clothing is recommended to protect against ultraviolet light–induced skin damage.
- Surgery may be necessary to correct extensive craniofacial defects in patients with Waardenburg or Apert syndromes.
- Colostomy may be necessary in patients with Hirschsprung syndrome and aganglionic megacolon.
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