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Congenital Patterned Leukodermas Treatment & Management

  • Author: Raymond E Boissy, PhD; Chief Editor: William D James, MD  more...
Updated: Aug 11, 2014

Medical Care

See the list below:

  • Limited medical treatment is available for abnormalities of the skin, hair, eyes, or ears that result from a paucity or absence of melanocytes. Surgical skin-grafting techniques have been developed, with variable success in establishing pigmentation. Camouflaging involved areas with skin stains or sunless self-tanning agents may be helpful to some patients. The use of sunscreens and clothing is recommended to protect against ultraviolet light–induced skin damage.
  • Surgery may be necessary to correct extensive craniofacial defects in patients with Waardenburg or Apert syndromes.
  • Colostomy may be necessary in patients with Hirschsprung syndrome and aganglionic megacolon.
Contributor Information and Disclosures

Raymond E Boissy, PhD Director of Basic Science Research, Professor, Departments of Dermatology and Cell Biology, University of Cincinnati College of Medicine

Raymond E Boissy, PhD is a member of the following medical societies: Sigma Xi

Disclosure: Nothing to disclose.


Steven Hoath, MD Director of Skin Sciences Institute, Professor of Pediatrics, Department of Pediatrics, University of Cincinnati College of Medicine

Disclosure: Nothing to disclose.

Specialty Editor Board

Michael J Wells, MD, FAAD Associate Professor, Department of Dermatology, Texas Tech University Health Sciences Center, Paul L Foster School of Medicine

Michael J Wells, MD, FAAD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, Texas Medical Association

Disclosure: Nothing to disclose.

Van Perry, MD Assistant Professor, Department of Medicine, Division of Dermatology, University of Texas School of Medicine at San Antonio

Van Perry, MD is a member of the following medical societies: American Academy of Dermatology

Disclosure: Nothing to disclose.

Chief Editor

William D James, MD Paul R Gross Professor of Dermatology, Vice-Chairman, Residency Program Director, Department of Dermatology, University of Pennsylvania School of Medicine

William D James, MD is a member of the following medical societies: American Academy of Dermatology, Society for Investigative Dermatology

Disclosure: Nothing to disclose.

Additional Contributors

Kathryn Schwarzenberger, MD Associate Professor of Medicine, Division of Dermatology, University of Vermont College of Medicine; Consulting Staff, Division of Dermatology, Fletcher Allen Health Care

Kathryn Schwarzenberger, MD is a member of the following medical societies: Women's Dermatologic Society, American Contact Dermatitis Society, Medical Dermatology Society, Dermatology Foundation, Alpha Omega Alpha, American Academy of Dermatology

Disclosure: Nothing to disclose.

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