Cutis Laxa (Elastolysis) Treatment & Management
- Author: Daniel J Hogan, MD; Chief Editor: Dirk M Elston, MD more...
No treatment exists to prevent disease progression, although dapsone can be used acutely to control swelling in persons with acquired cutis laxa (elastolysis), consistent with the suspected role of neutrophil elastase. Penicillamine and doxycycline are ineffective.
Cutis Laxa Internationale is an international support group for patients with cutis laxa (elastolysis).
Surgical correction of redundant skin folds, prolapses, or hernias may be undertaken. However, surgery often produces only temporary benefit.
Botulinum toxin injections are being considered for improving the aged appearance and facial defects seen in persons with cutis laxa (elastolysis).
Consult a dermatologist for evaluation of the underlying cause of cutis laxa (elastolysis).
Consult an internal medicine specialist for evaluation of the underlying cause of cutis laxa (elastolysis) and internal organ involvement.
Cutis laxa (elastolysis) increases the risk for aortic aneurysm; therefore, regular cardiac monitoring is recommended to avert a potentially fatal aortic rupture.
Affected individuals may require a consultation with a pulmonologist.
Consultation with a geneticist is suggested, particularly for patients presenting in childhood.
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