Cutis Marmorata Telangiectatica Congenita Follow-up

  • Author: Robert A Schwartz, MD, MPH; Chief Editor: William D James, MD   more...
 
Updated: May 6, 2011
 

Complications

Hemangiomas and lymphangiomas have been seen in association with cutis marmorata telangiectatica congenita. Diffuse dermal angiomatosis may also arise in cutis marmorata telangiectatica congenita.[24] The former is a variant of reactive angioendotheliomatosis, often evident clinically as painful, violaceous, nonhealing erosions or ulcers. It is characterized histologically by diffuse endothelial cell hyperplasia within the reticular dermis rather than the intravascular proliferation typical of reactive angiomatosis.

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Prognosis

The prognosis for cutis marmorata telangiectatica congenita (CMTC) is good. Skin lesions usually improve, especially during the patient's first 2 years of life. This phenomenon is attributed to skin maturation. Macrocephaly cutis marmorata telangiectatica congenita may improve in adolescence and later life.[25]

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Contributor Information and Disclosures
Author

Robert A Schwartz, MD, MPH  Professor and Head, Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, University of Medicine and Dentistry of New Jersey-New Jersey Medical School

Robert A Schwartz, MD, MPH is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American College of Physicians, and Sigma Xi

Disclosure: Nothing to disclose.

Coauthor(s)

Anna Zalewska, MD, PhD  Professor of Dermatology and Venereology, Psychodermatology Department, Chair of Clinical Immunology and Microbiology, Medical University of Lodz, Poland

Disclosure: Nothing to disclose.

Meltem Onder, MD  Professor of Dermatology, Director of Contact Dermatitis and Behcet's Disease Clinic, Gazi University School of Medicine

Meltem Onder, MD is a member of the following medical societies: American Academy of Dermatology and International Society of Dermatology

Disclosure: Nothing to disclose.

Emel Erdal, MD  Associate Professor of Dermatology, Mesa Hospital, Turkey

Disclosure: Nothing to disclose.

Specialty Editor Board

Noah S Scheinfeld, MD, JD, FAAD  Assistant Clinical Professor, Department of Dermatology, Columbia University College of Physicians and Surgeons; Consulting Staff, Department of Dermatology, St Luke's Roosevelt Hospital Center, Beth Israel Medical Center, and New York Eye and Ear Infirmary; Private Practice

Noah S Scheinfeld, MD, JD, FAAD is a member of the following medical societies: American Academy of Dermatology

Disclosure: Optigenex Consulting fee Independent contractor

Michael J Wells, MD  Associate Professor, Department of Dermatology, Texas Tech University Health Sciences Center

Michael J Wells, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, and Texas Medical Association

Disclosure: Nothing to disclose.

Julia R Nunley, MD  Professor, Program Director, Dermatology Residency, Department of Dermatology, Virginia Commonwealth University Medical Center

Julia R Nunley, MD is a member of the following medical societies: American Academy of Dermatology, American College of Physicians, American Society of Nephrology, International Society of Nephrology, Medical Dermatology Society, Medical Society of Virginia, National Kidney Foundation, Phi Beta Kappa, and Women's Dermatologic Society

Disclosure: Novartis Grant/research funds Consulting; Biolex Grant/research funds sub-investigator

Glen H Crawford, MD  Assistant Clinical Professor, Department of Dermatology, University of Pennsylvania School of Medicine; Chief, Division of Dermatology, The Pennsylvania Hospital

Glen H Crawford, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, Phi Beta Kappa, and Society of USAF Flight Surgeons

Disclosure: Nothing to disclose.

Chief Editor

William D James, MD  Paul R Gross Professor of Dermatology, University of Pennsylvania School of Medicine; Vice-Chair, Program Director, Department of Dermatology, University of Pennsylvania Health System

William D James, MD is a member of the following medical societies: American Academy of Dermatology and Society for Investigative Dermatology

Disclosure: Elsevier Royalty Other

References

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Reticular skin lesions are observed on the right arm of a 7-year-old girl.
The reticulated mottling is observed on the skin of the back of a newborn.
Similar lesions are seen on the abdominal skin of the patient in Image 2.
 
 
 
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