Tufted Angioma

Updated: Aug 17, 2015
  • Author: Mitchel P Goldman, MD; Chief Editor: Dirk M Elston, MD  more...
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Overview

Background

Tufted angiomas are rare vascular tumors most commonly localized to the skin and subcutaneous tissues and characterized by slow angiomatous proliferation. Although adult-onset cases have been described, tufted angiomas occur far more frequently in children. Tufted angiomas have a benign course, with no reported cases of aggressive behavior or metastases. However, tufted angiomas seldom self-involute. [1]

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Epidemiology

Frequency

United States

The incidence of tufted angiomas is low. As of the year 2000, only 54 cases are described in the English-language literature in the United States and Europe.

International

The international incidence of tufted angioma is also low. However, after Nakagawa identified the condition, angioblastoma, in 1949, more cases have been described in Japan. By 2000, 157 cases had been reported. [2, 3, 4]

Race

No racial predilection is recognized for tufted angioma.

Sex

The prevalence of tufted angioma is equal in both sexes.

Age

Most series report that 60-70% of tufted angiomas develop before the patient is aged 5 years, and 25% of tumors appear by the time the patient is aged 1 year. The Japanese-language literature, however, reports that more than 50% of tufted angiomas appear in the patient's first year of life. Of these patients, 15% are believed to have had a blemish in the area where the tufted angioma later developed; this observation suggests a congenital mode of presentation.

Less than 10% of tufted angiomas develop in individuals older than 50 years, and tumors in persons older than 60-80 years are rare. [1, 4] One 81-year-old patient with a tufted angioma of 2 years' duration is reported in the French-language literature, and a case has been described in an 84-year-old man in Japan. [5, 6]

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