eMedicine Specialties > Dermatology > Pediatric Diseases
Dermatopathia Pigmentosa Reticularis: Treatment & Medication
Updated: Feb 1, 2008
- Overview
- Differential Diagnoses & Workup
- Treatment & Medication
- Follow-up
Treatment
Medical Care
No specific treatment exists for this disorder, except for symptomatic management of some of the associated conditions, such as palmoplantar hyperkeratosis. For hyperkeratosis, topical retinoic acids and keratolytics may be beneficial. Nonscarring blisters are generally transient and self-healing. Cold compress may suffice.
Activity
Advise patients to avoid sun exposure, which may trigger blister formation.
More on Dermatopathia Pigmentosa Reticularis |
| Overview: Dermatopathia Pigmentosa Reticularis |
| Differential Diagnoses & Workup: Dermatopathia Pigmentosa Reticularis |
Treatment & Medication: Dermatopathia Pigmentosa Reticularis |
| Follow-up: Dermatopathia Pigmentosa Reticularis |
| References |
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References
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Dereure O. [Naegeli-Franceschetti-Jadassohn syndrome and dermatopathia pigmentosa reticularis. Two allelic ectodermal dysplasias related to mutations of dominant gene coding for keratin 14]. Ann Dermatol Venereol. Jun-Jul 2007;134(6-7):595. [Medline].
Heimer WL 2nd, Brauner G, James WD. Dermatopathia pigmentosa reticularis: a report of a family demonstrating autosomal dominant inheritance. J Am Acad Dermatol. Feb 1992;26(2 Pt 2):298-301. [Medline].
Itin PH, Lautenschlager S, Meyer R, Mevorah B, Rufli T. Natural history of the Naegeli-Franceschetti-Jadassohn syndrome and further delineation of its clinical manifestations. J Am Acad Dermatol. Jun 1993;28(6):942-50. [Medline].
Sprecher E, Itin P, Whittock NV, McGrath JA, Meyer R, DiGiovanna JJ, et al. Refined mapping of Naegeli-Franceschetti- Jadassohn syndrome to a 6 cM interval on chromosome 17q11.2-q21 and investigation of candidate genes. J Invest Dermatol. Sep 2002;119(3):692-8. [Medline].
Whittock NV, Coleman CM, McLean WH, Ashton GH, Acland KM, Eady RA, et al. The gene for Naegeli-Franceschetti-Jadassohn syndrome maps to 17q21. J Invest Dermatol. Oct 2000;115(4):694-8. [Medline].
Brar BK, Mehta V, Kubba A. Dermatopathia pigmentosa reticularis. Pediatr Dermatol. Sep-Oct 2007;24(5):566-70. [Medline].
Lugassy J, Itin P, Ishida-Yamamoto A, Holland K, Huson S, Geiger D, et al. Naegeli-Franceschetti-Jadassohn syndrome and dermatopathia pigmentosa reticularis: two allelic ectodermal dysplasias caused by dominant mutations in KRT14. Am J Hum Genet. Oct 2006;79(4):724-30. [Medline].
Fulk CS. Primary disorders of hyperpigmentation. J Am Acad Dermatol. Jan 1984;10(1):1-16. [Medline].
Maso MJ, Schwartz RA, Lambert WC. Dermatopathia pigmentosa reticularis. Arch Dermatol. Jul 1990;126(7):935-9. [Medline].
Rycroft RJ, Calnan CD, Allenby CF. Dermatopathia pigmentosa reticularis. Clin Exp Dermatol. Mar 1977;2(1):39-44. [Medline].
Schnur RE, Heymann WR. Reticulate hyperpigmentation. Semin Cutan Med Surg. Mar 1997;16(1):72-80. [Medline].
van der Lugt L. Dermatopathia pigmentosa reticularis hyperkeratotica et mutilans. Dermatologica. 1970;140(5):294-302. [Medline].
Further Reading
Keywords
DPR, Naegeli-Franceschetti-Jadassohn, NFJ, NFJS
Treatment & Medication: Dermatopathia Pigmentosa Reticularis