eMedicine Specialties > Dermatology > Pediatric Diseases

Epidermal Nevus Syndrome: Multimedia

Author: Robert A Schwartz, MD, MPH, Professor and Head, Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, UMDNJ-New Jersey Medical School
Coauthor(s): Sergiusz Jozwiak, MD, PhD, Head, Professor, Department of Child Neurology, The Children's Memorial Health Institute of Warsaw, Poland
Contributor Information and Disclosures

Updated: Jul 2, 2009

Multimedia

Characteristic epidermal nevus in the axillary fo...
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Media file 1: Characteristic epidermal nevus in the axillary fossa of a child with Jadassohn nevus phakomatosis (same patient as in Media Files 2-3).
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Characteristic epidermal nevus in the axillary fo...

Characteristic epidermal nevus in the axillary fossa of a child with Jadassohn nevus phakomatosis (same patient as in Media Files 2-3).

An extensive plaque is observed over most of the ...
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Media file 2: An extensive plaque is observed over most of the left scapula, neck area, and lumbosacral location (same patient as in Media Files 1 and 3).
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An extensive plaque is observed over most of the ...

An extensive plaque is observed over most of the left scapula, neck area, and lumbosacral location (same patient as in Media Files 1 and 3).

Plaque is evident in the region of the left groin...
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Media file 3: Plaque is evident in the region of the left groin, and it has a unilateral distribution (same patient as in Media Files 1-2).
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Plaque is evident in the region of the left groin...

Plaque is evident in the region of the left groin, and it has a unilateral distribution (same patient as in Media Files 1-2).

Epidermal nevus syndrome, demonstrating extension...
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Media file 4: Epidermal nevus syndrome, demonstrating extension of a plaque distally.
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Epidermal nevus syndrome, demonstrating extension...

Epidermal nevus syndrome, demonstrating extension of a plaque distally.

Extensive unilateral linear epidermal nevi in a 1...
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Media file 5: Extensive unilateral linear epidermal nevi in a 14-year-old girl with Jadassohn nevus phakomatosis. The plaques are elevated; some have verrucous characteristics.
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Extensive unilateral linear epidermal nevi in a 1...

Extensive unilateral linear epidermal nevi in a 14-year-old girl with Jadassohn nevus phakomatosis. The plaques are elevated; some have verrucous characteristics.

An 8-year-old girl with Jadassohn nevus syndrome....
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Media file 6: An 8-year-old girl with Jadassohn nevus syndrome. Note typical plaques in the midline and on the arm and the neck. The plaques are darker and more verrucous on the arm and the neck than on the midline.
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An 8-year-old girl with Jadassohn nevus syndrome....

An 8-year-old girl with Jadassohn nevus syndrome. Note typical plaques in the midline and on the arm and the neck. The plaques are darker and more verrucous on the arm and the neck than on the midline.

More on Epidermal Nevus Syndrome

Overview: Epidermal Nevus Syndrome
Differential Diagnoses & Workup: Epidermal Nevus Syndrome
Treatment & Medication: Epidermal Nevus Syndrome
Follow-up: Epidermal Nevus Syndrome
Multimedia: Epidermal Nevus Syndrome
References
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Further Reading

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Keywords

epidermal nevus syndrome, epidermal nevus, epidermal nevi, EN, Solomon syndrome, linear sebaceous epidermal nevus syndrome, LSN, inflammatory linear verrucous epidermal nevus syndrome, ILVEN, Schimmelpenning syndrome, Schimmelpenning-Feuerstein-Mims syndrome, nevus comedonicus syndrome, NC, proteus syndrome, congential hemidysplasia with ichthyosiform nevus and limb defects, CHILD syndrome, Jadassohn nevus syndrome, nevus unius lateralis syndrome, ENS, linear epidermal nevus, LEN

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Contributor Information and Disclosures

Author

Robert A Schwartz, MD, MPH, Professor and Head, Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, UMDNJ-New Jersey Medical School
Robert A Schwartz, MD, MPH is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American College of Physicians, and Sigma Xi
Disclosure: Nothing to disclose.

Coauthor(s)

Sergiusz Jozwiak, MD, PhD, Head, Professor, Department of Child Neurology, The Children's Memorial Health Institute of Warsaw, Poland
Sergiusz Jozwiak, MD, PhD is a member of the following medical societies: Sigma Xi
Disclosure: Nothing to disclose.

Medical Editor

Mark A Crowe, MD, Assistant Clinical Instructor, Department of Medicine, Division of Dermatology, University of Washington School of Medicine
Mark A Crowe, MD is a member of the following medical societies: American Academy of Dermatology and North American Clinical Dermatologic Society
Disclosure: Nothing to disclose.

Pharmacy Editor

David F Butler, MD, Professor of Dermatology, Texas A&M University College of Medicine; Chair, Department of Dermatology, Director, Dermatology Residency Training Program, Scott and White Clinic, Northside Clinic
David F Butler, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, American Society for Dermatologic Surgery, American Society for MOHS Surgery, Association of Military Dermatologists, and Phi Beta Kappa
Disclosure: Nothing to disclose.

Managing Editor

Van Perry, MD, Assistant Professor, Department of Medicine, Division of Dermatology, University of Texas Health Science Center
Van Perry, MD is a member of the following medical societies: American Academy of Dermatology and American Society for Laser Medicine and Surgery
Disclosure: Nothing to disclose.

CME Editor

Glen H Crawford, MD, Assistant Clinical Professor, Department of Dermatology, University of Pennsylvania School of Medicine; Chief, Division of Dermatology, The Pennsylvania Hospital
Glen H Crawford, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, Phi Beta Kappa, and Society of USAF Flight Surgeons
Disclosure: Nothing to disclose.

Chief Editor

Dirk M Elston, MD, Director, Department of Dermatology, Geisinger Medical Center
Dirk M Elston, MD is a member of the following medical societies: American Academy of Dermatology
Disclosure: Nothing to disclose.

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