eMedicine Specialties > Dermatology > Pediatric Diseases

Naegeli-Franceschetti-Jadassohn Syndrome: Multimedia

Author: Theo Rufli, MD, Professor of Dermatology and Venereology, Chair, Department of Dermatology, University Hospital of Basle, Switzerland
Contributor Information and Disclosures

Updated: Jan 25, 2007

Multimedia

Lack of dermatoglyphics in a patient with Naegeli...Media file 1: Lack of dermatoglyphics in a patient with Naegeli-Franceschetti-Jadassohn syndrome.
Lack of dermatoglyphics in a patient with Naegeli...

Lack of dermatoglyphics in a patient with Naegeli-Franceschetti-Jadassohn syndrome.

Reticulated pigmentation on the trunk in a patien...Media file 2: Reticulated pigmentation on the trunk in a patient with Naegeli-Franceschetti-Jadassohn syndrome.
Reticulated pigmentation on the trunk in a patien...

Reticulated pigmentation on the trunk in a patient with Naegeli-Franceschetti-Jadassohn syndrome.

Periorbital reticulated pigmentation in a patient...Media file 3: Periorbital reticulated pigmentation in a patient with Naegeli-Franceschetti-Jadassohn syndrome.
Periorbital reticulated pigmentation in a patient...

Periorbital reticulated pigmentation in a patient with Naegeli-Franceschetti-Jadassohn syndrome.

Spotty palmoplantar hyperkeratosis in Naegeli-Fra...Media file 4: Spotty palmoplantar hyperkeratosis in Naegeli-Franceschetti-Jadassohn syndrome.
Spotty palmoplantar hyperkeratosis in Naegeli-Fra...

Spotty palmoplantar hyperkeratosis in Naegeli-Franceschetti-Jadassohn syndrome.

Defective denture with yellow spots on the enamel...Media file 5: Defective denture with yellow spots on the enamel in a patient with Naegeli-Franceschetti-Jadassohn syndrome.
Defective denture with yellow spots on the enamel...

Defective denture with yellow spots on the enamel in a patient with Naegeli-Franceschetti-Jadassohn syndrome.

More on Naegeli-Franceschetti-Jadassohn Syndrome

Overview: Naegeli-Franceschetti-Jadassohn Syndrome
Differential Diagnoses & Workup: Naegeli-Franceschetti-Jadassohn Syndrome
Treatment & Medication: Naegeli-Franceschetti-Jadassohn Syndrome
Multimedia: Naegeli-Franceschetti-Jadassohn Syndrome
References

References

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  31. Zinsser F. Atrophia curis reticularis cum pigmentatione, dystrophia et leukoplakia oris. Ikonogr Dermat. 1910;5:219-223.

Further Reading

Keywords

NFJ syndrome, MIM 161000, reticulate pigmentary disorders, ectodermal dysplasia, hyperpigmentation, hypohidrosis, palmoplantar keratoderma

Contributor Information and Disclosures

Author

Theo Rufli, MD, Professor of Dermatology and Venereology, Chair, Department of Dermatology, University Hospital of Basle, Switzerland
Disclosure: Nothing to disclose.

Medical Editor

James Fulton Jr, MD, PhD, Center for Cosmetic Dermatology; Consultant, Vivant Pharmaceuticals, LLC
James Fulton Jr, MD, PhD is a member of the following medical societies: American Academy of Cosmetic Surgery, American Academy of Dermatology, American Society for Laser Medicine and Surgery, Dermatology Foundation, International Society of Cosmetic and Laser Surgeons, and Skin Cancer Foundation
Disclosure: vivant pharmaceuticals Ownership interest Consulting

Pharmacy Editor

David F Butler, MD, Professor of Dermatology, Texas A&M University College of Medicine; Chair, Department of Dermatology, Director, Dermatology Residency Training Program, Scott and White Clinic, Northside Clinic
David F Butler, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, American Society for Dermatologic Surgery, American Society for MOHS Surgery, Association of Military Dermatologists, and Phi Beta Kappa
Disclosure: Nothing to disclose.

Managing Editor

Robert A Schwartz, MD, MPH, Professor and Head, Dermatology, Professor of Pathology, Pediatrics, Medicine, and Preventive Medicine and Community Health, UMDNJ-New Jersey Medical School
Robert A Schwartz, MD, MPH is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American College of Physicians, and Sigma Xi
Disclosure: Nothing to disclose.

CME Editor

Glen H Crawford, MD, Assistant Clinical Professor, Department of Dermatology, University of Pennsylvania School of Medicine; Chief, Division of Dermatology, The Pennsylvania Hospital
Glen H Crawford, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Medical Association, Phi Beta Kappa, and Society of USAF Flight Surgeons
Disclosure: Nothing to disclose.

Chief Editor

Dirk M Elston, MD, Director, Department of Dermatology, Geisinger Medical Center
Dirk M Elston, MD is a member of the following medical societies: American Academy of Dermatology
Disclosure: Nothing to disclose.

 
 
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