eMedicine Specialties > Neurology > Movement and Neurodegenerative Diseases

Neuroacanthocytosis: Follow-up

Author: Eric Dinnerstein, MD, Consulting Staff Neurologist, Maine Neurology
Coauthor(s): Stephen A Berman, MD, PhD, Professor, Department of Internal Medicine, Section of Neurology, Dartmouth Medical School; Chief, Neurology Service, White River Junction Veterans Medical Center; Maritza Arroyo-Muñiz, MD, Associate Program Director, Professor of Neurology, Department of Neurology, University of Puerto Rico
Contributor Information and Disclosures

Updated: Sep 14, 2006

Follow-up

Prognosis

  • Disease progression is poorly understood, and no cure exists.
 


More on Neuroacanthocytosis

Overview: Neuroacanthocytosis
Differential Diagnoses & Workup: Neuroacanthocytosis
Treatment & Medication: Neuroacanthocytosis
Follow-up: Neuroacanthocytosis
References

References

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  3. Brooks DJ, Ibanez V, Playford ED, et al. Presynaptic and postsynaptic striatal dopaminergic function in neuroacanthocytosis: a positron emission tomographic study. Ann Neurol. Aug 1991;30(2):166-71. [Medline].

  4. Critchley EM, Clark DB, Wikler A. Acanthocytosis and neurological disorder without betalipoproteinemia. Arch Neurol. Feb 1968;18(2):134-40. [Medline].

  5. Dubinsky RM, Hallett M, Levey R, Di Chiro G. Regional brain glucose metabolism in neuroacanthocytosis. Neurology. Sep 1989;39(9):1253-5. [Medline].

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Further Reading

Keywords

chorea-acanthocytosis, Levine-Critchley syndrome, acanthocytosis, Bassen-Kornsweig disease, abetalipoproteinemia, familial hypobetalipoproteinemia, lipoprotein disorders, chorea-acanthocytosis McLeod syndrome, MLS, ChAc, McLeod syndrome, Huntington disease–like2, HDL2, pantothenate kinase–associated neurodegeneration, PKAN

Contributor Information and Disclosures

Author

Eric Dinnerstein, MD, Consulting Staff Neurologist, Maine Neurology
Eric Dinnerstein, MD is a member of the following medical societies: American Academy of Neurology and American Medical Association
Disclosure: Nothing to disclose.

Coauthor(s)

Stephen A Berman, MD, PhD, Professor, Department of Internal Medicine, Section of Neurology, Dartmouth Medical School; Chief, Neurology Service, White River Junction Veterans Medical Center
Stephen A Berman, MD, PhD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Neurology, and Phi Beta Kappa
Disclosure: Nothing to disclose.

Maritza Arroyo-Muñiz, MD, Associate Program Director, Professor of Neurology, Department of Neurology, University of Puerto Rico
Maritza Arroyo-Muñiz, MD is a member of the following medical societies: American Academy of Neurology and National Stroke Association
Disclosure: Nothing to disclose.

Medical Editor

Roberta J Seidman, MD, Director of Neuropathology, Clinical Associate Professor, Department of Pathology, Stony Brook University Medical Center
Roberta J Seidman, MD is a member of the following medical societies: American Academy of Neurology, American Association for the Advancement of Science, and American Association of Neuropathologists
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

Nestor Galvez-Jimenez, MD, Program Director of Movement Disorders, Department of Neurology, Division of Medicine, Director of Neurology Residency Training Program, Cleveland Clinic Florida
Nestor Galvez-Jimenez, MD is a member of the following medical societies: American Academy of Neurology, American College of Physicians, and Movement Disorders Society
Disclosure: Nothing to disclose.

CME Editor

Matthew J Baker, MD, Consulting Staff, Collier Neurologic Specialists, Naples Community Hospital
Matthew J Baker, MD is a member of the following medical societies: American Academy of Neurology
Disclosure: Nothing to disclose.

Chief Editor

Nicholas Y Lorenzo, MD, Chief Editor, eMedicine Neurology; Consulting Staff, Neurology Specialists and Consultants
Nicholas Y Lorenzo, MD is a member of the following medical societies: Alpha Omega Alpha and American Academy of Neurology
Disclosure: Nothing to disclose.

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