eMedicine Specialties > Neurology > Movement and Neurodegenerative Diseases

Olivopontocerebellar Atrophy: Follow-up

Author: Christina J Azevedo MD, Staff Physician, Department of Neurology, Dartmouth-Hitchcock Medical Center
Coauthor(s): Stephen A Berman, MD, PhD, Professor, Department of Internal Medicine, Section of Neurology, Dartmouth Medical School; Chief, Neurology Service, White River Junction Veterans Medical Center
Contributor Information and Disclosures

Updated: Feb 12, 2009

Follow-up

Complications

  • Falls are the primary complications in the early stages of olivopontocerebellar atrophy (OPCA).
  • Aspiration pneumonia is more common in later stages of OPCA.

Prognosis

Currently, no effective therapy is available for the neurodegenerative processes that constitute OPCA. Clinically, only supportive care can be given to patients with this progressive disease.

Miscellaneous

Medicolegal Pitfalls

Mental status and expressive abilities generally are preserved early in the disease. In cases that appear to be progressing to severe disability relatively rapidly, clarifying resuscitation status and advanced directives regarding feeding tube, tracheostomy, and aggressive care is advisable while the patient is able to express his or her wishes.

 
Acknowledgments

The authors and editors of eMedicine gratefully acknowledge the contributions of previous authors Kalpana Kari, MD; Syed T Arshad, MD; and Yash Mehndiratta, MD to the development and writing of this article.



More on Olivopontocerebellar Atrophy

Overview: Olivopontocerebellar Atrophy
Differential Diagnoses & Workup: Olivopontocerebellar Atrophy
Treatment & Medication: Olivopontocerebellar Atrophy
Follow-up: Olivopontocerebellar Atrophy
References
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Further Reading

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Keywords

spinocerebellar ataxia, dysarthria, dysphagia, ataxia, olivopontocerebellar atrophy, multiple system atrophy, MSA, autosomal dominant cerebellar atrophy, spinocerebellar atrophy, ADCA, Menzel OPCA, Menzel ataxia, Schut-Haymaker OPCA, Schut-Haymaker ataxia, Dejerine-Thomas ataxia, Holguin ataxia, Wadia-Swami syndrome, Sanger-Brown ataxia, Holmes ataxia, Marie ataxia, Nonne syndrome, ataxia of Holmes, SCA, OPCA

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Contributor Information and Disclosures

Author

Christina J Azevedo MD, Staff Physician, Department of Neurology, Dartmouth-Hitchcock Medical Center
Christina J Azevedo MD is a member of the following medical societies: American Academy of Neurology, American College of Physicians, and Oregon Medical Association
Disclosure: Nothing to disclose.

Coauthor(s)

Stephen A Berman, MD, PhD, Professor, Department of Internal Medicine, Section of Neurology, Dartmouth Medical School; Chief, Neurology Service, White River Junction Veterans Medical Center
Stephen A Berman, MD, PhD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Neurology, and Phi Beta Kappa
Disclosure: Nothing to disclose.

Medical Editor

Howard A Crystal, MD, Professor, Departments of Neurology and Pathology, State University of New York Downstate; Consulting Staff, Department of Neurology, University Hospital and Kings County Hospital Center
Howard A Crystal, MD is a member of the following medical societies: American Academy of Neurology and American Neurological Association
Disclosure: Medivations Honoraria Consulting

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Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

Nestor Galvez-Jimenez, MD, MSc, MHA, Chairman, Department of Neurology, Program Director, Movement Disorders, Department of Neurology, Division of Medicine, Cleveland Clinic Florida
Nestor Galvez-Jimenez, MD, MSc, MHA is a member of the following medical societies: American Academy of Neurology, American College of Physicians, and Movement Disorders Society
Disclosure: Nothing to disclose.

Chief Editor

Selim R Benbadis, MD, Professor, Director of Comprehensive Epilepsy Program, Departments of Neurology and Neurosurgery, University of South Florida School of Medicine, Tampa General Hospital
Selim R Benbadis, MD is a member of the following medical societies: American Academy of Neurology, American Academy of Sleep Medicine, American Clinical Neurophysiology Society, American Epilepsy Society, and American Medical Association
Disclosure: Nothing to disclose.

 
 
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