Focal Muscular Atrophies Differential Diagnoses

  • Author: Sridharan Ramaratnam, MBBS, MD; Chief Editor: Helmi L Lutsep, MD   more...
 
Updated: Apr 30, 2012
 
 

Differential Diagnoses

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Contributor Information and Disclosures
Author

Sridharan Ramaratnam, MBBS, MD  Head, Department of Neurology, Professor of Neurology, Chennai Neurospeciality and Research Institute, India

Sridharan Ramaratnam, MBBS, MD is a member of the following medical societies: American Academy of Neurology, Indian Medical Association, National Academy of Medical Sciences, India, and Royal College of Physicians and Surgeons of Glasgow

Disclosure: Nothing to disclose.

Coauthor(s)

Nicholas Lorenzo, MD  Consulting Staff, Neurology Specialists and Consultants

Nicholas Lorenzo, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Neurology, and American College of Physician Executives

Disclosure: Nothing to disclose.

Lakshmi Narasimhan Ranganathan, MD  Tutor, Institute Of Mental Health, Chennai, India; Senior Civil Assistant Surgeon, Tamil Nadu Medical Services

Disclosure: Nothing to disclose.

Specialty Editor Board

Francisco Talavera, PharmD, PhD  Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Medscape Salary Employment

Agapito S Lorenzo, MD  Laboratory Director, Associate Professor, Departments of Neurology, Creighton University and University of Nebraska Medical Center

Agapito S Lorenzo, MD is a member of the following medical societies: American Academy of Neurology and American Association of Neuromuscular and Electrodiagnostic Medicine

Disclosure: Nothing to disclose.

Chief Editor

Helmi L Lutsep, MD  Professor and Vice Chair, Department of Neurology, Oregon Health and Science University School of Medicine; Associate Director, Oregon Stroke Center

Helmi L Lutsep, MD is a member of the following medical societies: American Academy of Neurology and American Stroke Association

Disclosure: Co-Axia Consulting fee Review panel membership; AGA Medical Consulting fee Review panel membership; Concentric Medical Consulting fee Review panel membership

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A man with neuralgic amyotrophy presenting with wasting of deltoids involving the right side more than the left.
A middle-aged man with (atypical) anterior horn cell disease presenting with wasting of the right quadriceps.
EMG at rest from the right quadriceps muscle of a patient with atypical anterior horn cell disease and isolated atrophy of the right quadriceps; EMG shows spontaneous activity.
EMG on voluntary effort from the right quadriceps muscle of a patient with atypical anterior horn disease and isolated atrophy of the right quadriceps; EMG shows motor unit potentials that exhibit prolonged duration and polyphasia.
EMG on maximal effort from the right quadriceps muscle of a patient with atypical anterior horn disease and isolated atrophy of the right quadriceps; EMG shows an impaired interference pattern.
Clinical photograph of a subject with monomelic amyotrophy showing wasting of left forearm. Note the characteristic feature of oblique atrophy, where a normal brachioradialis dominates the atrophied forearm.
 
 
 
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