Neural Tube Defects Treatment & Management
- Author: George I Jallo, MD; Chief Editor: Amy Kao, MD more...
The newborn with an open NTD should be kept warm and the defect covered with a sterile wet saline dressing. The patient should be positioned in the prone position to prevent pressure on the defect.
The newborn with an open NTD should undergo prompt closure of the defect. The closure involves classic neurosurgical techniques.
Children with hydrocephalus also should have a ventriculoperitoneal shunt placed at the time of myelomeningocele closure.
Patients presenting with symptomatic Chiari malformations (refer to image below) should undergo suboccipital craniotomy and decompression of the posterior fossa and tonsils.
Children with syrinx (see the following images) need a laminectomy and placement of a syringosubarachnoid stent to divert the CSF out of the central canal.
Consultation with the following may prove helpful:
- Physical therapist
Activity is limited by the degree of involvement.
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