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Vein of Galen Malformation Differential Diagnoses

  • Author: Raj D Sheth, MD; Chief Editor: Amy Kao, MD  more...
Updated: Nov 18, 2015
Contributor Information and Disclosures

Raj D Sheth, MD Chief, Division of Pediatric Neurology, Nemours Children's Clinic; Professor of Neurology, Mayo College of Medicine; Professor of Pediatrics, University of Florida College of Medicine

Raj D Sheth, MD is a member of the following medical societies: American Academy of Neurology, American Academy of Pediatrics, American Epilepsy Society, American Neurological Association, Child Neurology Society

Disclosure: Nothing to disclose.

Specialty Editor Board

Francisco Talavera, PharmD, PhD Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Received salary from Medscape for employment. for: Medscape.

Kenneth J Mack, MD, PhD Senior Associate Consultant, Department of Child and Adolescent Neurology, Mayo Clinic

Kenneth J Mack, MD, PhD is a member of the following medical societies: American Academy of Neurology, Child Neurology Society, Phi Beta Kappa, Society for Neuroscience

Disclosure: Nothing to disclose.

Chief Editor

Amy Kao, MD Attending Neurologist, Children's National Medical Center

Amy Kao, MD is a member of the following medical societies: American Academy of Neurology, American Epilepsy Society, Child Neurology Society

Disclosure: Have stock from Cellectar Biosciences; have stock from Varian medical systems; have stock from Express Scripts.

Additional Contributors

Ann M Neumeyer, MD Medical Director, Lurie Center for Autism; Assistant Professor of Neurology, Harvard Medical School; Child Neurologist, Massachusetts General Hospital

Ann M Neumeyer, MD is a member of the following medical societies: American Academy of Neurology, Child Neurology Society, Massachusetts Medical Society

Disclosure: Nothing to disclose.


The authors and editors of Medscape Reference gratefully acknowledge the contributions of previous author, Ernesto Tiznado-Garcia, MD, to the development and writing of this article.

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Cerebral MRI showing large flow void in the central region with enlarged straight sinus.
Coronal MRI of head showing large central vein of Galen malformation with moderate degree of hydrocephalus.
Cranial MRI showing flow void in the sagittal plain and drainage to the straight and transverse sinuses.
Sagittal cerebral MRI with gadolinium showing the relationship of a vein of Galen malformation to the corpus callosum.
MRI venogram showing vein of Galen malformation with draining veins.
Venogram showing the draining vasculature for the vein of Galen malformation.
Skull radiograph showing coils that have been placed during an intravascular embolization of a vein of Galen malformation. Note the ventriculoperitoneal shunt catheter in the anterior head region to relieve hydrocephalus.
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