eMedicine Specialties > Neurology > Pediatric Neurology

Dopamine-Responsive Dystonia: Follow-up

Author: N K Nikhar, MD, MRCP, Assistant Professor, Department of Neurology, George Washington University School of Medicine
Coauthor(s): Haresh Mani, MD,, Associate Medical Director, Pulmonary and Mediastinal Pathology, American International Pathology Laboratories
Contributor Information and Disclosures

Updated: Jul 10, 2009

Follow-up

Further Outpatient Care

  • Regular outpatient follow-up is required for patients with dopamine-responsive dystonia to assess the efficacy of treatment and to adjust the dopamine dose accordingly. Although uncommon, dyskinesias and chorea may develop in treated patients. Monitor patients carefully for these conditions.

Complications

  • Limb contractures can occur in untreated patients.
  • Growth retardation occurs in untreated children.

Prognosis

  • The prognosis for patients with dopamine-responsive dystonia is good with adequate and early treatment.
 


More on Dopamine-Responsive Dystonia

Overview: Dopamine-Responsive Dystonia
Differential Diagnoses & Workup: Dopamine-Responsive Dystonia
Treatment & Medication: Dopamine-Responsive Dystonia
Follow-up: Dopamine-Responsive Dystonia
References
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Further Reading

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Keywords

dopamine-responsive dystonia, hereditary progressive dystonia with diurnal fluctuation, HPD, Segawa's disease, Segawa disease, DRD, dopa-responsive dystonia, inherited dystonia, mild parkinsonian features

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Contributor Information and Disclosures

Author

N K Nikhar, MD, MRCP, Assistant Professor, Department of Neurology, George Washington University School of Medicine
N K Nikhar, MD, MRCP is a member of the following medical societies: American Academy of Neurology
Disclosure: Nothing to disclose.

Coauthor(s)

Haresh Mani, MD,, Associate Medical Director, Pulmonary and Mediastinal Pathology, American International Pathology Laboratories
Disclosure: Nothing to disclose.

Medical Editor

Ann M Neumeyer, MD, Clinic Director, Instructor, Departments of Neurology and Pediatrics, Massachusetts General Hospital, Harvard Medical School
Ann M Neumeyer, MD is a member of the following medical societies: American Academy of Neurology, Child Neurology Society, and Massachusetts Medical Society
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: eMedicine Salary Employment

Managing Editor

Nestor Galvez-Jimenez, MD, MSc, MHA, Chairman, Department of Neurology, Program Director, Movement Disorders, Department of Neurology, Division of Medicine, Cleveland Clinic Florida
Nestor Galvez-Jimenez, MD, MSc, MHA is a member of the following medical societies: American Academy of Neurology, American College of Physicians, and Movement Disorders Society
Disclosure: Nothing to disclose.

Chief Editor

Amy Kao, MD, Assistant Professor, Department of Pediatrics, Division of Pediatric Neurology, Department of Neurology, Oregon Health and Science University; Consulting Staff, Shriners Hospital for Children
Amy Kao, MD is a member of the following medical societies: American Academy of Neurology, American Academy of Pediatrics, American Epilepsy Society, and Child Neurology Society
Disclosure: Nothing to disclose.

 
 
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