eMedicine Specialties > Neurology > Seizures and Epilepsy

Epilepsy in Adults with Mental Retardation: Multimedia

Author: Norberto Alvarez, MD, Assistant Professor, Department of Neurology, Harvard Medical School; Consulting Staff, Department of Neurology, Boston Children's Hospital
Contributor Information and Disclosures

Updated: Jun 19, 2008

Multimedia

A 36-year-old man with Sturge-Weber-Dimitri syndr...
(Enlarge Image)
Media file 1: A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.
[ CLOSE WINDOW ]
A 36-year-old man with Sturge-Weber-Dimitri syndr...

A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.

A 36-year-old man with Sturge-Weber-Dimitri syndr...
(Enlarge Image)
Media file 2: A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.
[ CLOSE WINDOW ]
A 36-year-old man with Sturge-Weber-Dimitri syndr...

A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.

A 36-year-old man with Sturge-Weber-Dimitri syndr...
(Enlarge Image)
Media file 3: A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.
[ CLOSE WINDOW ]
A 36-year-old man with Sturge-Weber-Dimitri syndr...

A 36-year-old man with Sturge-Weber-Dimitri syndrome. Extensive hemangiomas are present on both sides and involve the 3 branches of the trigeminal nerve. He has severe mental retardation, with chronic seizure disorder. CT showed extensive, bilateral gyriform calcifications, which were maximal in the occipital area and in the left frontal lobe. Small amount of calcification is seen in the right frontal lobe. Generalized but mild increase in ventricular size and indications of hemiatrophy are present over the left hemisphere.

More on Epilepsy in Adults with Mental Retardation

Overview: Epilepsy in Adults with Mental Retardation
Differential Diagnoses & Workup: Epilepsy in Adults with Mental Retardation
Treatment & Medication: Epilepsy in Adults with Mental Retardation
Follow-up: Epilepsy in Adults with Mental Retardation
Multimedia: Epilepsy in Adults with Mental Retardation
References
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Further Reading

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Keywords

epilepsy, mental retardation, seizures, Angelman syndrome, autism, cerebral palsy, Down syndrome, epileptic seizures, fragile X syndrome, malformations of cortical development, neurofibromatosis I, Rett syndrome, Sturge-Weber-Dimitri syndrome, tuberous sclerosis, neurocutaneous syndromes

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Contributor Information and Disclosures

Author

Norberto Alvarez, MD, Assistant Professor, Department of Neurology, Harvard Medical School; Consulting Staff, Department of Neurology, Boston Children's Hospital
Norberto Alvarez, MD is a member of the following medical societies: American Academy of Neurology, American Epilepsy Society, and Child Neurology Society
Disclosure: Nothing to disclose.

Medical Editor

Joseph F Hulihan, MD, Vice President, Medical Affairs, Ortho-McNeil Janssen Scientific Affairs, LLC
Joseph F Hulihan, MD is a member of the following medical societies: American Academy of Neurology, American Clinical Neurophysiology Society, American Epilepsy Society, American Headache Society, and American Medical Association
Disclosure: Johnson & Johnson Salary Employment; Johnson & Johnson Stock Employment

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

Jose E Cavazos, MD, PhD, Associate Professor with Tenure, Departments of Neurology, Pharmacology, and Physiology, University of Texas Health Science Center at San Antonio; Co-Director, South Texas Comprehensive Epilepsy Center; Director of the Epilepsy Center, Audie L Murphy Veterans Affairs Medical Center
Jose E Cavazos, MD, PhD is a member of the following medical societies: American Academy of Neurology, American Clinical Neurophysiology Society, American Epilepsy Society, and Society for Neuroscience
Disclosure: Glaxo-SmithKline Honoraria Speaking and teaching; Ortho-McNeil Neurologics Honoraria Speaking and teaching; UCB Pharma Honoraria Speaking and teaching

Chief Editor

Selim R Benbadis, MD, Professor, Director of Comprehensive Epilepsy Program, Departments of Neurology and Neurosurgery, University of South Florida School of Medicine, Tampa General Hospital
Selim R Benbadis, MD is a member of the following medical societies: American Academy of Neurology, American Academy of Sleep Medicine, American Clinical Neurophysiology Society, American Epilepsy Society, and American Medical Association
Disclosure: Nothing to disclose.

 
 
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