Ophthalmologic Manifestations of Pseudoxanthoma Elasticum Follow-up
- Author: Andrew A Dahl, MD; Chief Editor: Hampton Roy Sr, MD more...
Further Outpatient Care
- Hypertension should be monitored.
- Patients should receive regular eye examinations.
Deterrence/Prevention
- Pregnancy, oral contraceptives, and high calcium and phosphorus intake seem to aggravate all manifestations of pseudoxanthoma elasticum.
Complications
- Blindness
- Recurrent GI hemorrhage
- Myocardial infarction
- Subarachnoid hemorrhage
- Cerebrovascular accidents
- Death
Prognosis
- The greatest morbidity in patients with pseudoxanthoma elasticum and angioid streaks is the loss of central vision that occurs in a high percentage of patients in the fifth to sixth decade of life.
Patient Education
- Inform and educate patients about the multisystem potential complications of pseudoxanthoma elasticum.
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