eMedicine Specialties > Ophthalmology > Retina

Retinoschisis, Juvenile: Follow-up

Author: Mi-Kyoung Song, MD, Vitreoretinal Surgeon, Eye Associates of New Mexico
Coauthor(s): Kent W Small, MD, Director/President, Macular and Retinal Disease Center; President, Molecular Insight LLC; Consulting Surgeon, Glendale Eye Medical Group
Contributor Information and Disclosures

Updated: Nov 26, 2007

Follow-up

Further Outpatient Care

  • Careful funduscopic examinations should be performed initially at a frequent interval in the first decade. Thereafter, patients can be monitored on an annual basis as long as no new symptoms occur.

Complications

  • Complications that can affect the visual acuity are vitreous hemorrhages, retinal detachments, and retinal atrophy.

Prognosis

  • With prompt identification and management of individuals with XJR, the vision should be preserved adequately.

Patient Education

  • Educating the patient and the family members on the symptoms of vitreous hemorrhage and retinal detachment can result in prompt detection and management of these events that can threaten central vision.

Miscellaneous

Medicolegal Pitfalls

  • Patients with XJR may be unaware of their visual loss until they fail a school vision screening. Family members of individuals with XJR should be screened early with a dilated funduscopic examination to rule out any retinal pathology and to intervene with appropriate surgical management to preserve central vision. Also, it is important to educate the family members and the individual to report any decrease in vision or progressive scotoma that may represent retinal detachment.
 


More on Retinoschisis, Juvenile

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Multimedia: Retinoschisis, Juvenile
References
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References

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Further Reading

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Keywords

X-linked juvenile retinoschisis, XJR, congenital cystic retinal detachment, congenital vascular veils in the vitreous, vitreous veils

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Contributor Information and Disclosures

Author

Mi-Kyoung Song, MD, Vitreoretinal Surgeon, Eye Associates of New Mexico
Mi-Kyoung Song, MD is a member of the following medical societies: American Academy of Ophthalmology, American Medical Association, American Society of Retina Specialists, and New Mexico Medical Society
Disclosure: Nothing to disclose.

Coauthor(s)

Kent W Small, MD, Director/President, Macular and Retinal Disease Center; President, Molecular Insight LLC; Consulting Surgeon, Glendale Eye Medical Group
Kent W Small, MD is a member of the following medical societies: American Academy of Ophthalmology, American Association for the Advancement of Science, American College of Physician Executives, American Medical Association, American Medical Informatics Association, American Ophthalmological Society, American Society of Human Genetics, Association for Research in Vision and Ophthalmology, California Medical Association, Macula Society, Pan-American Association of Ophthalmology, and Retina Society
Disclosure: Nothing to disclose.

Medical Editor

Russell P Jayne, MD, Consulting Vitreoretinal Surgeon, The Retina Center at Las Vegas
Russell P Jayne, MD is a member of the following medical societies: American Medical Association, American Society of Cataract and Refractive Surgery, and American Society of Retina Specialists
Disclosure: Nothing to disclose.

Pharmacy Editor

Simon K Law, MD, PharmD, Assistant Professor of Ophthalmology, Jules Stein Eye Institute; Chief of Section of Ophthalmology Surgical Services, Department of Veterans Affairs Healthcare Center, West Los Angeles
Simon K Law, MD, PharmD is a member of the following medical societies: American Academy of Ophthalmology, American Glaucoma Society, and Association for Research in Vision and Ophthalmology
Disclosure: Nothing to disclose.

Managing Editor

Steve Charles, MD, Director of Charles Retina Institute; Clinical Professor, Department of Ophthalmology, University of Tennessee College of Medicine
Steve Charles, MD is a member of the following medical societies: American Academy of Ophthalmology, American Society of Retina Specialists, Club Jules Gonin, Macula Society, and Retina Society
Disclosure: Alcon Laboratories Consulting fee Consulting

CME Editor

Lance L Brown, OD, MD, Ophthalmologist, Affiliated With Freeman Hospital and St John's Hospital, Regional Eye Center, Joplin, Missouri
Disclosure: Nothing to disclose.

Chief Editor

Hampton Roy Sr, MD, Associate Clinical Professor, Department of Ophthalmology, University of Arkansas for Medical Sciences
Hampton Roy Sr, MD is a member of the following medical societies: American Academy of Ophthalmology, American College of Surgeons, and Pan-American Association of Ophthalmology
Disclosure: Nothing to disclose.

 
 
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