eMedicine Specialties > Orthopedic Surgery > Hand & Upper Extremity

Sprengel Deformity: Follow-up

Author: Mihir M Thacker, MBBS, MS(Orth), DNB(Orth), FCPS(Orth), D'Ortho, Assistant Professor of Orthopedic Surgery and Pediatrics, Thomas Jefferson University; Consulting Staff, Department of Pediatric Orthopedic Surgery, Alfred I duPont Hospital for Children; Orthopedic Oncologist, Helen F Graham Cancer Center and Christiana Care Health Services
Coauthor(s): David S Feldman, MD, Chief, Pediatric Orthopedic Surgery, Associate Professor of Orthopedic Surgery, Director, Center for Children, Hospital for Joint Diseases, New York University Medical Center
Contributor Information and Disclosures

Updated: Jul 8, 2009

Outcome and Prognosis

Prognostic factors include the following:

  • Severity of the deformity
  • Age at surgery: Generally, results of surgery in children older than age 6 years are not as good.
  • Type of procedure: Relocation surgeries have better functional outcomes.
  • Associated anomalies: Anomalies such as Klippel-Feil syndrome compromise the eventual result.

Future and Controversies

Future

In a report by Mears, the author described a novel approach that included an oblique plane osteotomy of the scapular body, along with release of the long head of triceps from the scapula.36 He reported a significant improvement in function following this procedure.

Controversies

Surgical correction in older patients (>8 y) is controversial, and the results of surgery are not as good. However, in a study by Doita et al, the authors had good results after surgical correction in 2 adults, and they recommended surgery even in older patients.17

 


More on Sprengel Deformity

Overview: Sprengel Deformity
Workup: Sprengel Deformity
Treatment: Sprengel Deformity
Follow-up: Sprengel Deformity
Multimedia: Sprengel Deformity
References
Further Reading

References

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  36. Mears DC. Partial resection of the scapula and a release of the long head of triceps for the management of Sprengel's deformity. J Pediatr Orthop. Mar-Apr 2001;21(2):242-5. [Medline].

Keywords

Sprengel deformity, Sprengel's deformity, Sprengel anomaly, Sprengel's anomaly, congenital high scapula, congenital elevation of the scapula, failure of scapular descent, Sprengel's shoulder, Sprengel shoulder, hochgradige dislocation der scapula, high-grade dislocation of the scapula, hypoplastic scapula, elevated scapula, absent ribs, fused ribs, chest wall asymmetry, Klippel-Feil syndrome, cervical ribs, congenital scoliosis, cervical spina bifida, diastematomyelia, omovertebral bone, high shoulder, shoulder deformity, Greig syndrome, Greig cephalopolysyndactyly syndrome, GCPS, Poland syndrome, Poland anomaly, VATER association, velocardiofacial / velo-cardio-facial syndrome, VCFS, DiGeorge syndrome, floating harbor syndrome, floating-harbor syndrome, Goldenhar syndrome, oculo-auriculo-vertebral/oculoauriculovertebral syndrome, OAV syndrome, X-linked dominant hydrocephalus, skeletal anomalies, mental disturbance syndrome

Contributor Information and Disclosures

Author

Mihir M Thacker, MBBS, MS(Orth), DNB(Orth), FCPS(Orth), D'Ortho, Assistant Professor of Orthopedic Surgery and Pediatrics, Thomas Jefferson University; Consulting Staff, Department of Pediatric Orthopedic Surgery, Alfred I duPont Hospital for Children; Orthopedic Oncologist, Helen F Graham Cancer Center and Christiana Care Health Services
Mihir M Thacker, MBBS, MS(Orth), DNB(Orth), FCPS(Orth), D'Ortho is a member of the following medical societies: Children's Oncology Group, Limb Lengthening and Reconstruction Society ASAMI-North America, Medical Council of India, and Musculoskeletal Tumor Society
Disclosure: Nothing to disclose.

Coauthor(s)

David S Feldman, MD, Chief, Pediatric Orthopedic Surgery, Associate Professor of Orthopedic Surgery, Director, Center for Children, Hospital for Joint Diseases, New York University Medical Center
David S Feldman, MD is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Medical Association, American Orthopaedic Association, Pediatric Orthopaedic Society of North America, and Scoliosis Research Society
Disclosure: Nothing to disclose.

Medical Editor

Michael S Clarke, MD, Clinical Associate Professor, Department of Orthopedic Surgery, University of Missouri-Columbia School of Medicine
Michael S Clarke, MD is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Academy of Pediatrics, American Association for Hand Surgery, American College of Surgeons, American Medical Association, Arthroscopy Association of North America, Clinical Orthopaedic Society, Mid-Central States Orthopaedic Society, and Missouri State Medical Association
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: eMedicine Salary Employment

Managing Editor

Robert J Nowinski, DO, Clinical Assistant Professor of Orthopaedic Surgery, Ohio State University College of Medicine and Public Health, Ohio University College of Osteopathic Medicine; Private Practice, Orthopedic and Neurological Consultants, Inc, Columbus, Ohio
Robert J Nowinski, DO is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American College of Osteopathic Surgeons, American Medical Association, American Osteopathic Association, Ohio Osteopathic Association, and Ohio State Medical Association
Disclosure: Tornier Grant/research funds Other; Tornier Honoraria Speaking and teaching

CME Editor

Dinesh Patel, MD, FACS, Associate Clinical Professor of Orthopedic Surgery, Harvard Medical School; Chief of Arthroscopic Surgery, Department of Orthopedic Surgery, Massachusetts General Hospital
Dinesh Patel, MD, FACS is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Association of Physicians of Indian Origin, American College of International Physicians, and American College of Surgeons
Disclosure: Nothing to disclose.

Chief Editor

Harris Gellman, MD, Consulting Surgeon, Broward Hand Center; Voluntary Clinical Professor of Orthopedic Surgery and Plastic Surgery, Departments of Orthopedic Surgery and Surgery, University of Miami School of Medicine
Harris Gellman, MD is a member of the following medical societies: American Academy of Medical Acupuncture, American Academy of Orthopaedic Surgeons, American Orthopaedic Association, American Society for Surgery of the Hand, and Arkansas Medical Society
Disclosure: Nothing to disclose.

 
 
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