Outcome and Prognosis
Because postaxial hypoplasia of the lower extremity (fibular hemimelia) represents such a wide range of abnormalities with varying degrees of involvement, no simple statement can be made regarding the patient's prognosis. Judiciously chosen, well-timed procedures specifically tailored to the individual patient provide the best prospects for a well-aligned, functional limb of adequate length.
Future and Controversies
One controversy regarding postaxial hypoplasia of the lower extremity (fibular hemimelia) is its name. Historically, it has been called fibular aplasia or hypoplasia. This name has been defended largely because of historical precedent. However, as more insights have been gained into the constellation of related abnormalities stemming from the embryological limb bud, postaxial hypoplasia of the lower extremity may describe the syndrome more accurately. It also helps remind the clinician to look for other subtle abnormalities and not focus on only the obvious fibular deficiency.
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References
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Further Reading
Keywords
fibular hemimelia, fibular hypoplasia, fibula hypoplasia, fibula aplasia, fibular aplasia, fibular abnormality, postaxial hypoplasia of the lower extremity, limb-length discrepancy, postaxial hypoplasia of the lower extremity, amelia, phocomelia, ectromelia, sirenomelia
Follow-up: Fibular Hemimelia