Dysplasia Epiphysealis Hemimelica Treatment & Management
- Author: Khalid A Bakarman, MD, MB, BCh, SBIO; Chief Editor: Harris Gellman, MD more...
Medical Therapy
Supportive joint care, consisting of short-term splinting of the joint, may be beneficial.
Surgical Therapy
Most reported cases of DEH in the literature have been treated surgically, with surgical treatment consisting of excision of the mass, as well as correction of any angular deformity, while preserving the integrity of the affected joint as much as possible.[26, 27]
Follow-up
After surgery, the affected limb requires a short period of immobilization with a cast or splint, followed by active range of motion of the joint.
Complications
- Recurrence of the angular deformity after the corrective osteotomy - May be anticipated if the growth plate at the affected joint is open and active and the lesion itself has not been removed[23, 28]
- Degenerative osteoarthritis
- Fixed deformity
- Leg-length discrepancy[4, 28, 29]
- Loose bodies
Outcome and Prognosis
DEH, although an uncommon condition, can result in considerable disability because of direct involvement of the articular surface of the joint. Treatment with surgical excision offers the best results, but corrective osteotomy and reoperation for recurrent lesion may also be required.[30, 31]
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