eMedicine Specialties > Orthopedic Surgery > Pediatrics

Streeter Dysplasia: Follow-up

Author: Twee Do, MD, Assistant Professor, Department of Pediatric Orthopedic Surgery, University of Cincinnati College of Medicine; Director, Neuromuscular Orthopedic Services, Cincinnati Children's Hospital Medical Center
Contributor Information and Disclosures

Updated: Mar 30, 2009

Outcome and Prognosis

The prognosis for the isolated superficial extremity bands is good. Aside from cosmetic variability, no functional deficits remain (see Image 1).

Image shows the lower limb of a young child born ...

Image shows the lower limb of a young child born with moderate bands that extend deep to the fascia but do not compromise the neurovascular system.

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Image shows the lower limb of a young child born ...

Image shows the lower limb of a young child born with moderate bands that extend deep to the fascia but do not compromise the neurovascular system.


Deeper bands may be associated with progressive problems leading to later lymphatic and neurovascular compromise that requires surgery. For patients with acrosyndactyly, hand function is limited secondary to stiffness of the joints, but good prehension and grasp may be obtained with reconstructive procedures. Children who have had intrauterine amputations are usually well adapted to their physical limitations, and often little needs to be done. In children with a transverse deficiency proximal to the ankle joint, a prosthesis is required for full function.

Future and Controversies

Today, expecting parents are able to determine a lot about their child before birth. Obstetric ultrasound is currently the most common method to identify amniotic band syndrome in the prenatal period. When the new family is confronted with knowledge of a deformed neonate, whether the deformity is anencephaly or cleft lip and palate, controversy still exists as to the next step. Should the option for termination be offered, or should families be allowed to attempt to selectively produce the perfect child? This is an ethical debate that still has no final answer.

 


More on Streeter Dysplasia

Overview: Streeter Dysplasia
Workup: Streeter Dysplasia
Treatment: Streeter Dysplasia
Follow-up: Streeter Dysplasia
Multimedia: Streeter Dysplasia
References
Further Reading
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References

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Further Reading

Related eMedicine topics

Anencephaly

Cleft Lip

Cleft Palate

Clubfoot

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Keywords

Streeter dysplasia, congenital constriction band syndrome, amniotic band syndrome, ABS, constricting rings, acrosyndactyly, intrauterine amputation, digital amputations, ADAM complex, limb body wall syndrome, pseudo-ainhum, pseudoainhum, hemihypertrophy, anterolateral bowing, pseudarthrosis, leg-length discrepancy, teratologic clubfeet

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Contributor Information and Disclosures

Author

Twee Do, MD, Assistant Professor, Department of Pediatric Orthopedic Surgery, University of Cincinnati College of Medicine; Director, Neuromuscular Orthopedic Services, Cincinnati Children's Hospital Medical Center
Twee Do, MD is a member of the following medical societies: American Academy of Orthopaedic Surgeons and American Academy of Pediatrics
Disclosure: Nothing to disclose.

Medical Editor

Charles T Mehlman, DO, MPH, Director, Musculoskeletal Outcomes Research, Associate Professor, Division of Pediatric Orthopedic Surgery, Cincinnati Children's Hospital Medical Center
Charles T Mehlman, DO, MPH is a member of the following medical societies: American Academy of Pediatrics, American Fracture Association, American Medical Association, American Orthopaedic Foot and Ankle Society, American Osteopathic Association, Arthroscopy Association of North America, North American Spine Society, Ohio State Medical Association, Pediatric Orthopaedic Society of North America, and Scoliosis Research Society
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

George H Thompson, MD, Director, Pediatric Orthopedics, Rainbow Babies and Children's Hospital
George H Thompson, MD is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Orthopaedic Association, Pediatric Orthopaedic Society of North America, and Scoliosis Research Society
Disclosure: Nothing to disclose.

CME Editor

Dinesh Patel, MD, FACS, Associate Clinical Professor of Orthopedic Surgery, Harvard Medical School; Chief of Arthroscopic Surgery, Department of Orthopedic Surgery, Massachusetts General Hospital
Dinesh Patel, MD, FACS is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Association of Physicians of Indian Origin, American College of International Physicians, and American College of Surgeons
Disclosure: Nothing to disclose.

Chief Editor

Dennis P Grogan, MD, Clinical Professor, Department of Orthopedic Surgery, University of South Florida College of Medicine; Chief of Staff, Department of Orthopedic Surgery, Shriners Hospital for Children of Tampa
Dennis P Grogan, MD is a member of the following medical societies: American Academy of Orthopaedic Surgeons, American Medical Association, American Orthopaedic Association, American Orthopaedic Foot and Ankle Society, Eastern Orthopaedic Association, Irish American Orthopaedic Society, Pediatric Orthopaedic Society of North America, and Scoliosis Research Society
Disclosure: Nothing to disclose.

 
 
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