eMedicine Specialties > Plastic Surgery > Head/Neck

Ear, Congenital Deformities

Author: Carl H Manstein, MD, Private Practice, Manstein Plastic Surgical Association
Contributor Information and Disclosures

Updated: Jul 25, 2008

Introduction

Protruding ear and external ear microtia (or a variant) are the two most frequently encountered congenital ear problems in plastic surgery. The former condition is commonly treated by many practitioners, while the latter has become the bailiwick of just a few surgeons. Most of this discussion focuses on prominent ears because of their common occurrence. Otoplasty has undergone important developments, with numerous techniques being presented in the surgical literature. Congenital ear microtia and atresia is treated in only a few centers by surgeons with an established reputation, similar to the way some centers specialize in craniofacial osteotomy surgery.

History of the Procedure

Many different approaches to setback otoplasty have been developed. Originally, the first operations were merely resection of skin from the posterior sulcus. Over the years, an evolution of operations has occurred, including those with and without sutures, with and without resection of cartilage, and with or without scoring of cartilage. With this many variations, no single "right" technique exists.

Microtia as a modern operation was first pioneered by Tanzer from DartmouthMedicalSchool. Tanzer was the first to develop the technique of using a whole piece of rib cartilage to simulate the cartilaginous structure of the external ear. Burt Brent from Stanford, Calif, expounded upon Tanzer's work and has written extensively about microtia reconstruction.

Problem

The expression "beauty is in the eye of the beholder" is often quoted and still quite relevant. What constitutes a prominent ear? Ray Elliot stated in his 1990 review article in Clinics of Plastic Surgery, "the esthetic ear protrudes less than 2 cm when measured from the surface of the helix to the mastoid scalp at the midpoint of the ear's length."1 However, once this measurement achieves a distance of less than 1.2 cm, the ear has an equally displeasing "pinned back" appearance. The ear protrudes more at the lower pole and less so at the upper pole because of the shape of the skull. The scaphoconchal angle should have a natural soft roll and should not block the view of the helix anywhere along its course when viewed anteriorly.

Frequency

No statistics are available on the prevalence of protruding or prominent ears. Heredity plays a role in many deformities of the external ear.

Etiology

Most embryologic studies of the ear focus on the development of the 6 ear hillocks. These hillocks appear around the fundus of the first branchial groove by 38 days of gestation. As the groove closes and the first and second arches come together, the primitive ear is formed by day 50 of gestation. The first 3 hillocks come from the first branchial arch and the second 3 from the second branchial arch. Absence of hillocks 2-5 produces a frequent and typical microtia. Malformations of the ear can appear anywhere during this development.

Pathophysiology

Features seen in the patient with prominent or protruding ears (in decreasing order of importance) include the following:

  • Absent antihelical fold
  • Obtuse scaphoconchal angle
  • Increased distance of helical rim to scalp
  • Deep conchal bowl

Address some or all of these problems in the planning and execution of the operation to correct the abnormality.

Auricular anatomy in children varies only slightly from that in adults. By the third year, 85% of ear growth and development occurs, and little growth occurs after 10 years. The ear's height may increase gradually into adulthood but its distance from the scalp changes little after 10 years. Because of this, setback otoplasty can safely be performed on children as young as 5-6 years.

Presentation

Most parents, while emotionally distressed when their baby is born with a portion of the external auricle missing or severely distorted, are unconcerned about protruding ears at birth. Patients tend to seek surgical opinion for protruding ear problems at two stages of life. Parents often seek medical advice for their children at the start of school because of the child's complaints of classmates' teasing. The jeer of "Dumbo" is difficult for a first grader. The second group of patients consists primarily of women in their twenties or early thirties. These patients also are embarrassed about their protruding ears.

Indications

For the child born without an external ear, the indications for surgical reconstruction are obvious. Parents are anxious to proceed as soon as possible to spare their child any embarrassment. Unlike cleft lip surgery, which is performed in the first few weeks of life, most experienced surgeons recommend waiting to do multistages at age 6-7 years. The more important question is not whether surgery is indicated, but which of the techniques for reconstruction is indicated for the individual.

In the patient born with a prominent ear or deformity, the situation may be a little different. With the obtuse scaphoconchal angle and absent antihelical fold, distance from the helical rim varies. Many authorities believe the external ear should protrude no more than 2 cm from the surface of the helix to the mastoid scalp at the midpoint of the ear's length. This measurement is a guide and not an absolute rule. Much depends upon the patient's expectations as well as the surgeon's experience. Although congenital absence is almost always unilateral, patients with prominent ears usually require a bilateral operation.

Children with protruding ears generally do well when operated on as early as age 5-6 years. A study from the Medical College of Wisconsin presented a series of 12 patients in whom otoplasty was performed before the age of 4 years with good results.2 Taunts from schoolmates begin at this time. Parents, not realizing how cruel kindergarten children can be, are often oblivious to this ridicule. Young girls reveal much less of this mental anguish because they are able to wear their hair long and cover their ears. They never wear a ponytail, lest a peer discovers their ears stick out.

In this author's practice, a common indication for setback otoplasty is the approximately 20-year-old woman who is getting married and now wants to wear her hair in an upswept fashion. Boys do not have that option. Because of a genetic predisposition to protruding ears, some parents find that seeking plastic surgical consultation for their children is difficult. To admit his or her child is flawed, the parent must admit he or she is flawed.

Relevant Anatomy

Anatomy of the normal ear

  • Width of ear equals approximately 55% of length
  • Helix-to-mastoid distance - Upper third equals 10-12 mm; middle third equals 16-18 mm; lower third equals 20-22 mm
  • Sides should be within 3 mm of each other
  • Axis of ear is parallel to profile of nose

The ear can be difficult to reproduce surgically because only a thin layer of skin covers the cartilaginous structure.3 This cartilaginous structure is attached to the temporal bone medially by several minor intrinsic muscles. A looser attachment of skin is found upon the posterior aspect of the auricle than the anterior aspect of the auricle. The vascular supply comes from the superficial temporal and posterior auricular vessels. Corresponding veins drain the ear. The sensory supply arises from the great auricular nerve, with the upper portion of the ear supplied by the lesser occipital and auriculotemporal nerves. The conchal region is supplied by the vagal branch.

Prominent or protruding ears

  • Absent antihelical fold
  • Increased scaphoconchal angle
  • Deep conchal bowl
  • Increased distance from helical rim to scalp
  • Flattening of superior crus
  • Normal helical length

Cup ear deformity (lop-ear, constricted ear)

  • Flattening of antihelix
  • Widening of concha
  • Overhang of helix
  • Compression of scapha and fossa triangularis
  • Indistinct antihelix and crura
  • Shortened length of helix
  • Ear appears small, but no difference in size

Cryptotia

  • Absence of retroauricular sulcus, causing the superior pole of ear to appear buried
  • Sharply curved antihelical crus
  • No foreshortening of auricle

Stahl ear

  • Presence of third crus
  • Flat antihelix
  • Malformed scaphoid fossa

Contraindications

Contraindications for treatment of prominent ears include the following:

  • Unreasonable expectations from either patient or family
  • Child younger than 5 years
  • Patient who is unable to tolerate postoperative wound care, including a protective bandage head wrap
  • Patient who opposes the operation despite his or her parents' wishes to proceed

More on Ear, Congenital Deformities

Overview: Ear, Congenital Deformities
Workup: Ear, Congenital Deformities
Treatment: Ear, Congenital Deformities
Follow-up: Ear, Congenital Deformities
Multimedia: Ear, Congenital Deformities
References

References

  1. Elliott RA Jr. Otoplasty: a combined approach. Clin Plast Surg. Apr 1990;17(2):373-81. [Medline].

  2. Gosain AK, Recinos RF. Otoplasty in children less than four years of age: surgical technique. J Craniofac Surg. Jul 2002;13(4):505-9. [Medline].

  3. Furnas DW. Complications of surgery of the external ear. Clin Plast Surg. Apr 1990;17(2):305-18. [Medline].

  4. Matsuo K, Hayashi R, Kiyono M, et al. Nonsurgical correction of congenital auricular deformities. Clin Plast Surg. Apr 1990;17(2):383-95. [Medline].

  5. Rubino C, Farace F, Figus A, et al. Anterior scoring of the upper helical cartilage as a refinement in aesthetic otoplasty. Aesthetic Plast Surg. Mar-Apr 2005;29(2):88-93; discussion 94. [Medline].

  6. Erol OO. New modification in otoplasty: anterior approach. Plast Reconstr Surg. Jan 2001;107(1):193-202; discussion 203-5. [Medline].

  7. Furnas DW. Correction of prominent ears with multiple sutures. Clin Plast Surg. Jul 1978;5(3):491-5. [Medline].

  8. Bauer BS, Song DH, Aitken ME. Combined otoplasty technique: chondrocutaneous conchal resection as the cornerstone to correction of the prominent ear. Plast Reconstr Surg. Sep 15 2002;110(4):1033-40; discussion 1041. [Medline].

  9. Blessing JD. Physician Assistant's Drug Handbook. Springhouse, Pa: Springhouse Pub Co; 1999.

  10. Davis J. Part II: Aesthetic surgery. In: Aesthetic and Reconstructive Surgery. 1987:129-87.

  11. Medical Economics Staff. Physician's Desk Reference. 53rd ed. Medical Economics Co; 2000.

  12. Wilkes GH, Wolfaardt JF. Craniofacial osseointegrated prosthetic reconstruction. In: Habal MB, ed. Advances in Plastic and Reconstructive Surgery. Vol 15. 1999:51-82.

Further Reading

Keywords

ear deformity, congenital ear deformity, protruding ear, ear microtia, setback otoplasty, set-back otoplasty, protruding ears, prominent ears, lop-ear, constricted ear, external ear microtia

Contributor Information and Disclosures

Author

Carl H Manstein, MD, Private Practice, Manstein Plastic Surgical Association
Carl H Manstein, MD is a member of the following medical societies: American Society of Plastic Surgeons, Pennsylvania Medical Society, and Sigma Xi
Disclosure: Nothing to disclose.

Medical Editor

Lawrence Ketch, MD, FAAP, FACS, Head, Program Director, Associate Professor, Department of Surgery, Division of Plastic Surgery, University of Colorado Health Sciences Center; Chief, Pediatric Plastic, The Children's Hospital of Denver
Lawrence Ketch, MD, FAAP, FACS is a member of the following medical societies: American Academy of Pediatrics, American Association for Hand Surgery, American Association of Plastic Surgeons, American Burn Association, American Cleft Palate/Craniofacial Association, American College of Surgeons, American Society for Surgery of the Hand, American Society of Maxillofacial Surgeons, American Society of Plastic Surgeons, Association for Academic Surgery, and Plastic Surgery Research Council
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

Jaime R Garza, MD, DDS, FACS, Consulting Staff, Private Practice
Jaime R Garza, MD, DDS, FACS is a member of the following medical societies: Alpha Omega Alpha, American Academy of Otolaryngology-Head and Neck Surgery, American Cleft Palate/Craniofacial Association, American College of Surgeons, American Medical Association, American Society for Aesthetic Plastic Surgery, American Society of Maxillofacial Surgeons, Texas Medical Association, and Texas Society of Plastic Surgeons
Disclosure: Nothing to disclose.

CME Editor

Nicolas (Nick) G Slenkovich, MD, Practice Director, Colorado Plastic Surgery Center at Swedish Medical Center
Nicolas (Nick) G Slenkovich, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American Medical Association, American Society of Plastic Surgeons, and Colorado Medical Society
Disclosure: Nothing to disclose.

Chief Editor

Deepak Narayan, MD, FRCS, Associate Professor of Surgery (Plastic), Yale University School of Medicine; Chief of Plastic Surgery, West Haven Veterans Affairs Medical Center
Deepak Narayan, MD, FRCS is a member of the following medical societies: American Association for the Advancement of Science, American College of Surgeons, American Medical Association, American Society of Maxillofacial Surgeons, American Society of Plastic Surgeons, Indian Medical Association, Plastic Surgery Research Council, Royal College of Surgeons of Edinburgh, and Royal College of Surgeons of England
Disclosure: Nothing to disclose.

 
 
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