eMedicine Specialties > Hematology > Stem Cells and Disorders
Lymphoproliferative Syndrome, X-linked: Follow-up
Updated: Sep 15, 2008
Follow-up
Complications
- See Pathophysiology.
Prognosis
- Except for reported cases of optimal outcome after monoclonal anti-CD20, and remission due to stem cell transplantation, few children with X-linked lymphoproliferative syndrome (XLP) survive to adulthood. Therefore, most patients with available matched donors apparently should be referred for transplantation. However, more data are needed to substantiate the efficacy of this form of therapy for X-linked lymphoproliferative disease (XLP).
Miscellaneous
Medicolegal Pitfalls
- X-linked lymphoproliferative syndrome (XLP) should be suspected in the case of an exceptionally severe lymphadenopathic reaction in a patient with mononucleosis. Otherwise, the rarity of X-linked lymphoproliferative syndrome (XLP) suggests little likelihood of legal risk.
More on Lymphoproliferative Syndrome, X-linked |
| Overview: Lymphoproliferative Syndrome, X-linked |
| Differential Diagnoses & Workup: Lymphoproliferative Syndrome, X-linked |
| Treatment & Medication: Lymphoproliferative Syndrome, X-linked |
Follow-up: Lymphoproliferative Syndrome, X-linked |
| References |
| « Previous Page |
References
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Further Reading
Keywords
X-linked lymphoproliferative syndrome, X-linked lymphoproliferative disorder, lymphoproliferative disorders, lymphoproliferative diseases, XLP syndrome, Duncan syndrome, Duncan's syndrome, X-linked recessive progressive combined variable immunodeficiency syndrome, familial fatal EBV infection, Purtilo syndrome, Epstein-Barr virus, EBV, infectious mononucleosis, hypogammaglobulinemia, lymphoma
Follow-up: Lymphoproliferative Syndrome, X-linked