eMedicine Specialties > Hematology > Stem Cells and Disorders
Myeloproliferative Disease: Follow-up
Updated: Feb 13, 2008
Follow-up
Complications
- Patients are at risk of both thrombotic and hemorrhagic events.
- Thrombotic and hemorrhagic events are particularly common in polycythemia vera (PV) and essential thrombocythemia (ET). Thrombosis is the cause of death in 30-40% of patients.
- A particularly serious thrombotic event that may be associated with polycythemia vera is Budd-Chiari syndrome, which is due to hepatic venous or inferior venal caval thrombosis.
- Patients are at risk of developing secondary acute leukemia from their underlying disorder as well as their treatment.
Miscellaneous
Medicolegal Pitfalls
When suspecting polycythemia in patients with iron deficiency, replenish iron before conducting red blood cell mass studies; otherwise, some cases of true polycythemia may be missed.
More on Myeloproliferative Disease |
| Overview: Myeloproliferative Disease |
| Differential Diagnoses & Workup: Myeloproliferative Disease |
| Treatment & Medication: Myeloproliferative Disease |
Follow-up: Myeloproliferative Disease |
| Multimedia: Myeloproliferative Disease |
| References |
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References
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Further Reading
Keywords
MPD, polycythemia vera, PV, polycythemia rubra vera, primary thrombocythemia, PT, agnogenic myeloid metaplasia, AMM, chronic myelogenous leukemia, chronic myeloid leukemia, CML, myelofibrosis, MF, acute leukemia, myelodysplastic syndrome, essential thrombocythemia, ET, Budd-Chiari syndrome, chronic idiopathic myelofibrosis, CIM, chronic neutrophilic leukemia, CNL, chronic eosinophilic leukemia, CEL, hypereosinophilic syndrome, HES
Follow-up: Myeloproliferative Disease