eMedicine Specialties > Radiology > Brain/Spine

Syringohydromyelia: Multimedia

Author: Farhood Saremi, MD, Professor of Radiology, Director of Cardiothoracic Radiology, Department of Radiological Sciences, University of California-Irvine
Coauthor(s): Chi-Shing Zee, MD, Chief of Neuroradiology, Professor, Departments of Radiology and Neurosurgery, University of Southern California School of Medicine; John L Go, MD, Assistant Professor, Department of Radiology, Section of Neuroradiology, Keck School of Medicine, University of Southern California Medical Center
Contributor Information and Disclosures

Updated: Dec 10, 2008

Multimedia

T1-weighted sagittal MRI scan demonstrates syring...Media file 1: T1-weighted sagittal MRI scan demonstrates syringomyelia with a Chiari I malformation without hydrocephalus. The syrinx cavity does not communicate with the fourth ventricle and arises immediately caudal to the descended cerebellar tonsils. (See also next Image.)
T1-weighted sagittal MRI scan demonstrates syring...

T1-weighted sagittal MRI scan demonstrates syringomyelia with a Chiari I malformation without hydrocephalus. The syrinx cavity does not communicate with the fourth ventricle and arises immediately caudal to the descended cerebellar tonsils. (See also next Image.)

Corresponding T2-weighted cervical MRI scan of a ...Media file 2: Corresponding T2-weighted cervical MRI scan of a patient with a Chiari I malformation (same patient as in Image above). Note the areas of flow void within the syrinx cavity. The flow void in the syrinx cavity is not a distinguishing characteristic of syringomyelia and may be seen in cases associated with Chiari malformations, posttraumatic syringes, and adhesive arachnoiditis. The presence of a cerebrospinal fluid flow void reflects the pulsatile movements of syrinx fluid. Such movements have been proposed as a cause of syrinx propagation, and observation of flow void may have prognostic significance.
Corresponding T2-weighted cervical MRI scan of a ...

Corresponding T2-weighted cervical MRI scan of a patient with a Chiari I malformation (same patient as in Image above). Note the areas of flow void within the syrinx cavity. The flow void in the syrinx cavity is not a distinguishing characteristic of syringomyelia and may be seen in cases associated with Chiari malformations, posttraumatic syringes, and adhesive arachnoiditis. The presence of a cerebrospinal fluid flow void reflects the pulsatile movements of syrinx fluid. Such movements have been proposed as a cause of syrinx propagation, and observation of flow void may have prognostic significance.

Midsagittal T1-weighted cervical MRI scan of a yo...Media file 3: Midsagittal T1-weighted cervical MRI scan of a young man with a posttraumatic syrinx. Note how the syrinx extends rostrally from the level of the injury. The incidence of significant syringomyelia above the spinal fracture site is approximately 3-5%. With longer survival in paraplegic and quadriplegic patients, the incidence of posttraumatic syringomyelia is likely to increase. (See also next Image.)
Midsagittal T1-weighted cervical MRI scan of a yo...

Midsagittal T1-weighted cervical MRI scan of a young man with a posttraumatic syrinx. Note how the syrinx extends rostrally from the level of the injury. The incidence of significant syringomyelia above the spinal fracture site is approximately 3-5%. With longer survival in paraplegic and quadriplegic patients, the incidence of posttraumatic syringomyelia is likely to increase. (See also next Image.)

Midsagittal T2-weighted cervical MRI scan (same p...Media file 4: Midsagittal T2-weighted cervical MRI scan (same patient as in Image above) demonstrates a flow void sign in the center of the posttraumatic syrinx, reflecting pulsatile fluid motion. Detection of cerebrospinal fluid (CSF) movement in a posttraumatic spinal cord lesion may alter therapy. Preoperative assessment may be made on the basis of the presence or absence of the flow void sign on T2-weighted MRI. Symptomatic posttraumatic syringes with positive flow void sign respond favorably to syrinx-subarachnoid shunting.
Midsagittal T2-weighted cervical MRI scan (same p...

Midsagittal T2-weighted cervical MRI scan (same patient as in Image above) demonstrates a flow void sign in the center of the posttraumatic syrinx, reflecting pulsatile fluid motion. Detection of cerebrospinal fluid (CSF) movement in a posttraumatic spinal cord lesion may alter therapy. Preoperative assessment may be made on the basis of the presence or absence of the flow void sign on T2-weighted MRI. Symptomatic posttraumatic syringes with positive flow void sign respond favorably to syrinx-subarachnoid shunting.

Conus ependymoma associated with syringohydromyel...Media file 5: Conus ependymoma associated with syringohydromyelia. Gadolinium-enhanced sagittal MRI scan of the thoracolumbar junction demonstrates an enhancing tumor in the conus medullaris. The syrinx extends rostrally into the cervical cord (not shown). MRI studies of syringomyelia should involve the entire cord to exclude associated pathologies and should include intravenous contrastenhanced MRI studies to exclude tumor.
Conus ependymoma associated with syringohydromyel...

Conus ependymoma associated with syringohydromyelia. Gadolinium-enhanced sagittal MRI scan of the thoracolumbar junction demonstrates an enhancing tumor in the conus medullaris. The syrinx extends rostrally into the cervical cord (not shown). MRI studies of syringomyelia should involve the entire cord to exclude associated pathologies and should include intravenous contrastenhanced MRI studies to exclude tumor.

Postoperative arachnoiditis with secondary syring...Media file 6: Postoperative arachnoiditis with secondary syringomyelia. T1-weighted sagittal MRI scan shows L1 vertebral body wedge fracture, extensive laminectomy, and a large loculated syrinx. Deformity of the cord margins may suggest arachnoiditis. Adhesive spinal arachnoiditis may develop after trauma, infection, subarachnoid hemorrhage, and spinal surgery.
Postoperative arachnoiditis with secondary syring...

Postoperative arachnoiditis with secondary syringomyelia. T1-weighted sagittal MRI scan shows L1 vertebral body wedge fracture, extensive laminectomy, and a large loculated syrinx. Deformity of the cord margins may suggest arachnoiditis. Adhesive spinal arachnoiditis may develop after trauma, infection, subarachnoid hemorrhage, and spinal surgery.

More on Syringohydromyelia

Overview: Syringohydromyelia
Imaging: Syringohydromyelia
Multimedia: Syringohydromyelia
References
Further Reading

References

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Keywords

syringohydromyelia, hydromyelia, syringomyelia, hydrocephalus, multiple sclerosis, spinal arachnoiditis, cord syrinx, tubular cavitation of spinal cord

Contributor Information and Disclosures

Author

Farhood Saremi, MD, Professor of Radiology, Director of Cardiothoracic Radiology, Department of Radiological Sciences, University of California-Irvine
Farhood Saremi, MD is a member of the following medical societies: American College of Radiology and Radiological Society of North America
Disclosure: Nothing to disclose.

Coauthor(s)

Chi-Shing Zee, MD, Chief of Neuroradiology, Professor, Departments of Radiology and Neurosurgery, University of Southern California School of Medicine
Chi-Shing Zee, MD is a member of the following medical societies: American Society of Neuroradiology
Disclosure: Nothing to disclose.

John L Go, MD, Assistant Professor, Department of Radiology, Section of Neuroradiology, Keck School of Medicine, University of Southern California Medical Center
Disclosure: Nothing to disclose.

Medical Editor

Lucien M Levy, MD, PhD, Director of Neuroradiology, Professor of Radiology, Department of Radiology, George Washington University Medical Center
Lucien M Levy, MD, PhD is a member of the following medical societies: American Cancer Society, American College of Radiology, American Heart Association, American Medical Association, American Roentgen Ray Society, American Society of Neuroradiology, and Radiological Society of North America
Disclosure: Nothing to disclose.

Pharmacy Editor

Bernard D Coombs, MB, ChB, PhD, Consulting Staff, Department of Specialist Rehabilitation Services, Hutt Valley District Health Board, New Zealand
Disclosure: Nothing to disclose.

CME Editor

Robert M Krasny, MD, Consulting Staff, Department of Radiology, The Angeles Clinic and Research Institute
Robert M Krasny, MD is a member of the following medical societies: American Roentgen Ray Society and Radiological Society of North America
Disclosure: Nothing to disclose.

Chief Editor

James G Smirniotopoulos, MD, Professor of Radiology, Neurology, and Biomedical Informatics, Chairman, Department of Radiology and Radiological Sciences, Uniformed Services University of the Health Sciences
James G Smirniotopoulos, MD is a member of the following medical societies: American College of Radiology, American Roentgen Ray Society, American Society of Head and Neck Radiology, American Society of Neuroradiology, American Society of Pediatric Neuroradiology, Association of University Radiologists, and Radiological Society of North America
Disclosure: Nothing to disclose.

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