eMedicine Specialties > Radiology > Gastrointestinal

Caroli Disease: Follow-up

Author: William J Romano, MD, FRCPC, Director, Interventional Radiology Research, Department of Radiology, William Beaumont Hospital; Clinical Assistant Professor, Department of Radiology, Wayne State University School of Medicine
Contributor Information and Disclosures

Updated: Apr 6, 2009

Intervention

Medicolegal Pitfalls

  • Iatrogenic complications from interventional radiology procedures such as PTC, stone removal, tube drainage, and stent placement can be serious. These include, but are not limited to, bleeding, hemobilia, infection, sepsis, reactions to the contrast medium, pneumothorax, bile ascites, allergic reactions to other procedural medications, renal failure, liver injury, and liver infarction. Surgical correction may be required.
  • Misdiagnosis of Caroli disease is not uncommon because the diagnosis is largely one of exclusion. Abnormal findings on cross-sectional images are typical but their cause may be mistaken. Misinterpretation of the imaging results may delay diagnosis of the disease or its complications.
  • Misdiagnosis of cancer related to cholangiocarcinoma in a patient with Caroli disease is possible. Once Caroli disease is diagnosed, related complications should be excluded. If changes (eg, development of a mass) occur with subsequent studies, cholangiocarcinoma should be suspected.

Special Concerns

  • Pediatric patients require tailored examinations.
 


More on Caroli Disease

Overview: Caroli Disease
Imaging: Caroli Disease
Follow-up: Caroli Disease
Multimedia: Caroli Disease
References
Further Reading
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References

  1. Sgro M, Rossetti S, Barozzino T, Toi A, Langer J, Harris PC, et al. Caroli's disease: prenatal diagnosis, postnatal outcome and genetic analysis. Ultrasound Obstet Gynecol. Jan 2004;23(1):73-6. [Medline].

  2. Levy AD, Rohrmann CA Jr, Murakata LA, Lonergan GJ. Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol. Oct 2002;179(4):1053-7. [Medline]. [Full Text].

  3. Ananthakrishnan AN, Saeian K. Caroli's disease: identification and treatment strategy. Curr Gastroenterol Rep. Apr 2007;9(2):151-5. [Medline].

  4. Wang ZX, Yan LN, Li B, Zeng Y, Wen TF, Wang WT. Orthotopic liver transplantation for patients with Caroli's disease. Hepatobiliary Pancreat Dis Int. Feb 2008;7(1):97-100. [Medline].

  5. Ulrich F, Pratschke J, Pascher A, Neumann UP, Lopez-Hänninen E, Jonas S, et al. Long-term outcome of liver resection and transplantation for Caroli disease and syndrome. Ann Surg. Feb 2008;247(2):357-64. [Medline].

  6. Millwala F, Segev DL, Thuluvath PJ. Caroli's disease and outcomes after liver transplantation. Liver Transpl. Jan 2008;14(1):11-7. [Medline].

  7. Asselah T, Ernst O, Sergent G. Caroli''s disease: a magnetic resonance cholangiopancreatography diagnosis. Am J Gastroenterol. Jan 1998;93(1):109-10. [Medline].

  8. Guy F, Cognet F, Dranssart M, Cercueil JP, Conciatori L, Krausé D. Caroli's disease: magnetic resonance imaging features. Eur Radiol. Nov 2002;12(11):2730-6. [Medline].

  9. Caroli-Bosc FX, Demarquay JF, Conio M. The role of therapeutic endoscopy associated with extracorporeal shock- wave lithotripsy and bile acid treatment in the management of Caroli''s disease. Endoscopy. Aug 1998;30(6):559-63. [Medline].

  10. Ciambotti GF, Ravi J, Abrol RP. Right-sided monolobar Caroli''s disease with intrahepatic stones: nonsurgical management with ERCP. Gastrointest Endosc. Nov-Dec 1994;40(6):761-4. [Medline].

  11. Gold DM, Stark B, Pettei MJ. Successful use of an internal biliary stent in Caroli''s disease. Gastrointest Endosc. Dec 1995;42(6):589-92. [Medline].

  12. Kaiser JA, Mall JC, Salmen BJ. Diagnosis of Caroli disease by computed tomography: report of two cases. Radiology. Sep 1979;132(3):661-4. [Medline].

  13. Marchal GJ, Desmet VJ, Proesmans WC. Caroli disease: high-frequency US and pathologic findings. Radiology. Feb 1986;158(2):507-11. [Medline].

  14. Mittelstaedt CA, Volberg FM, Fischer GJ. Caroli''s disease: sonographic findings. AJR Am J Roentgenol. Mar 1980;134(3):585-7. [Medline].

  15. Sgro M, Rossetti S, Barozzino T, Toi A, Langer J, Harris PC, et al. Caroli's disease: prenatal diagnosis, postnatal outcome and genetic analysis. Ultrasound Obstet Gynecol. Jan 2004;23(1):73-6. [Medline].

  16. Toma P, Lucigrai G, Pelizza A. Sonographic patterns of Caroli''s disease: report of 5 new cases. J Clin Ultrasound. Mar-Apr 1991;19(3):155-61. [Medline].

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Keywords

Caroli disease, Caroli's disease, communicating cavernous ectasia, congenital cystic dilatation of the intrahepatic biliary tree

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Contributor Information and Disclosures

Author

William J Romano, MD, FRCPC, Director, Interventional Radiology Research, Department of Radiology, William Beaumont Hospital; Clinical Assistant Professor, Department of Radiology, Wayne State University School of Medicine
William J Romano, MD, FRCPC is a member of the following medical societies: Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

Medical Editor

Zahir Amin, MD, MBBS, MRCP, FRCR, Consulting Staff, Department of Imaging, University College Hospital, UK
Zahir Amin, MD, MBBS, MRCP, FRCR is a member of the following medical societies: British Institute of Radiology, British Medical Association, and Royal College of Radiologists
Disclosure: Nothing to disclose.

Pharmacy Editor

Bernard D Coombs, MB, ChB, PhD, Consulting Staff, Department of Specialist Rehabilitation Services, Hutt Valley District Health Board, New Zealand
Disclosure: Nothing to disclose.

Managing Editor

Abraham H Dachman, MD, FACR, Professor, Department of Radiology, The University of Chicago School of Medicine; Director of CT, Department of Radiology, The University of Chicago Hospitals
Abraham H Dachman, MD, FACR is a member of the following medical societies: Radiological Society of North America
Disclosure: iCAD, Inc. Consulting fee Consulting; iCAD, Inc. Grant/research funds Other; GE Healtcare, Inc. Honoraria Speaking and teaching

CME Editor

Robert M Krasny, MD, Consulting Staff, Department of Radiology, Resolution Imaging Medical Corporation
Robert M Krasny, MD is a member of the following medical societies: American Roentgen Ray Society and Radiological Society of North America
Disclosure: Nothing to disclose.

Chief Editor

John Karani, MBBS, FRCR, Clinical Director of Radiology and Consultant Radiologist, Department of Radiology, King's College Hospital, London
John Karani, MBBS, FRCR is a member of the following medical societies: British Institute of Radiology, British Society of Interventional Radiology, Cardiovascular and Interventional Radiological Society of Europe, European Society of Gastrointestinal and Abdominal Radiology, European Society of Radiology, Radiological Society of North America, and Royal College of Radiologists
Disclosure: Nothing to disclose.

 
 
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