eMedicine Specialties > Radiology > Genitourinary
Autosomal Dominant Polycystic Kidney Disease: Multimedia
Updated: Dec 23, 2008
Multimedia
 | Media file 1: Plain radiograph of the kidney, ureters, and bladder in a 50-year-old woman with adult-type polycystic kidney disease. The kidneys are enlarged with multiple, curvilinear, and ringlike calcifications arising from the renal cyst. The surgical clip from renal transplant is seen projected over the left iliac wing. |
 | Media file 2: Excretory 30-minute urographic image in a patient with polycystic kidney disease. The kidneys are enlarged with an elongated, splayed, and distorted collecting system resulting from the presence of innumerable cysts. Note bilateral avascular necrosis of the femoral heads. |
 | Media file 3: Sonogram of the kidney in a patient with polycystic kidney disease shows numerous cysts of varying sizes. |
 | Media file 4: Sonogram of the liver (same patient as in Image above) shows multiple cysts. Approximately 29-73% of patients with adult-type polycystic disease have cysts in the liver. |
 | Media file 5: Excretory 5-minute urographic image in a young male patient with bilateral polycystic disease. The calyces are elongated and splayed because of the cysts, seen best on the right. Note the large size of both kidneys. |
 | Media file 6: Aortogram (same patient as in Image above) demonstrates stretching of the intrarenal arterial branches, seen best in the upper pole of the right kidney. |
 | Media file 7: Sonogram of the right kidney in a patient with adult-type polycystic kidney disease. The scan shows numerous cysts of varying sizes, with a large cyst in the upper pole. |
 | Media file 8: Selective renal arteriogram (same patient as in Image above). A large filling defect is demonstrated in the upper pole of the right kidney, forming an acute angle with the normal renal cortex that results in a characteristic beak appearance. |
 | Media file 9: Sonogram of the liver in a newborn with polycystic kidney disease shows numerous tiny cysts affecting both lobes of the liver. |
 | Media file 10: Sonogram of the kidney in a newborn (same patient as in Image above) shows numerous cysts of varying sizes predominantly situated in the periphery. |
 | Media file 11: Unenhanced axial computed tomography scan of the abdomen in a 45-year-old woman with adult polycystic kidney disease. The scan shows numerous cysts of different sizes involving the kidneys, liver, and pancreas. |
 | Media file 12:
Contrast-enhanced computed tomography scan in a
45-year-old woman with adult polycystic kidney disease (same
patient as in Image above) clearly demonstrates the cysts in
the head of the pancreas. |
 | Media file 13: Sonogram of the left kidney in a 45-year-old woman with bilateral polycystic kidney disease who presented with acute onset of left loin pain. The scan shows fluid around the left kidney and in the left pleural space, consistent with a ruptured renal cyst. |
 | Media file 14: A 42-year-old man known to have autosomal dominant polycystic kidney disease presented with sudden left-upper-quadrant pain and hypotension. Sonography performed in the emergency department showed echogenic fluid in the left upper quadrant. The spleen was not identified. Some free peritoneal fluid also was seen (sonogram not shown). Contrast-enhanced computed tomography scan of the upper abdomen shows that the medial spleen (S) is associated with both intracapsular and extracapsular fluid. Note the cysts within the right kidney. |
 | Media file 15: Contrast-enhanced computed tomography scan of the upper abdomen in the same patient as in Image 14 shows cysts in both kidneys. Note the free peritoneal fluid around the tip of the liver. |
 | Media file 16: Because the patient shown in Images 14-15 was hemodynamically unstable, a splenic angiogram was obtained, with a focus on embolizing the spleen. The angiogram shows a medially displaced spleen with separation or stretching of the splenic capsule. A slit is seen in the lower lateral border as a result of splenic rupture (arrow). The spleen was embolized successfully, and no surgical intervention was required. The patient had splenic cysts, as previously recorded elsewhere. The presumptive diagnosis was spontaneous rupture of a splenic cyst. The patient had no history of trauma. |
More on Autosomal Dominant Polycystic Kidney Disease |
| Overview: Autosomal Dominant Polycystic Kidney Disease |
| Imaging: Autosomal Dominant Polycystic Kidney Disease |
| Follow-up: Autosomal Dominant Polycystic Kidney Disease |
 Multimedia: Autosomal Dominant Polycystic Kidney Disease |
| References |
| « Previous Page |
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Further Reading
Keywords
autosomal dominant polycystic kidney disease, Potter type III disease, adult polycystic kidney disease, kidney disease, polycystic kidney disease, renal cyst, ADPKD, ADPCKD, renal failure, hypertension, impaired renal function, PKD1, PKD2, PKD3
