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Autosomal Recessive Polycystic Kidney Disease: Multimedia
Updated: Apr 24, 2008
Multimedia
 | Media file 1: Autosomal recessive polycystic kidney disease (ARPKD). Abdominal radiograph demonstrates bilateral flank masses in a 3-day-old boy with ARPKD. |
 | Media file 2: Autosomal recessive polycystic kidney disease (ARPKD). Excretory urogram of the same patient as in Image 1 demonstrates excretion into the bilaterally massively enlarged kidneys (arrows), with distorted pelvocalyceal systems and the vague suggestion of striated nephrograms. |
 | Media file 3: Autosomal recessive polycystic kidney disease (ARPKD). Axial nonenhanced CT scan of a 1-day-old boy with ARPKD shows massively enlarged, hypoattenuating kidneys (K) that occupy most of the abdominal area. |
 | Media file 4: Autosomal recessive polycystic kidney disease (ARPKD). Obstetric sonogram demonstrates massively enlarged kidneys (arrows) in this fetus with ARPKD. The kidneys occupy most of the abdomen. A segment of the fetal spine (S) is seen dorsally. On this sonogram, there is no evidence of oligohydramnios. |
 | Media file 5: Autosomal recessive polycystic kidney disease (ARPKD). Coronal image of the kidneys from the same study as in Image 4. The poles of the enlarged kidney are marked by the cursors of the electronic calipers used to measure the length of the kidneys. |
 | Media file 6: Autosomal recessive polycystic kidney disease (ARPKD). Sagittal sonogram through the enlarged right kidney (arrows) of a 1-day-old boy with ARPKD. There is echogenic parenchyma with loss of the normal hypoechoic medullary pyramids and loss of the corticomedullary differentiation. Note that the kidney contour is regular without focal masses. |
 | Media file 7: Autosomal recessive polycystic kidney disease (ARPKD). Image from the same patient shown in Image 6. Oblique sonographic image through the liver (L), gallbladder (G), and right kidney (K) demonstrates a kidney that is more echogenic than the liver, without hypoechoic medullary pyramids. |
 | Media file 8: Autosomal recessive polycystic kidney disease (ARPKD). Sonogram through the long axis of the left kidney. Arrowheads and electronic calipers mark the contour of the kidney. This image is of the same patient seen in Images 6-7. It demonstrates an enlarged echogenic kidney with a discrete hypoechoic cyst (arrow). |
 | Media file 9: Autosomal recessive polycystic kidney disease (ARPKD). Sagittal sonogram in a newborn girl with ARPKD shows a massively enlarged right kidney (arrowheads) that measures 10.2 cm in length. They kidney is echogenic with loss of the normal corticomedullary junction. |
 | Media file 10: Autosomal recessive polycystic kidney disease (ARPKD). Transaxial section through the same kidney (arrowheads) as in Image 9 demonstrates a very echogenic kidney with loss of the corticomedullary junction. Foci of intense echogenicity (arrows) may be due to the acoustic interfaces at the walls of tiny cysts or to focal renal calcification. |
 | Media file 11: Autosomal recessive polycystic kidney disease (ARPKD). Sagittal sonogram through the kidney of a newborn boy with ARPKD and pulmonary hypoplasia demonstrates a hypoechoic rim along the periphery of the kidney (arrows). |
 | Media file 12: Autosomal recessive polycystic kidney disease (ARPKD). Sagittal sonogram through the other kidney of the newborn shown in Image 11 reveals echogenic pyramids (arrows) that mimic medullary nephrocalcinosis. |
 | Media file 13: Autosomal recessive polycystic kidney disease (ARPKD). Sagittal sonogram of the 10.6-cm, elongated left kidney of the newborn girl shown in Images 9-10 demonstrates an echogenic kidney with a discrete hypoechoic cyst (arrow). |
 | Media file 14: Autosomal recessive polycystic kidney disease (ARPKD). Hepatic sonogram of a child with ARPKD demonstrates both tubular and round dilated hepatic ducts (arrows). |
 | Media file 15: Autosomal recessive polycystic kidney disease (ARPKD). Image of the same patient seen in Image 14 demonstrates a nodular protrusion of tissue into a dilated hepatic duct (arrow). |
More on Autosomal Recessive Polycystic Kidney Disease |
| Overview: Autosomal Recessive Polycystic Kidney Disease |
| Imaging: Autosomal Recessive Polycystic Kidney Disease |
| Follow-up: Autosomal Recessive Polycystic Kidney Disease |
 Multimedia: Autosomal Recessive Polycystic Kidney Disease |
| References |
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References
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Further Reading
Keywords
autosomal recessive polycystic kidney disease, ARPKD, PDK, infantile polycystic kidney disease, polycystic disease of the newborn, hamartomatous form of polycystic kidney disease, polycystic kidney disease, Potter type I, chromosome 6, PKHD1, perinatal ARPKD, neonatal ARPKD, infantile ARPKD, juvenile ARPKD
