eMedicine Specialties > Radiology > Musculoskeletal

Osteochondroma and Osteochondromatosis: Multimedia

Author: Ali Nawaz Khan, MBBS, FRCS, FRCP, FRCR, Consultant Radiologist and Honorary Professor, North Manchester General Hospital Pennine Acute NHS Trust, UK
Coauthor(s): Mohammed Jassim Al-Salman, MBBS, Consulting Radiologist, King Abdul Aziz Medical City, National Guard Hospital; Sumaira MacDonald, MBChB, PhD, MRCP, FRCR, Lecturer, Sheffield University Medical School; Endovascular Fellow, Sheffield Vascular Institute
Contributor Information and Disclosures

Updated: Oct 19, 2009

Multimedia

Plain radiograph of the cervical spine shows a so...Media file 1: Plain radiograph of the cervical spine shows a solitary osteochondroma of the posterior elements of C6.
Plain radiograph of the cervical spine shows a so...

Plain radiograph of the cervical spine shows a solitary osteochondroma of the posterior elements of C6.

Radiographs of both hands of 36-year-old man show...Media file 2: Radiographs of both hands of 36-year-old man show multiple osteochondromas involving the radii right distal fibula, metacarpals, and phalanges. Note the large osteochondroma involving the terminal phalanx of the right index finger.
Radiographs of both hands of 36-year-old man show...

Radiographs of both hands of 36-year-old man show multiple osteochondromas involving the radii right distal fibula, metacarpals, and phalanges. Note the large osteochondroma involving the terminal phalanx of the right index finger.

Plain radiograph of the pelvis in a 41-year-old w...Media file 3: Plain radiograph of the pelvis in a 41-year-old woman shows multiple osteochondromas affecting the left transverse process of L5, the iliac blades, the superior pubic rami, the ischial spines, and the femoral necks. Note the modeling deformity of the femoral necks and the narrowing of the pelvic inlet as a result of osteochondromas. Several reports have described osteochondromas interfering with normal vaginal birth in pregnancy and leading to a higher rate of Cesarean deliveries.
Plain radiograph of the pelvis in a 41-year-old w...

Plain radiograph of the pelvis in a 41-year-old woman shows multiple osteochondromas affecting the left transverse process of L5, the iliac blades, the superior pubic rami, the ischial spines, and the femoral necks. Note the modeling deformity of the femoral necks and the narrowing of the pelvic inlet as a result of osteochondromas. Several reports have described osteochondromas interfering with normal vaginal birth in pregnancy and leading to a higher rate of Cesarean deliveries.

Multiple osteochondromatosis. Plain radiograph of...Media file 4: Multiple osteochondromatosis. Plain radiograph of the lower limbs of a 10-year-old boy with a family history of hereditary multiple exostoses shows widening of the lower femoral metaphyses and osteochondroma involving the upper fibulae and tibia.
Multiple osteochondromatosis. Plain radiograph of...

Multiple osteochondromatosis. Plain radiograph of the lower limbs of a 10-year-old boy with a family history of hereditary multiple exostoses shows widening of the lower femoral metaphyses and osteochondroma involving the upper fibulae and tibia.

Solitary osteochondroma. Radiograph of 24-year-ol...Media file 5: Solitary osteochondroma. Radiograph of 24-year-old woman who presented with a hard, palpable mass on the medial aspect of the upper calf. A bulbous, pedunculated osteochondroma arising from the medial side of the upper tibial diaphysis and pointing away from the metaphysis is noted. The patient reported no history of hereditary multiple exostoses.
Solitary osteochondroma. Radiograph of 24-year-ol...

Solitary osteochondroma. Radiograph of 24-year-old woman who presented with a hard, palpable mass on the medial aspect of the upper calf. A bulbous, pedunculated osteochondroma arising from the medial side of the upper tibial diaphysis and pointing away from the metaphysis is noted. The patient reported no history of hereditary multiple exostoses.

Multiple osteochondromatosis. Fractures of the lo...Media file 6: Multiple osteochondromatosis. Fractures of the lower tibia and fibula as a complication of hereditary multiple exostoses. Note the osteochondromas involving the calcaneum and the upper and lower portions of the tibia and fibula.
Multiple osteochondromatosis. Fractures of the lo...

Multiple osteochondromatosis. Fractures of the lower tibia and fibula as a complication of hereditary multiple exostoses. Note the osteochondromas involving the calcaneum and the upper and lower portions of the tibia and fibula.

Multiple osteochondromatosis. Radiograph of the p...Media file 7: Multiple osteochondromatosis. Radiograph of the pelvis in a 28-year-old woman known to have hereditary multiple exostoses who presented with a painful swelling of the left buttock. Note the multiple osteochondromas and fragmentation of the osteochondroma arising from the left anterior iliac crest (see Image 8 in Multimedia).
Multiple osteochondromatosis. Radiograph of the p...

Multiple osteochondromatosis. Radiograph of the pelvis in a 28-year-old woman known to have hereditary multiple exostoses who presented with a painful swelling of the left buttock. Note the multiple osteochondromas and fragmentation of the osteochondroma arising from the left anterior iliac crest (see Image 8 in Multimedia).

Multiple osteochondromatosis. Nonenhanced, axial ...Media file 8: Multiple osteochondromatosis. Nonenhanced, axial computed tomography (CT) scan through the pelvis (same patient as in Image 7 in Multimedia). Note the fragmentation of the osteochondroma and the considerable soft-tissue mass. Histology of the resected specimen revealed a low-grade chondrosarcoma.
Multiple osteochondromatosis. Nonenhanced, axial ...

Multiple osteochondromatosis. Nonenhanced, axial computed tomography (CT) scan through the pelvis (same patient as in Image 7 in Multimedia). Note the fragmentation of the osteochondroma and the considerable soft-tissue mass. Histology of the resected specimen revealed a low-grade chondrosarcoma.

Osteochondroma with malignant degeneration. Plain...Media file 9: Osteochondroma with malignant degeneration. Plain radiograph of the pelvis in a 68-year-old woman who presented with a painful lump over the left greater trochanter. Note the sclerotic exostosis arising from the left greater trochanter. Technetium-99m (99mTc) diphosphonate scintigram (left) shows intense activity in the region of the left greater trochanter. At surgery (right), the lesion was diagnosed as a low-grade chondrosarcoma superimposed on an osteochondroma.
Osteochondroma with malignant degeneration. Plain...

Osteochondroma with malignant degeneration. Plain radiograph of the pelvis in a 68-year-old woman who presented with a painful lump over the left greater trochanter. Note the sclerotic exostosis arising from the left greater trochanter. Technetium-99m (99mTc) diphosphonate scintigram (left) shows intense activity in the region of the left greater trochanter. At surgery (right), the lesion was diagnosed as a low-grade chondrosarcoma superimposed on an osteochondroma.

More on Osteochondroma and Osteochondromatosis

Overview: Osteochondroma and Osteochondromatosis
Imaging: Osteochondroma and Osteochondromatosis
Follow-up: Osteochondroma and Osteochondromatosis
Multimedia: Osteochondroma and Osteochondromatosis
References
Further Reading

References

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Further Reading

Related eMedicine topics

Dysplasia Epiphysealis Hemimelica

Solitary Osteochondroma

Bone Metastases

Clinical guidelines

ACR Appropriateness Criteria® chronic hip pain
Taljanovic M, Daffner RH, Weissman BN, Bennett DL, Bleba JS, Jacobson JA, Morrison WB, Resnik CS, Roberts CC, Schweitzer ME, Seeger LL, Wise JN, Payne WK, Expert Panel on Musculoskeletal Imaging. ACR Appropriateness Criteria® chronic hip pain. [online publication]. Reston (VA): American College of Radiology (ACR); 2008. 8 p. [78 references]

Clinical trials

The Health Related Quality of Life in Patients With Hereditary Multiple Exostoses

Gene Mutations and Orthopaedic Symptoms Correlation of Multiple Hereditary Exostoses: Multicentre Project

Keywords

osteochondroma, osteochondromatosis, hereditary multiple exostoses, HME, multiple osteocartilaginous exostoses, diaphyseal achalasia, diaphysial achalasia, multiple hereditary osteochondromata, multiple congenital osteochondromata, diaphyseal aclasis, diaphysial aclasis, chondral osteogenic dysplasia of direction, chondral osteoma, deforming chondrodysplasia, dyschondroplasia exostosing disease, exostotic dysplasia, multiple osteomatoses osteogenic disease, familial bony spurs, metaphyseal spurs, multiple epiphyseal dysplasia, dysplasia epiphysealis hemimelica, Trevor disease, Trevor's disease

Contributor Information and Disclosures

Author

Ali Nawaz Khan, MBBS, FRCS, FRCP, FRCR, Consultant Radiologist and Honorary Professor, North Manchester General Hospital Pennine Acute NHS Trust, UK
Ali Nawaz Khan, MBBS, FRCS, FRCP, FRCR is a member of the following medical societies: American Association for the Advancement of Science, American Institute of Ultrasound in Medicine, British Medical Association, British Society of Interventional Radiology, Royal College of Physicians, Royal College of Physicians and Surgeons of the United States, Royal College of Radiologists, and Royal College of Surgeons of England
Disclosure: Nothing to disclose.

Coauthor(s)

Mohammed Jassim Al-Salman, MBBS, Consulting Radiologist, King Abdul Aziz Medical City, National Guard Hospital
Disclosure: Nothing to disclose.

Sumaira MacDonald, MBChB, PhD, MRCP, FRCR, Lecturer, Sheffield University Medical School; Endovascular Fellow, Sheffield Vascular Institute
Sumaira MacDonald, MBChB, PhD, MRCP, FRCR is a member of the following medical societies: British Medical Association, Royal College of Physicians, and Royal College of Radiologists
Disclosure: Nothing to disclose.

Medical Editor

Michael A Bruno, MD, Associate Professor, Departments of Radiology and Medicine, Pennsylvania State University College of Medicine; Director, Radiology Quality Management Services, Milton S Hershey Medical Center, Pennsylvania State University College of Medicine
Michael A Bruno, MD is a member of the following medical societies: American College of Radiology, American Roentgen Ray Society, Association of University Radiologists, Radiological Society of North America, Society of Nuclear Medicine, and Society of Skeletal Radiology
Disclosure: Nothing to disclose.

Pharmacy Editor

Bernard D Coombs, MB, ChB, PhD, Consulting Staff, Department of Specialist Rehabilitation Services, Hutt Valley District Health Board, New Zealand
Disclosure: Nothing to disclose.

Managing Editor

Theodore E Keats, MD, Professor, Departments of Radiology and Orthopedics, University of Virginia School of Medicine
Disclosure: Nothing to disclose.

CME Editor

Robert M Krasny, MD, Resolution Imaging Medical Corporation
Robert M Krasny, MD is a member of the following medical societies: American Roentgen Ray Society and Radiological Society of North America
Disclosure: Nothing to disclose.

Chief Editor

Felix S Chew, MD, MBA, EdM, Professor, Department of Radiology, Vice Chairman for Radiology Informatics, Section Head of Musculoskeletal Radiology, University of Washington
Felix S Chew, MD, MBA, EdM is a member of the following medical societies: American Roentgen Ray Society, Association of University Radiologists, and Radiological Society of North America
Disclosure: Nothing to disclose.

 
 
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