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Hemophilia, Musculoskeletal Complications: Multimedia
Updated: Mar 21, 2008
Multimedia
 | Media file 1: Knee radiograph in a 37-year-old man with hemophilia. This image shows moderate factor IX hemophilia. The bony excrescence on the lateral side of the femur is a hemophilic pseudotumor. |
 | Media file 2: Radiograph of the lower extremity of the 3-year-old daughter of the patient in Image 1. This image shows mild factor IX hemophilia with talar tilt. The girl not only inherited 1 diseased X chromosome from her father but also has Turner (XO) syndrome. The child's only X chromosome had the hemophilia gene. |
 | Media file 3: Magnetic resonance image from a patient with hemophilia. This image shows dark, synovial masses that erode the cartilage and produce subchondral cysts (arrows). |
 | Media file 4: Anteroposterior radiograph from a patient with hemophilia. This image demonstrates hemarthrosis with hemosiderin deposition. Note the irregularity of the articular surfaces and the presence of subchondral sclerosis with cysts. Image courtesy of Javier Beltran, MD. |
 | Media file 5: Lateral radiograph from the same patient as in Image 4. This image shows a large hemarthrosis that is distending the suprapatellar recess. Image courtesy of Javier Beltran, MD. |
 | Media file 6: Axial gradient-echo magnetic resonance image from a patient with hemophilia. This image demonstrates hemosiderin deposition in the synovium as hypointense material that outlines the joint capsule. Image courtesy of Javier Beltran, MD. |
 | Media file 7: Radiograph in a patient with hemophilia. This image depicts a pseudotumor that is deforming the cortex of the femur (arrow). Other ossified masses in the soft tissues (arrowheads) are probably soft-tissue pseudotumors. |
 | Media file 8: Sagittal magnetic resonance image of the ankle joint in a patient with hemophilia. This image shows extension of abnormal joint fluid from the ankle joint into the subtalar joint. Note the dark hemosiderin posterior to the subtalar fluid (arrow). |
 | Media file 9: Computed tomography scan of the pelvis in a patient with hemophilia. This image demonstrates a giant pseudotumor (a large expansile lytic lesion that involves the right iliac bone and extends into the sacrum, with inhomogeneous internal attenuation). Image courtesy of Javier Beltran, MD. |
 | Media file 10: Axial T2-weighted magnetic resonance image of the pelvis. This image demonstrates a large pseudotumor of the pelvis with sacral extension. Image courtesy of Javier Beltran, MD. |
 | Media file 11: Lateral elbow radiograph in a patient with hemophilia. This image shows an opaque joint effusion due to the presence of iron in the synovium (arrows). |
 | Media file 12: Radiograph of the ankle in a 20-year-old patient with hemophilia. This image shows the development of osteonecrosis (arrow) in the talar dome. |
 | Media file 13: Sagittal T2-weighted magnetic resonance image of the lower extremity in a patient with hemophilia. This image demonstrates hemosiderin-laden synovium with low signal intensity that outlines the capsule of the tibiotalar joint. Image courtesy of Javier Beltran, MD. |
 | Media file 14: Radiograph of the shoulder of a 35-year-old man with hemophilia. This image shows advanced degenerative joint disease. The infiltrate in the lung is due to a fungal infection as a complication of the patient's positive HIV. |
 | Media file 15: Radiograph of the leg in a patient with hemophilia. This image depicts stage III joint disease, as determined by the Arnold-Hilgartner classification. |
 | Media file 16: Radiograph of the leg in a patient with hemophilia. This image depicts stage IV joint disease, as determined by the Arnold-Hilgartner classification. |
 | Media file 17: Coronal T2-weighted magnetic resonance image of the knee in a patient with hemophilia. This image demonstrates pseudotumor of the knee, a lytic lesion in the lateral femoral condyle, as well as the characteristic manifestations of hemosiderin deposition in the knee joint and the subchondral cystic changes in the medial femoral condyle. Image courtesy of Javier Beltran, MD. |
More on Hemophilia, Musculoskeletal Complications |
| Overview: Hemophilia, Musculoskeletal Complications |
| Imaging: Hemophilia, Musculoskeletal Complications |
| Follow-up: Hemophilia, Musculoskeletal Complications |
 Multimedia: Hemophilia, Musculoskeletal Complications |
| References |
| « Previous Page |
References
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Further Reading
Keywords
hemophilic arthropathy, hemophilic soft-tissue bleeding, pseudotumor, hemophilia A, classic hemophilia, factor VIII deficiency, hemophilia B, Christmas disease, factor IX deficiency, bleeding disorder, Arnold-Hilgartner staging/classification, hemarthrosis
