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Uterus, Mullerian Duct Abnormalities: Multimedia

Author: Ibrahim Syed, MD,, Clinical Assistant Professor of Diagnostic Radiology, Volunteer Faculty, University of Toledo Medical Center; Consulting Staff Radiologist, Vista Health System, Waukegan, IL
Coauthor(s): Hero K Hussain, MD, FRCR, Associate Professor of Radiology, Director of Clinical MR Services, Chief of Body MRI Section, Department of Radiology, University of Michigan Health Service; William Weadock, MD, Associate Professor of Radiology, Department of Radiology, University of Michigan Medical Center; James Ellis, MD, Professor of Radiology and Urology, University of Michigan
Contributor Information and Disclosures

Updated: Oct 16, 2009

Multimedia

Uterus, müllerian duct abnormalities. This w...Media file 1: Uterus, müllerian duct abnormalities. This was difficult to differentiate as septate or bicornuate uterus using hysterosalpingography. It was a surgically proven case of bicornuate uterus.
Uterus, müllerian duct abnormalities. This w...

Uterus, müllerian duct abnormalities. This was difficult to differentiate as septate or bicornuate uterus using hysterosalpingography. It was a surgically proven case of bicornuate uterus.

<A name=target2></a>Uterus, müllerian duct a...Media file 2: Uterus, müllerian duct abnormalities. Surgically proven case of bicornuate uterus. Correct diagnosis may be suggested based on hysterosalpingography findings, which are, most notably, the widened intercornual distance (>4 cm) and the widened intercornual angle (>60°).
<A name=target2></a>Uterus, müllerian duct a...

Uterus, müllerian duct abnormalities. Surgically proven case of bicornuate uterus. Correct diagnosis may be suggested based on hysterosalpingography findings, which are, most notably, the widened intercornual distance (>4 cm) and the widened intercornual angle (>60°).

Uterus, müllerian duct abnormalities. T-shap...Media file 3: Uterus, müllerian duct abnormalities. T-shaped uterus. Classic configuration of the uterine cavity in a typical diethylstilbestrol-exposed uterus (American Fertility Society class VII). Uteri are typically hypoplastic. In this patient, no maternal history of diethylstilbestrol exposure was found.
Uterus, müllerian duct abnormalities. T-shap...

Uterus, müllerian duct abnormalities. T-shaped uterus. Classic configuration of the uterine cavity in a typical diethylstilbestrol-exposed uterus (American Fertility Society class VII). Uteri are typically hypoplastic. In this patient, no maternal history of diethylstilbestrol exposure was found.

Uterus, müllerian duct abnormalities. T2 fas...Media file 4: Uterus, müllerian duct abnormalities. T2 fast spin-echo MRI image of septate uterus acquired in the oblique plane along the long axis of the uterus. Note that the outer fundal contour (superior border) is flat or slightly concave, which is sufficient to make the diagnosis of septate uterus.
Uterus, müllerian duct abnormalities. T2 fas...

Uterus, müllerian duct abnormalities. T2 fast spin-echo MRI image of septate uterus acquired in the oblique plane along the long axis of the uterus. Note that the outer fundal contour (superior border) is flat or slightly concave, which is sufficient to make the diagnosis of septate uterus.

Uterus, müllerian duct abnormalities. Septat...Media file 5: Uterus, müllerian duct abnormalities. Septate uterus. Note that a longer septum divides the uterine cavity. Outer fundal contour is flat.
Uterus, müllerian duct abnormalities. Septat...

Uterus, müllerian duct abnormalities. Septate uterus. Note that a longer septum divides the uterine cavity. Outer fundal contour is flat.

Uterus, müllerian duct abnormalities. MRI im...Media file 6: Uterus, müllerian duct abnormalities. MRI image of septate uterus. The patient has a thin, fibrous septum that cannot be resolved distally at the fundus. More importantly, the outer fundal contour remains convex, thus excluding a bicornuate uterus.
Uterus, müllerian duct abnormalities. MRI im...

Uterus, müllerian duct abnormalities. MRI image of septate uterus. The patient has a thin, fibrous septum that cannot be resolved distally at the fundus. More importantly, the outer fundal contour remains convex, thus excluding a bicornuate uterus.

Uterus, m<FONT style="FONT-FAMILY: Georgia, Times...Media file 7: Uterus, müllerian duct abnormalities. Bicornuate uterus. The midline uterine external fundal cleft (superior border) has a depression greater than 1 cm, excluding septate uterus from the differential diagnosis. This image is of bicornuate bicollis, since 2 cervices are present. Bicornuate uterus is distinguished from didelphys uterus because some degree of fusion has occurred between the lower uterine segments (ie, they are fused, although the cavities are not communicating).
Uterus, m<FONT style="FONT-FAMILY: Georgia, Times...

Uterus, müllerian duct abnormalities. Bicornuate uterus. The midline uterine external fundal cleft (superior border) has a depression greater than 1 cm, excluding septate uterus from the differential diagnosis. This image is of bicornuate bicollis, since 2 cervices are present. Bicornuate uterus is distinguished from didelphys uterus because some degree of fusion has occurred between the lower uterine segments (ie, they are fused, although the cavities are not communicating).

Uterus, müllerian duct abnormalities. Didelp...Media file 8: Uterus, müllerian duct abnormalities. Didelphys uterus. Complete separation and full development of both müllerian ducts is noted. (a) Two vaginas and 2 cervices; (b) 2 distinct cervices; (c) 2 uterine horns are widely splayed; (d) cross section of uterine bodies and cervices.
Uterus, müllerian duct abnormalities. Didelp...

Uterus, müllerian duct abnormalities. Didelphys uterus. Complete separation and full development of both müllerian ducts is noted. (a) Two vaginas and 2 cervices; (b) 2 distinct cervices; (c) 2 uterine horns are widely splayed; (d) cross section of uterine bodies and cervices.

Uterus, müllerian duct abnormalities. Unicor...Media file 9: Uterus, müllerian duct abnormalities. Unicornuate uterus. Patient has full development of a single uterine horn and a normal-appearing cervix. This anomaly was one of many in this patient with Goldenhar syndrome.
Uterus, müllerian duct abnormalities. Unicor...

Uterus, müllerian duct abnormalities. Unicornuate uterus. Patient has full development of a single uterine horn and a normal-appearing cervix. This anomaly was one of many in this patient with Goldenhar syndrome.

Uterus, müllerian duct abnormalities. Normal...Media file 10: Uterus, müllerian duct abnormalities. Normal uterus. Note a single uterine cavity and flat or convex outer fundal contour.
Uterus, müllerian duct abnormalities. Normal...

Uterus, müllerian duct abnormalities. Normal uterus. Note a single uterine cavity and flat or convex outer fundal contour.

Uterus, müllerian duct abnormalities. Septat...Media file 11: Uterus, müllerian duct abnormalities. Septate uterus. Midline septum can be of variable length and can be muscular or fibrous. In the diagram, the septum is shown as an extension of the uterine myometrium.
Uterus, müllerian duct abnormalities. Septat...

Uterus, müllerian duct abnormalities. Septate uterus. Midline septum can be of variable length and can be muscular or fibrous. In the diagram, the septum is shown as an extension of the uterine myometrium.

Uterus, müllerian duct abnormalities. Septat...Media file 12: Uterus, müllerian duct abnormalities. Septate uterus. The midline septum can extend for a variable length and can be muscular or fibrous. In the diagram, the septum is thin and linear as expected in the fibrous type. Since the composition of the septum varies, whether it is composed of muscle or fibrous tissue is not a means to distinguish septate from other forms of uterine anomalies.
Uterus, müllerian duct abnormalities. Septat...

Uterus, müllerian duct abnormalities. Septate uterus. The midline septum can extend for a variable length and can be muscular or fibrous. In the diagram, the septum is thin and linear as expected in the fibrous type. Since the composition of the septum varies, whether it is composed of muscle or fibrous tissue is not a means to distinguish septate from other forms of uterine anomalies.

<A name=target13></a>Uterus, müllerian duct ...Media file 13: Uterus, müllerian duct abnormalities. Bicornuate uterus. Note the partial fusion of the lower uterine segment and persistently separated upper uterine segments. Of key importance is the prominent fundal cleft (>1 cm), which distinguishes the anomaly from septate uterus.
<A name=target13></a>Uterus, müllerian duct ...

Uterus, müllerian duct abnormalities. Bicornuate uterus. Note the partial fusion of the lower uterine segment and persistently separated upper uterine segments. Of key importance is the prominent fundal cleft (>1 cm), which distinguishes the anomaly from septate uterus.

Uterus, müllerian duct abnormalities. Unicor...Media file 14: Uterus, müllerian duct abnormalities. Unicornuate uterus. Note the failure of the development of one half of the uterus. This form may be associated with a rudimentary horn arising from the contralateral müllerian duct.
Uterus, müllerian duct abnormalities. Unicor...

Uterus, müllerian duct abnormalities. Unicornuate uterus. Note the failure of the development of one half of the uterus. This form may be associated with a rudimentary horn arising from the contralateral müllerian duct.

Uterus, müllerian duct abnormalities. Didelp...Media file 15: Uterus, müllerian duct abnormalities. Didelphys uterus. Note the complete separation but full development of each müllerian duct.
Uterus, müllerian duct abnormalities. Didelp...

Uterus, müllerian duct abnormalities. Didelphys uterus. Note the complete separation but full development of each müllerian duct.

Uterus, müllerian duct abnormalities. Arcuat...Media file 16: Uterus, müllerian duct abnormalities. Arcuate uterus. Mild thickening of the midline fundal myometrium resulting in fundal cavity indentation but normal outer fundal contour. Some authors consider it a normal variant. It is not associated with an increased risk of obstetric/gynecologic complications.
Uterus, müllerian duct abnormalities. Arcuat...

Uterus, müllerian duct abnormalities. Arcuate uterus. Mild thickening of the midline fundal myometrium resulting in fundal cavity indentation but normal outer fundal contour. Some authors consider it a normal variant. It is not associated with an increased risk of obstetric/gynecologic complications.

Uterus, müllerian duct abnormalities. Diethy...Media file 17: Uterus, müllerian duct abnormalities. Diethylstilbestrol-exposed uterus. Myometrial hypertrophy results in a T-shaped uterine cavity and cavity irregularity, which is pathognomonic for the anomaly. Typically, the uteri are hypoplastic.
Uterus, müllerian duct abnormalities. Diethy...

Uterus, müllerian duct abnormalities. Diethylstilbestrol-exposed uterus. Myometrial hypertrophy results in a T-shaped uterine cavity and cavity irregularity, which is pathognomonic for the anomaly. Typically, the uteri are hypoplastic.

More on Uterus, Mullerian Duct Abnormalities

Overview: Uterus, Mullerian Duct Abnormalities
Imaging: Uterus, Mullerian Duct Abnormalities
Multimedia: Uterus, Mullerian Duct Abnormalities
References
Further Reading

References

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Keywords

müllerian duct abnormalities of the uterus, uterine, female reproductive tract, müllerian congenital uterine anomalies, müllerian anomalies, müllerian duct anomalies, Mayer-Rokitansky-Kuster-Hauser syndrome, female reproductive tract developmental abnormalities, paramesonephric developmental abnormalities

Contributor Information and Disclosures

Author

Ibrahim Syed, MD,, Clinical Assistant Professor of Diagnostic Radiology, Volunteer Faculty, University of Toledo Medical Center; Consulting Staff Radiologist, Vista Health System, Waukegan, IL
Ibrahim Syed, MD, is a member of the following medical societies: American College of Radiology, American Medical Association, American Roentgen Ray Society, Illinois State Medical Society, and Radiological Society of North America
Disclosure: Nothing to disclose.

Coauthor(s)

Hero K Hussain, MD, FRCR, Associate Professor of Radiology, Director of Clinical MR Services, Chief of Body MRI Section, Department of Radiology, University of Michigan Health Service
Hero K Hussain, MD, FRCR is a member of the following medical societies: American Roentgen Ray Society, International Society for Magnetic Resonance in Medicine, Radiological Society of North America, and Society of Uroradiology
Disclosure: Nothing to disclose.

William Weadock, MD, Associate Professor of Radiology, Department of Radiology, University of Michigan Medical Center
William Weadock, MD is a member of the following medical societies: American Medical Association, American Roentgen Ray Society, and Radiological Society of North America
Disclosure: Nothing to disclose.

James Ellis, MD, Professor of Radiology and Urology, University of Michigan
James Ellis, MD is a member of the following medical societies: Alpha Omega Alpha, American College of Radiology, American Roentgen Ray Society, Association of University Radiologists, Radiological Society of North America, and Society of Uroradiology
Disclosure: Nuance Inc. Honoraria Consulting; GE Healthcare None Unpaid research investigator; Legal firm representing GE Healthcare Consulting fee Consulting

Medical Editor

Christopher L Sistrom, MD, Associate Chair for Research, Assistant Professor, Department of Radiology, University of Florida School of Medicine
Christopher L Sistrom, MD is a member of the following medical societies: Alpha Omega Alpha, American College of Radiology, American Institute of Ultrasound in Medicine, American Roentgen Ray Society, Association of University Radiologists, Phi Beta Kappa, and Radiological Society of North America
Disclosure: Nothing to disclose.

Pharmacy Editor

Bernard D Coombs, MB, ChB, PhD, Consulting Staff, Department of Specialist Rehabilitation Services, Hutt Valley District Health Board, New Zealand
Disclosure: Nothing to disclose.

Managing Editor

Karen L Reuter, MD, FACR, Professor, Department of Radiology, Lahey Clinic Medical Center
Karen L Reuter, MD, FACR is a member of the following medical societies: American Association for Women Radiologists, American College of Radiology, American Institute of Ultrasound in Medicine, American Roentgen Ray Society, and Radiological Society of North America
Disclosure: Nothing to disclose.

CME Editor

Robert M Krasny, MD, Resolution Imaging Medical Corporation
Robert M Krasny, MD is a member of the following medical societies: American Roentgen Ray Society and Radiological Society of North America
Disclosure: Nothing to disclose.

Chief Editor

Eugene C Lin, MD, Consulting Radiologist, Virginia Mason Medical Center; Clinical Assistant Professor of Radiology, University of Washington School of Medicine
Eugene C Lin, MD is a member of the following medical societies: American College of Nuclear Medicine, American College of Radiology, Radiological Society of North America, and Society of Nuclear Medicine
Disclosure: Nothing to disclose.

 
 
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