eMedicine Specialties > Radiology > Pediatrics
Dandy-Walker Malformation: Multimedia
Updated: Sep 11, 2009
Multimedia
 | Media file 1: A sagittal T1-weighted magnetic resonance imaging (MRI) scan in a 5-year-old girl (also see Images 2-3 in Multimedia Section) shows a large posterior fossa cyst elevating the torcular herophili and sinus rectus (short arrow). The hypoplastic vermis is everted over the posterior fossa cyst (long arrow). The cerebellar hemispheres and brainstem (b) are hypoplastic. Thinned occipital squama is seen (arrowheads). |
 | Media file 2: An axial T2-weighted MRI (also see Image 1 and Image 3, in Multimedia Section) scan that shows hydrocephalus, a large cerebrospinal fluid cyst in the posterior fossa, thinned occipital bone (arrows), and hypoplastic cerebellar hemispheres with a winged appearance (c). |
 | Media file 3: An axial T1-weighted MRI (also see Images 1-2, in Multimedia Section) scan showing ventriculomegaly and a superiorly displaced posterior fossa cyst. |
 | Media file 4: This sagittal T1-weighted MRI scan in an 11-day-old boy (also see Image 5 in Multimedia Section) shows agenesis of the corpus callosum, a hypoplastic brainstem (b), elevation of the torcular herophili (lambdoid-torcular inversion, large arrow), a large fourth ventricle, and a markedly hypoplastic vermis that is rotated superiorly (small arrow). |
 | Media file 5: An axial T1-weighted MRI (also see Image 4, in Multimedia Section) showing an elevated, anteriorly displaced torcular herophili (arrow) and a superiorly displaced posterior fossa cyst. |
 | Media file 6: An axial computed tomography (CT) scan in a 7-year-old girl with hydrocephalus showing a large cerebrospinal fluid cyst in the posterior fossa and hypoplastic cerebellar hemispheres with a winged appearance (c). |
 | Media file 7: An axial CT scan in a 1-day-old boy that shows a large posterior fossa cyst, separation of the lambdoid sutures (large arrows), and concavity of the petrous ridges (small arrows). |
 | Media file 8: This sagittal T1-weighted MRI shows agenesis of the corpus callosum and a hypoplastic inferior vermis in a 13-year-old girl with thoracal scoliosis and Dandy-Walker variant. The fourth ventricle is slightly enlarged, but the posterior fossa typically is normal in size. |
 | Media file 9: This sagittal T1-weighted MRI shows a large retrocerebellar cerebrospinal fluid collection and a normal fourth ventricle and vermis in a patient with mega cisterna magna in Dandy-Walker malformation. |
 | Media file 10: A posterior fossa arachnoid cyst in a 15-month-old girl with a lumbar pilonidal sinus. The sagittal T1-weighted MRI shows a large posterior fossa cyst that is compressing the cerebellar hemispheres, vermis, fourth ventricle (arrow), and brainstem. |
 | Media file 11: Joubert syndrome in an 8-month-old boy. The axial CT scan obtained near the pontomesencephalic junction shows a batwing configuration of the fourth ventricle and unusual definition of the superior cerebellar peduncles at this level (arrows). The vermis is dysgenetic, and the 2 cerebellar hemispheres appose each other in the midline. |
 | Media file 12: An in utero sonogram of Dandy-Walker malformation; note the abnormal cerebellar vermis in association with a posterior fossa cyst (arrow) and splaying of the cerebellar hemispheres. Image courtesy of Ecker et al. |
 | Media file 13: An antenatal sonogram that shows Dandy-Walker malformation (arrow) in a fetus (same patient as in Image 14 in Multimedia Section). Courtesy of Umit Aksoy, MD, Uludag University, Bursa, Turkey. |
 | Media file 14: An antenatal MRI showing Dandy-Walker malformation in a fetus (same patient as in Image 13 in Multimedia Section). Courtesy of Umit Aksoy, MD, Uludag University, Bursa, Turkey. |
 | Media file 15: A CT scan depicting Dandy-Walker malformation. |
 | Media file 16: An axial CT scan showing the sinus confluence (large arrow) and sinus transversus (small arrows) displaced superiorly in Dandy-Walker malformation (lambdoid-torcular inversion). |
More on Dandy-Walker Malformation |
| Overview: Dandy-Walker Malformation |
| Imaging: Dandy-Walker Malformation |
| Follow-up: Dandy-Walker Malformation |
 Multimedia: Dandy-Walker Malformation |
| References |
| Further Reading |
| « Previous Page |
References
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Further Reading
Related eMedicine topics
Arteriovenous Malformations
Atrioventricular Septal Defect, Complete
Management of Spina Bifida, Hydrocephalus and Shunts
Arachnoid Cyst
Ataxia with Identified Genetic and Biochemical Defects
Corpus Callosum, Agenesis
Clinical guidelines
ACR Appropriateness Criteria® ataxia. American College of Radiology - Medical Specialty Society. 1999 (revised 2006). 10 pages. NGC:005547
Clinical trials
Brain Development Research Program
Keywords
Dandy-Walker malformation, Dandy-Walker, Dandy-Walker syndrome, Dandy-Walker cyst, Dandy-Walker deformity, Dandy Walker, cerebellum, cerebellar disease, brain disease, central nervous system disease, Luschka-Magendie foramina atresia
