eMedicine Specialties > Otolaryngology and Facial Plastic Surgery > Congenital Malformations of the Head & Neck

Congenital Malformations, Nose: Multimedia

Author: Ted L Tewfik, MD, FRCS(C), Professor, Department of Otolaryngology, Director of Continuing Medical Education of Otolaryngology, McGill University Medical School; Director, Director of Professional Affairs of Otolaryngology, Department of Otolaryngology, Montreal Children's Hospital; Senior Staff, Montreal General Hospital and Royal Victoria Hospital
Coauthor(s): Fahad Al-Saab, MD, Staff Physician, Department of Otolaryngology Head and Neck Surgery, McGill University; Adi Yoskovitch, MD, MSc, Chief, Department of Otolaryngology - Head and Neck Surgery, Fleury Hospital, Canada
Contributor Information and Disclosures

Updated: Oct 21, 2008

Multimedia

A patient with a congenital nasal dermoid.Media file 1: A patient with a congenital nasal dermoid.
A patient with a congenital nasal dermoid.

A patient with a congenital nasal dermoid.

A patient with encephalocele.Media file 2: A patient with encephalocele.
A patient with encephalocele.

A patient with encephalocele.

This MRI depicts a dermoid. The dermoid is intrac...Media file 3: This MRI depicts a dermoid. The dermoid is intracranial but separate from the brain. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat. New York: Oxford UP; 1997, with permission).
This MRI depicts a dermoid. The dermoid is intrac...

This MRI depicts a dermoid. The dermoid is intracranial but separate from the brain. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat. New York: Oxford UP; 1997, with permission).

CT scan demonstrating encephalocele.Media file 4: CT scan demonstrating encephalocele.
CT scan demonstrating encephalocele.

CT scan demonstrating encephalocele.

The photograph shows a child with median nasal cl...Media file 5: The photograph shows a child with median nasal cleft. Note the marked hypertelorism and pronounced separation of the nostrils.
The photograph shows a child with median nasal cl...

The photograph shows a child with median nasal cleft. Note the marked hypertelorism and pronounced separation of the nostrils.

The photograph shows an infant with arhinia. (Fro...Media file 6: The photograph shows an infant with arhinia. (From Navarro-Vila et al, J Craniomaxillofac Surg 19:56, 1991, with permission).
The photograph shows an infant with arhinia. (Fro...

The photograph shows an infant with arhinia. (From Navarro-Vila et al, J Craniomaxillofac Surg 19:56, 1991, with permission).

This photograph shows an infant with epignathus. ...Media file 7: This photograph shows an infant with epignathus. Endotracheal intubation was essential to maintain the airway. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat, New York: Oxford UP; 1997, with permission).
This photograph shows an infant with epignathus. ...

This photograph shows an infant with epignathus. Endotracheal intubation was essential to maintain the airway. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat, New York: Oxford UP; 1997, with permission).

This plain radiograph of the epignathus in Pictur...Media file 8: This plain radiograph of the epignathus in Picture 7 depicts bone and teeth formation. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat, New York: Oxford UP; 1997, with permission).
This plain radiograph of the epignathus in Pictur...

This plain radiograph of the epignathus in Picture 7 depicts bone and teeth formation. (From TL Tewfik, VM Der Kaloustian, eds. Congenital Anomalies of the Ear, Nose and Throat, New York: Oxford UP; 1997, with permission).

This drawing shows soft tissue clefts in the Tess...Media file 9: This drawing shows soft tissue clefts in the Tessier classification system.
This drawing shows soft tissue clefts in the Tess...

This drawing shows soft tissue clefts in the Tessier classification system.

This drawing shows bone clefts in the Tessier cla...Media file 10: This drawing shows bone clefts in the Tessier classification system.
This drawing shows bone clefts in the Tessier cla...

This drawing shows bone clefts in the Tessier classification system.

More on Congenital Malformations, Nose

References

References

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  2. Broekman ML, Hoving EW, Kho KH, et al. Nasal encephalocele in a child with Beckwith-Wiedemann syndrome. J Neurosurg Pediatrics. Jun 2008;1(6):485-7. [Medline].

  3. Chiu HH, Hsu WC, Shih JC, et al. The EXIT (Ex Utero Intrapartum Treatment) Procedure. J Formos Med Assoc. Sep 2008;107(9):745-8. [Medline].

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  15. Sessions RB, Picken C. Congenital anomalies of the nose. In: Bailey BJ, ed. Head and Neck Surgery-Otolaryngology. 2nd ed. Philadelphia: Lippincott-Raven; 1998:1177-1185.

  16. Wardinsky TD, Pagon RA, Kropp RJ, et al. Nasal dermoid sinus cysts: association with intracranial extension and multiple malformations. Cleft Palate Craniofac J. Jan 1991;28(1):87-95. [Medline].

  17. Zeitouni AG, Shapiro RS. Congenital anomalies of the nose and anterior skull base. In: Tewfik TL, Der Kaloustian VM, eds. Congenital Anomalies of the Ear, Nose, and Throat. NY: Oxford University Press; 1997:189-200.

Further Reading

Keywords

nose, nose malformations, congenital malformations of the nose, gliomas, encephaloceles, nasal clefts, proboscis lateralis, arhinia, polyrrhinia, nasopharyngeal teratoma, epignathus

Contributor Information and Disclosures

Author

Ted L Tewfik, MD, FRCS(C), Professor, Department of Otolaryngology, Director of Continuing Medical Education of Otolaryngology, McGill University Medical School; Director, Director of Professional Affairs of Otolaryngology, Department of Otolaryngology, Montreal Children's Hospital; Senior Staff, Montreal General Hospital and Royal Victoria Hospital
Ted L Tewfik, MD, FRCS(C) is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American College of Surgeons, American Society of Pediatric Otolaryngology, Canadian Medical Association, Canadian Society of Otolaryngology-Head & Neck Surgery, Quebec Medical Association, and Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

Coauthor(s)

Fahad Al-Saab, MD, Staff Physician, Department of Otolaryngology Head and Neck Surgery, McGill University
Fahad Al-Saab, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery and Canadian Society of Otolaryngology-Head & Neck Surgery
Disclosure: Nothing to disclose.

Adi Yoskovitch, MD, MSc, Chief, Department of Otolaryngology - Head and Neck Surgery, Fleury Hospital, Canada
Adi Yoskovitch, MD, MSc is a member of the following medical societies: American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, Canadian Academy of Facial Plastic and Reconstructive Surgery, and Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

Medical Editor

Mimi S Kokoska, MD, Associate Professor, Department of Otolaryngology-Head and Neck Surgery, University of Arkansas for Medical Sciences; Chief, Department of Otolaryngology-Head and Neck Surgery, Central Arkansas Veterans Healthcare System
Mimi S Kokoska, MD is a member of the following medical societies: American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, American College of Physician Executives, American College of Surgeons, American Head and Neck Society, and Arkansas Medical Society
Disclosure: Nothing to disclose.

Pharmacy Editor

Francisco Talavera, PharmD, PhD, Senior Pharmacy Editor, eMedicine
Disclosure: Nothing to disclose.

Managing Editor

Gregory C Allen, MD, Assistant Professor, Department of Otolaryngology-Head and Neck Surgery, University of Colorado School of Medicine
Gregory C Allen, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American Academy of Pediatrics, American Cleft Palate/Craniofacial Association, American College of Surgeons, American Laryngological Rhinological and Otological Society, American Medical Association, Christian Medical & Dental Society, and Colorado Medical Society
Disclosure: Nothing to disclose.

CME Editor

Christopher L Slack, MD, Otolaryngology-Facial Plastic Surgery, Private Practice, Associated Coastal ENT; Medical Director, Treasure Coast Sleep Disorders
Christopher L Slack, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, and American Medical Association
Disclosure: Nothing to disclose.

Chief Editor

Arlen D Meyers, MD, MBA, Professor, Department of Otolaryngology-Head and Neck Surgery, University of Colorado School of Medicine
Arlen D Meyers, MD, MBA is a member of the following medical societies: American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, and American Head and Neck Society
Disclosure: Covidien Corp Consulting fee Consulting; US Tobacco Corporation unstricted gift unknown

 
 
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