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Genetic Sensorineural Hearing Loss Follow-up

  • Author: Stephanie A Moody Antonio, MD; Chief Editor: Arlen D Meyers, MD, MBA  more...
Updated: Feb 03, 2016

Further Outpatient Care

See the list below:

  • Otologist
    • Encourage follow-up annually and as needed.
    • Frequent findings include problems with the hearing aid, disease of the external or middle ear, and progressive hearing loss.
    • Follow-up must also reassess the accuracy of the initial diagnosis with appropriate modifications made to the habilitative plan.
  • Audiologist
    • After a device hearing amplification is in place, systematic monitoring is necessary to ensure proper function of the device while monitoring speech and language development.
    • Schedule audiologic reevaluation every 3 months during the first year and then every 6 months thereafter.
    • Calibrate hearing aids periodically and fit new molds when necessary.
    • Periodic audiometric testing is necessary to rule out fluctuation or progression of hearing loss.
  • Speech and language pathologist
    • Speech and language therapy is imperative to promote proper language and communication skills.
    • A plan for systematic monitoring is required to ensure that a child with hearing impairment develops the necessary speech and communication skills to meet his or her daily communication needs.


The patient must avoid ototoxic medications and loud noise exposure in the absence of hearing protection.



See the list below:

  • Children with unilateral hearing loss have difficulty with sound localization and with hearing in settings with background noise that can make school life difficult. Among such children, the incidence of school-grade failure, distractibility, daydreaming, inability to follow directions, and behavioral problems increases.
  • Children with profound bilateral hearing loss have reductions in receptive and expressive language skills, rates of graduation from high school, reading levels, and math skills. Deaf individuals may have low rates of employment, few opportunities for financial gain, restricted socialization, language barriers that resulting in limited social groups and reduced quality of life.


With proper amplification, speech and language therapy, and an educational program, a patient with SNHL may participate in mainstream society, obtain gainful employment, and be competent in adult life. Children with profound deafness that is rehabilitated with cochlear implants achieve language development on par with that of their peers.


Patient Education

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Contributor Information and Disclosures

Stephanie A Moody Antonio, MD Associate Professor, Department of Otolaryngology-Head and Neck Surgery, Eastern Virginia Medical School

Stephanie A Moody Antonio, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, Virginia Society of Otolaryngology-Head and Neck Surgery, American Neurotology Society, American Medical Association

Disclosure: Nothing to disclose.


Barry Strasnick, MD, FACS Chairman, Professor, Department of Otolaryngology-Head and Neck Surgery, Eastern Virginia Medical School

Barry Strasnick, MD, FACS is a member of the following medical societies: Alpha Omega Alpha, American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, American Auditory Society, American College of Surgeons, American Medical Association, American Tinnitus Association, Ear Foundation Alumni Society, Norfolk Academy of Medicine, North American Skull Base Society, Society of University Otolaryngologists-Head and Neck Surgeons, Vestibular Disorders Association, Virginia Society of Otolaryngology-Head and Neck Surgery

Disclosure: Nothing to disclose.

Specialty Editor Board

Francisco Talavera, PharmD, PhD Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Received salary from Medscape for employment. for: Medscape.

Ted L Tewfik, MD Professor of Otolaryngology-Head and Neck Surgery, Professor of Pediatric Surgery, McGill University Faculty of Medicine; Senior Staff, Montreal Children's Hospital, Montreal General Hospital, and Royal Victoria Hospital

Ted L Tewfik, MD is a member of the following medical societies: American Society of Pediatric Otolaryngology, Canadian Society of Otolaryngology-Head & Neck Surgery

Disclosure: Nothing to disclose.

Chief Editor

Arlen D Meyers, MD, MBA Professor of Otolaryngology, Dentistry, and Engineering, University of Colorado School of Medicine

Arlen D Meyers, MD, MBA is a member of the following medical societies: American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, American Head and Neck Society

Disclosure: Serve(d) as a director, officer, partner, employee, advisor, consultant or trustee for: Cerescan;RxRevu;SymbiaAllergySolutions<br/>Received income in an amount equal to or greater than $250 from: Symbia<br/>Received from Allergy Solutions, Inc for board membership; Received honoraria from RxRevu for chief medical editor; Received salary from Medvoy for founder and president; Received consulting fee from Corvectra for senior medical advisor; Received ownership interest from Cerescan for consulting; Received consulting fee from Essiahealth for advisor; Received consulting fee from Carespan for advisor; Received consulting fee from Covidien for consulting.

Additional Contributors

Robert A Battista, MD, FACS Assistant Professor of Otolaryngology, Northwestern University, The Feinberg School of Medicine; Physician, Ear Institute of Chicago, LLC

Robert A Battista, MD, FACS is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, Illinois State Medical Society, American Neurotology Society, American College of Surgeons

Disclosure: Nothing to disclose.


The authors and editors of Medscape Reference gratefully acknowledge the contributions of previous author Karen K Hoffmann, MD, to the development and writing of this article.

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Inner ear.
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