Genetic Sensorineural Hearing Loss Follow-up
- Author: Stephanie A Moody Antonio, MD; Chief Editor: Arlen D Meyers, MD, MBA more...
Further Outpatient Care
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- Encourage follow-up annually and as needed.
- Frequent findings include problems with the hearing aid, disease of the external or middle ear, and progressive hearing loss.
- Follow-up must also reassess the accuracy of the initial diagnosis with appropriate modifications made to the habilitative plan.
- After a device hearing amplification is in place, systematic monitoring is necessary to ensure proper function of the device while monitoring speech and language development.
- Schedule audiologic reevaluation every 3 months during the first year and then every 6 months thereafter.
- Calibrate hearing aids periodically and fit new molds when necessary.
- Periodic audiometric testing is necessary to rule out fluctuation or progression of hearing loss.
- Speech and language pathologist
- Speech and language therapy is imperative to promote proper language and communication skills.
- A plan for systematic monitoring is required to ensure that a child with hearing impairment develops the necessary speech and communication skills to meet his or her daily communication needs.
The patient must avoid ototoxic medications and loud noise exposure in the absence of hearing protection.
See the list below:
- Children with unilateral hearing loss have difficulty with sound localization and with hearing in settings with background noise that can make school life difficult. Among such children, the incidence of school-grade failure, distractibility, daydreaming, inability to follow directions, and behavioral problems increases.
- Children with profound bilateral hearing loss have reductions in receptive and expressive language skills, rates of graduation from high school, reading levels, and math skills. Deaf individuals may have low rates of employment, few opportunities for financial gain, restricted socialization, language barriers that resulting in limited social groups and reduced quality of life.
With proper amplification, speech and language therapy, and an educational program, a patient with SNHL may participate in mainstream society, obtain gainful employment, and be competent in adult life. Children with profound deafness that is rehabilitated with cochlear implants achieve language development on par with that of their peers.
See the list below:
- When counseling the parents of a child who is hearing impaired, one must address the probability of having subsequent affected children. This risk depends on the status of the parents and on the number of affected offspring.
- The website www.babyhearing.org is designed to help parents understand hearing loss identification and treatment.
- The American Academy of Otolaryngology-Head and Neck surgery provides several fact sheets with information on hearing loss and related ear issues at http://entlink.net/HealthInformation/Genes-and-Hearing-Loss.cfm.
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