Choanal Atresia Treatment & Management
- Author: Ted L Tewfik, MD, FRCSC; Chief Editor: Arlen D Meyers, MD, MBA more...
Surgical Therapy
Treatment can be divided into emergent and elective definitive categories. Bilateral choanal atresia in a neonate is an emergency that is best initially treated by inserting an oral airway to break the seal formed by the tongue against the palate. This oral airway can be well tolerated for several weeks. The method of repair is controversial, with no technique having gained universal acceptance. Bilateral choanal atresia in the newborn requires prompt diagnosis and airway stabilization. An oral airway, McGovern nipple, and intubation are viable options. The ideal procedure for choanal atresia restores the normal nasal passage, prevents damage to growing structures important in facial development, is technically safe, requires short operative time, and provides short hospitalization and convalescence.
Procedures
Transnasal puncture, with or without a microscope, became unpopular because of the high rate of failure that then required revision. This was attributed to the difficulty in visualizing the choanal area that required special surgical attention, such as the vomerine septal bridge and bony narrowing of the lateral walls. The transnasal approach becomes more difficult in the presence of septal deviation, turbinate hypertrophy, nasal discharge, and elongation of the depth from the nasal vestibule to the posterior choanae as patients grow.
The transseptal technique consists of making a window in the septum anterior to the atretic plate.
Transpalatal repair, as seen in the image below, is a technique that provides excellent exposure and has a high success rate but requires more operative time. The increased blood loss, possible occurrence of palatal fistula, palatal dysfunction, and maxillofacial growth disturbance are complications of this procedure.
Choanal atresia. Diagram illustrating the transpalatal correction of choanal atresia. The endoscopic technique (nasal or retropalatal), with or without powered instrumentation, offers excellent visualization with great ease in removing the bony choanae.[2] The potential of certain instruments for the management of choanal atresia was published, such as the retrograde 110° Sekunda endoscope and silicone horseshoe-shaped protectors.[3] Combined transoral-transnasal is another technique that provides a good alternative for managing choanal atresia, with easier, 4-handed surgery to ensure adequate posterior choana for nasal breathing.[4]
Microdebriders continue to advance the field of endoscopic surgery, providing clearer operative fields and causing less tissue trauma for experienced surgeons. However, the severity of complications, including the potential for rapidly aspirating orbital and cerebral contents when laminae are violated, must be appreciated and respected.
Carbon dioxide and potassium titanyl phosphate (KTP) lasers are easy and quick and create minimal discomfort to the patient. The time of hospitalization is short, and the operation can be repeated if a good result is not initially achieved. Most importantly, a stent is not usually needed. The use of mitomycin C topically as an adjunct to the surgical repair of choanal atresia may offer improved patency with a decreased need for stenting, dilatations, and revision surgery.[5]
Postoperative Details
Infants with documented gastroesophageal reflux disease (GERD) require prolonged stenting and dilatations for choanal restenosis and removal of granulation tissue. Stenting is usually performed using an endotracheal tube or Foley catheter. The advantages of Foley catheter stenting for choanal atresia are as follows:
- Well tolerated by the patient
- Simple to introduce, fix, and remove
- Minimizes septal or columellar necrosis
- Minimizes nasal cavity and paranasal sinus infections
- Adjustable with inflation or deflation of the balloon that controls the pressure on the choanal walls
- Easy to fix in cases of unilateral atresia
The use of stents in the treatment of patients with choanal atresia is a controversial subject. Some surgeons believe that stents are useful in stabilizing the nasal airway in the postoperative period to prevent the development of stenosis by maintaining a lumen. However, others believe that stents may act as a nidus for infection and may induce a foreign body reaction. This may contribute to choanal restenosis, much as an endotracheal tube may cause subglottic stenosis. Therefore, the use of stents following repair of choanal atresia requires the use of prophylactic antibiotic and antireflux medications. Cedin et al (2006) analyzed the long-term results of a new stentless surgical technique for choanal atresia.[6] They reported that, using neither stents or nasal packing, this technique allowed fast recovery in a one-step surgery.
Follow-up
Following surgical repair of choanal atresia, patients may require operative debridement or periodic dilatations. Periodic dilations can sometimes be performed as an outpatient procedure with local decongestant and topical anesthesia using urethral sounds.
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