Choanal Atresia Treatment & Management

  • Author: Ted L Tewfik, MD, FRCSC; Chief Editor: Arlen D Meyers, MD, MBA   more...
 
Updated: Jul 22, 2011
 

Surgical Therapy

Treatment can be divided into emergent and elective definitive categories. Bilateral choanal atresia in a neonate is an emergency that is best initially treated by inserting an oral airway to break the seal formed by the tongue against the palate. This oral airway can be well tolerated for several weeks. The method of repair is controversial, with no technique having gained universal acceptance. Bilateral choanal atresia in the newborn requires prompt diagnosis and airway stabilization. An oral airway, McGovern nipple, and intubation are viable options. The ideal procedure for choanal atresia restores the normal nasal passage, prevents damage to growing structures important in facial development, is technically safe, requires short operative time, and provides short hospitalization and convalescence.

Procedures

Transnasal puncture, with or without a microscope, became unpopular because of the high rate of failure that then required revision. This was attributed to the difficulty in visualizing the choanal area that required special surgical attention, such as the vomerine septal bridge and bony narrowing of the lateral walls. The transnasal approach becomes more difficult in the presence of septal deviation, turbinate hypertrophy, nasal discharge, and elongation of the depth from the nasal vestibule to the posterior choanae as patients grow.

The transseptal technique consists of making a window in the septum anterior to the atretic plate.

Transpalatal repair, as seen in the image below, is a technique that provides excellent exposure and has a high success rate but requires more operative time. The increased blood loss, possible occurrence of palatal fistula, palatal dysfunction, and maxillofacial growth disturbance are complications of this procedure.

Choanal atresia. Diagram illustrating the transpalChoanal atresia. Diagram illustrating the transpalatal correction of choanal atresia.

The endoscopic technique (nasal or retropalatal), with or without powered instrumentation, offers excellent visualization with great ease in removing the bony choanae.[2] The potential of certain instruments for the management of choanal atresia was published, such as the retrograde 110° Sekunda endoscope and silicone horseshoe-shaped protectors.[3] Combined transoral-transnasal is another technique that provides a good alternative for managing choanal atresia, with easier, 4-handed surgery to ensure adequate posterior choana for nasal breathing.[4]

Microdebriders continue to advance the field of endoscopic surgery, providing clearer operative fields and causing less tissue trauma for experienced surgeons. However, the severity of complications, including the potential for rapidly aspirating orbital and cerebral contents when laminae are violated, must be appreciated and respected.

Carbon dioxide and potassium titanyl phosphate (KTP) lasers are easy and quick and create minimal discomfort to the patient. The time of hospitalization is short, and the operation can be repeated if a good result is not initially achieved. Most importantly, a stent is not usually needed. The use of mitomycin C topically as an adjunct to the surgical repair of choanal atresia may offer improved patency with a decreased need for stenting, dilatations, and revision surgery.[5]

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Postoperative Details

Infants with documented gastroesophageal reflux disease (GERD) require prolonged stenting and dilatations for choanal restenosis and removal of granulation tissue. Stenting is usually performed using an endotracheal tube or Foley catheter. The advantages of Foley catheter stenting for choanal atresia are as follows:

  • Well tolerated by the patient
  • Simple to introduce, fix, and remove
  • Minimizes septal or columellar necrosis
  • Minimizes nasal cavity and paranasal sinus infections
  • Adjustable with inflation or deflation of the balloon that controls the pressure on the choanal walls
  • Easy to fix in cases of unilateral atresia

The use of stents in the treatment of patients with choanal atresia is a controversial subject. Some surgeons believe that stents are useful in stabilizing the nasal airway in the postoperative period to prevent the development of stenosis by maintaining a lumen. However, others believe that stents may act as a nidus for infection and may induce a foreign body reaction. This may contribute to choanal restenosis, much as an endotracheal tube may cause subglottic stenosis. Therefore, the use of stents following repair of choanal atresia requires the use of prophylactic antibiotic and antireflux medications. Cedin et al (2006) analyzed the long-term results of a new stentless surgical technique for choanal atresia.[6] They reported that, using neither stents or nasal packing, this technique allowed fast recovery in a one-step surgery.

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Follow-up

Following surgical repair of choanal atresia, patients may require operative debridement or periodic dilatations. Periodic dilations can sometimes be performed as an outpatient procedure with local decongestant and topical anesthesia using urethral sounds.

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Contributor Information and Disclosures
Author

Ted L Tewfik, MD, FRCSC  Professor, Department of Otolaryngology-Head and Neck Surgery, Director of Continuing Medical Education of Otolaryngology, McGill University Medical School; Director of Professional Affairs of Otolaryngology, Division of Otolaryngology, Montreal Children's Hospital; Senior Staff, Montreal General Hospital and Royal Victoria Hospital

Ted L Tewfik, MD, FRCSC, is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American College of Surgeons, American Society of Pediatric Otolaryngology, Canadian Medical Association, Canadian Society of Otolaryngology-Head & Neck Surgery, Quebec Medical Association, and Royal College of Physicians and Surgeons of Canada

Disclosure: Nothing to disclose.

Coauthor(s)

Yaser ALI Alrajhi, MD, FRCSC  Fellow, Department of Otolaryngology, Division of Pediatric Otolaryngology, McGill University Faculty of Medicine

Disclosure: Nothing to disclose.

Abdulrahman A Hagr, MBBS  Otolaryngology Consultant, King Abdulaziz University Hospital; Associate Professor, King Saud University

Abdulrahman A Hagr, MBBS is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery and Canadian Society of Otolaryngology-Head & Neck Surgery

Disclosure: Nothing to disclose.

Specialty Editor Board

Russell A Faust, MD, PhD  Consulting Staff, Department of Otolaryngology, Columbus Children's Hospital

Russell A Faust, MD, PhD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American College of Legal Medicine, American Laryngological Rhinological and Otological Society, American Rhinologic Society, American Society for Head and Neck Surgery, and American Society of Law, Medicine & Ethics

Disclosure: Nothing to disclose.

Francisco Talavera, PharmD, PhD  Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Medscape Salary Employment

Gregory C Allen, MD  Assistant Professor, Department of Otolaryngology-Head and Neck Surgery, University of Colorado School of Medicine

Gregory C Allen, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American Academy of Pediatrics, American Cleft Palate/Craniofacial Association, American College of Surgeons, American Laryngological Rhinological and Otological Society, American Medical Association, Christian Medical & Dental Society, and Colorado Medical Society

Disclosure: Nothing to disclose.

Christopher L Slack, MD  Private Practice in Otolaryngology and Facial Plastic Surgery, Associated Coastal ENT; Medical Director, Treasure Coast Sleep Disorders

Christopher L Slack, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, and American Medical Association

Disclosure: Nothing to disclose.

Chief Editor

Arlen D Meyers, MD, MBA  Professor, Department of Otolaryngology-Head and Neck Surgery, University of Colorado School of Medicine

Arlen D Meyers, MD, MBA is a member of the following medical societies: American Academy of Facial Plastic and Reconstructive Surgery, American Academy of Otolaryngology-Head and Neck Surgery, and American Head and Neck Society

Disclosure: Covidien Corp Consulting fee Consulting; US Tobacco Corporation Unrestricted gift Unknown; Axis Three Corporation Ownership interest Consulting; Omni Biosciences Ownership interest Consulting; Sentegra Ownership interest Board membership; Syndicom Ownership interest Consulting; Oxlo Consulting; Medvoy Ownership interest Management position; Cerescan Imaging Honoraria Consulting; GYRUS ACMI Honoraria Consulting

References
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Choanal atresia. Rhinogram demonstrating blockage of radiopaque dye at the posterior choanae. From T.L. Tewfik and V.M. Der Kaloustian, with permission.
Choanal atresia. CT scan showing membranous and bony choanal atresia. From T.L. Tewfik and V.M. Der Kaloustian, with permission.
Choanal atresia. Diagram illustrating the transpalatal correction of choanal atresia.
 
 
 
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