eMedicine Specialties > Pediatrics: Cardiac Disease and Critical Care Medicine > Cardiology

Double-Chambered Right Ventricle: Follow-up

Author: Shubhayan Sanatani, MD, Associate Professor, Department of Pediatrics, University of British Columbia at Vancouver; Consulting Staff, Division of Pediatric Cardiology, British Columbia Children's Hospital
Coauthor(s): Alejandro R Peirone, MD, Head, Section of Pediatric Cardiology, Hospital Privado de Cordoba; Consulting Staff, Division of Pediatric Cardiology, Hospital Espanol Medical Plaza and Children's Hospital of Cordoba
Contributor Information and Disclosures

Updated: May 18, 2009

Follow-up

Further Outpatient Care

  • Prior to surgical therapy for double-chambered right ventricle (DCRV), the follow-up is based on the degree of obstruction, associated lesions, and symptoms. Regular evaluation by a cardiologist is recommended.
  • The residual lesions determine the follow-up of these patients after surgery. The patients are initially frequently evaluated in order to monitor the progress after repair.
  • Exercise tolerance and quality of life, endocarditis prophylaxis, and recurrence of obstruction comprise the major issues during the long-term follow-up.

Prognosis

  • Long-term results in earlier series are excellent, with current results showing improvement. Ruling out residual lesions and providing follow-up care for patients with recurrent right ventricle (RV) obstruction are important.

Patient Education

Miscellaneous

Medicolegal Pitfalls

  • Failure to recognize double-chambered right ventricle (DCRV) in the presence of associated defects, particularly ventricular septal defect (VSD), which may result in reoperation
  • Failure to rule out residual lesions
  • Failure to provide follow-up care for patients with recurrent right ventricle obstruction

Special Concerns

  • Once the associated lesions have been repaired and the abnormal muscle bundles have been resected, pregnancy carries no additional risks. The same applies if mild gradients across the right ventricular outflow tract exist.
 
Acknowledgments

The authors and editors of eMedicine gratefully acknowledge the contributions of previous author Alejandro R Peirone, MD, to the writing and development of this article.



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References
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Further Reading

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Keywords

double-chambered right ventricle, divided right ventricle, anomalous right ventricular muscle bundles, AMB, two-chambered right ventricle, 2-chambered right ventricle, DCRV, separated right ventricle, ventricular septal defect, VSD, pulmonary valve stenosis, discrete subaortic stenosis, anomalous septoparietal band, anomalous apical shelf, hypertrophy of apical trabeculations, anomalous apical shelf with Ebstein malformation, bundle branch block, right ventricular outflow tract obstruction, tetralogy of Fallot, left ventricular outflow tract obstruction, pulmonary valve stenosis, Down syndrome, Noonan syndrome, treatment, diagnosis

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Contributor Information and Disclosures

Author

Shubhayan Sanatani, MD, Associate Professor, Department of Pediatrics, University of British Columbia at Vancouver; Consulting Staff, Division of Pediatric Cardiology, British Columbia Children's Hospital
Shubhayan Sanatani, MD is a member of the following medical societies: British Columbia Medical Association, Canadian Cardiovascular Society, Canadian Heart Rhythm Society, Canadian Heart Rhythm Society, Canadian Medical Association, Heart Rhythm Society, and Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

Coauthor(s)

Alejandro R Peirone, MD, Head, Section of Pediatric Cardiology, Hospital Privado de Cordoba; Consulting Staff, Division of Pediatric Cardiology, Hospital Espanol Medical Plaza and Children's Hospital of Cordoba
Disclosure: Nothing to disclose.

Medical Editor

Juan Carlos Alejos, MD, Clinical Professor, Department of Pediatrics, Division of Cardiology, University of California at Los Angeles
Juan Carlos Alejos, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American Heart Association, American Medical Association, and International Society for Heart and Lung Transplantation
Disclosure: Actelion Honoraria Speaking and teaching

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from financial planner; Avanir Pharma Stock Investment from financial planner ; WebMD Salary and stock Employment and investment from financial planner

Managing Editor

Julian M Stewart, MD, PhD, Associate Chairman of Pediatrics, Director, Center for Hypotension, Westchester Medical Center; Professor of Pediatrics and Physiology, New York Medical College
Julian M Stewart, MD, PhD is a member of the following medical societies: American Academy of Pediatrics
Disclosure: Nothing to disclose.

CME Editor

Gilbert Z Herzberg, MD, Assistant Professor, Department of Pediatrics, Section of Pediatric Cardiology, New York Medical College; Consulting Staff, Department of Pediatrics, Sound Shore Medical Center
Gilbert Z Herzberg, MD is a member of the following medical societies: American Academy of Pediatrics
Disclosure: Nothing to disclose.

Chief Editor

Stuart Berger, MD, Professor of Pediatrics, Division of Cardiology, Medical College of Wisconsin; Chief of Pediatric Cardiology, Medical Director of Pediatric Heart Transplant Program, Medical Director of The Heart Center, Children's Hospital of Wisconsin
Stuart Berger, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American College of Chest Physicians, American Heart Association, and Society for Cardiac Angiography and Interventions
Disclosure: Nothing to disclose.

 
 
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