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Pediatric Ebstein Anomaly Follow-up

  • Author: Raymond T Fedderly, MD; Chief Editor: Stuart Berger, MD  more...
Updated: Jan 04, 2016

Further Outpatient Care

Patients who are asymptomatic initially may develop increasing cyanosis or congestive heart failure. They require continued outpatient monitoring.

Adult patients are best served by having their follow-up at a center with adult congenital heart disease specialists and technologists.[11]


Patient Education

Patient and family education is directed at communicating the importance of prophylaxis for bacterial endocarditis and identifying the signs and symptoms of potential arrhythmias and progressive congestive heart failure.

Forpatient education resources, see Heart Health Center, as well as Palpitations.

Contributor Information and Disclosures

Raymond T Fedderly, MD Associate Professor, Department of Pediatric Cardiology, Children's Hospital of Wisconsin, Medical College of Wisconsin

Raymond T Fedderly, MD is a member of the following medical societies: American College of Cardiology, American Heart Association

Disclosure: Nothing to disclose.

Specialty Editor Board

Mary L Windle, PharmD Adjunct Associate Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Nothing to disclose.

John W Moore, MD, MPH Professor of Clinical Pediatrics, Section of Pediatic Cardiology, Department of Pediatrics, University of California San Diego School of Medicine; Director of Cardiology, Rady Children's Hospital

John W Moore, MD, MPH is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

Chief Editor

Stuart Berger, MD Medical Director of The Heart Center, Children's Hospital of Wisconsin; Associate Professor, Department of Pediatrics, Section of Pediatric Cardiology, Medical College of Wisconsin

Stuart Berger, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American College of Chest Physicians, American Heart Association, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

Additional Contributors

Charles I Berul, MD Professor of Pediatrics and Integrative Systems Biology, George Washington University School of Medicine; Chief, Division of Cardiology, Children's National Medical Center

Charles I Berul, MD is a member of the following medical societies: American Academy of Pediatrics, Heart Rhythm Society, Cardiac Electrophysiology Society, Pediatric and Congenital Electrophysiology Society, American College of Cardiology, American Heart Association, Society for Pediatric Research

Disclosure: Received grant/research funds from Medtronic for consulting.

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Frontal chest radiograph in an infant with severe Ebstein anomaly shows a large heart that leaves little space for the lung. Although the appearance is relatively nonspecific, the large heart should suggest Ebstein anomaly in the differential diagnosis.
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