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Ventricular Inversion Follow-up

  • Author: Ira H Gessner, MD; Chief Editor: Howard S Weber, MD, FSCAI  more...
 
Updated: Jan 16, 2015
 

Further Outpatient Care

All patients with ventricular inversion, including those with no clinically significant associated defect, require regular follow-up by a pediatric cardiologist or an adult cardiologist who is thoroughly familiar with congenital heart disease. A permanent risk of developing complete heart block and uncertain long-term stability of both the tricuspid valve and right ventricle dictate this need.

Patients with even mild degrees of clinically apparent tricuspid valve regurgitation require follow-up at regular intervals, no longer than yearly, because this abnormality tends to be progressive.

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Inpatient & Outpatient Medications

The type of associated heart defect and its effects on the patient dictate the medications needed.

Patients must observe precautions against bacterial endocarditis.

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Patient Education

Patient restrictions regarding exercise and other lifestyle issues depend on the associated cardiac defect.

Instruct parents and older patients regarding the symptoms of cardiac conduction abnormality and specifically the symptoms of sudden-onset of Adams-Stokes syndrome, which can cause complete heart block.

When children with ventricular inversion reach maturity, they must be educated regarding the importance of the defect and of any associated abnormalities.

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Contributor Information and Disclosures
Author

Ira H Gessner, MD Professor Emeritus, Pediatric Cardiology, University of Florida College of Medicine

Ira H Gessner, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American Heart Association, American Pediatric Society, Society for Pediatric Research

Disclosure: Nothing to disclose.

Specialty Editor Board

Mary L Windle, PharmD Adjunct Associate Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Nothing to disclose.

Hugh D Allen, MD Professor, Department of Pediatrics, Division of Pediatric Cardiology and Department of Internal Medicine, Ohio State University College of Medicine

Hugh D Allen, MD is a member of the following medical societies: American Academy of Pediatrics, American Society of Echocardiography, Society for Pediatric Research, Society of Pediatric Echocardiography, Western Society for Pediatric Research, American College of Cardiology, American Heart Association, American Pediatric Society

Disclosure: Nothing to disclose.

Chief Editor

Howard S Weber, MD, FSCAI Professor of Pediatrics, Section of Pediatric Cardiology, Pennsylvania State University College of Medicine; Director of Interventional Pediatric Cardiology, Penn State Hershey Children's Hospital

Howard S Weber, MD, FSCAI is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, Society for Cardiovascular Angiography and Interventions

Disclosure: Received income in an amount equal to or greater than $250 from: St. Jude Medical.

Additional Contributors

Jeffrey Allen Towbin, MD, MSc FAAP, FACC, FAHA, Professor, Departments of Pediatrics (Cardiology), Cardiovascular Sciences, and Molecular and Human Genetics, Baylor College of Medicine; Chief of Pediatric Cardiology, Foundation Chair in Pediatric Cardiac Research, Texas Children's Hospital

Jeffrey Allen Towbin, MD, MSc is a member of the following medical societies: American Academy of Pediatrics, American Association for the Advancement of Science, American College of Cardiology, American College of Sports Medicine, American Heart Association, American Medical Association, American Society of Human Genetics, New York Academy of Sciences, Society for Pediatric Research, Texas Medical Association, Texas Pediatric Society, Cardiac Electrophysiology Society

Disclosure: Nothing to disclose.

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This right ventricular angiogram shows a patient with transposition of the great arteries. The aorta arises directly from the right-sided anterior right ventricle (10° left anterior oblique [LAO]).
 
 
 
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