Pediatric Subvalvar Aortic Stenosis Medication

  • Author: Douglas J Schneider, MD; Chief Editor: Howard S Weber, MD, FSCAI  more...
 
Updated: Sep 19, 2015
 
 

Medication Summary

SAS is treated surgically.

 
Contributor Information and Disclosures
Author

Douglas J Schneider, MD Associate Professor of Pediatrics, Clinical Tract, Division of Pediatric Cardiology, Department of Pediatrics, University of Kentucky College of Medicine; Director, Pediatric Cardiac Catheterization Laboratory, Kentucky Children’s Hospital

Disclosure: Nothing to disclose.

Coauthor(s)

Gautam K Singh, MD, , MRCP Professor of Pediatrics, Division of Cardiology, Director of Noninvasive Imaging Research, Co-Director of Echocardiography Laboratory, Washington University in St Louis School of Medicine; Attending Faculty, Department of Pediatrics, Division of Cardiology, St Louis Children's Hospital

Gautam K Singh, MD, , MRCP is a member of the following medical societies: American College of Cardiology, American Heart Association, American Society of Echocardiography, Royal College of Physicians

Disclosure: Nothing to disclose.

Specialty Editor Board

Mary L Windle, PharmD Adjunct Associate Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Nothing to disclose.

John W Moore, MD, MPH Professor of Clinical Pediatrics, Section of Pediatic Cardiology, Department of Pediatrics, University of California San Diego School of Medicine; Director of Cardiology, Rady Children's Hospital

John W Moore, MD, MPH is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

Chief Editor

Howard S Weber, MD, FSCAI Professor of Pediatrics, Section of Pediatric Cardiology, Pennsylvania State University College of Medicine; Director of Interventional Pediatric Cardiology, Penn State Hershey Children's Hospital

Howard S Weber, MD, FSCAI is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, Society for Cardiovascular Angiography and Interventions

Disclosure: Received income in an amount equal to or greater than $250 from: St. Jude Medical.

Additional Contributors

Paul M Seib, MD Associate Professor of Pediatrics, University of Arkansas for Medical Sciences; Medical Director, Cardiac Catheterization Laboratory, Co-Medical Director, Cardiovascular Intensive Care Unit, Arkansas Children's Hospital

Paul M Seib, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American Heart Association, Arkansas Medical Society, International Society for Heart and Lung Transplantation, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

References
  1. Iwata Y, Imai Y, Shin'oka T, Kurosawa H. Subaortic stenosis associated with systolic anterior motion. Heart Vessels. 2008 Nov. 23(6):436-9. [Medline].

  2. Somerville J, Stone S, Ross D. Fate of patients with fixed subaortic stenosis after surgical removal. Br Heart J. 1980 Jun. 43(6):629-47. [Medline]. [Full Text].

  3. Bezold LI, Smith EO, Kelly K, et al. Development and validation of an echocardiographic model for predicting progression of discrete subaortic stenosis in children. Am J Cardiol. 1998 Feb 1. 81(3):314-20. [Medline].

  4. Edwards JE. Pathology of left ventricular outflow tract obstruction. Circulation. 1965 Apr. 31:586-99. [Medline].

  5. Pavione MA, Mendonça JT, Souza IS, Russo MA. Accessory mitral leaflet: an uncommon form of subaortic stenosis. Rev Bras Cir Cardiovasc. 2012 Jul-Sep. 27(3):477-80. [Medline].

  6. Ezon DS. Fixed subaortic stenosis: a clinical dilemma for clinicians and patients. Congenit Heart Dis. 2013 Sep. 8(5):450-6. [Medline].

  7. Gokalp S, Oztunc F. Clinically asymptomatic myocardial bridging in a child with familial subaortic stenosis. Cardiol Young. 2013 Jun 28. 1-3. [Medline].

  8. Barkhordarian R, Wen-Hong D, Li W, et al. Geometry of the left ventricular outflow tract in fixed subaortic stenosis and intact ventricular septum: an echocardiographic study in children and adults. J Thorac Cardiovasc Surg. 2007 Jan. 133(1):196-203. [Medline].

  9. Kleinert S, Geva T. Echocardiographic morphometry and geometry of the left ventricular outflow tract in fixed subaortic stenosis. J Am Coll Cardiol. 1993 Nov 1. 22(5):1501-8. [Medline].

  10. Reist-Marti SB, Dolf G, Leeb T, et al. Genetic evidence of subaortic stenosis in the Newfoundland dog. Vet Rec. 2012 Jun 9. 170 (23):597. [Medline].

  11. Newfeld EA, Muster AJ, Paul MH, et al. Discrete subvalvular aortic stenosis in childhood. Study of 51 patients. Am J Cardiol. 1976 Jul. 38(1):53-61. [Medline].

  12. Wright GB, Keane JF, Nadas AS, et al. Fixed subaortic stenosis in the young: medical and surgical course in 83 patients. Am J Cardiol. 1983 Oct 1. 52(7):830-5. [Medline].

  13. Suri RM, Dearani JA, Schaff HV, Danielson GK, Puga FJ. Long-term results of the Konno procedure for complex left ventricular outflow tract obstruction. J Thorac Cardiovasc Surg. 2006 Nov. 132(5):1064-71. [Medline].

  14. Karamlou T, Gurofsky R, Bojcevski A, et al. Prevalence and associated risk factors for intervention in 313 children with subaortic stenosis. Ann Thorac Surg. 2007 Sep. 84(3):900-6; discussion 906. [Medline].

  15. Rohlicek CV, del Pino SF, Hosking M, Miro J, Côté JM, Finley J. Natural history and surgical outcomes for isolated discrete subaortic stenosis in children. Heart. 1999 Dec. 82(6):708-13. [Medline]. [Full Text].

  16. Gersony WM. Natural history of discrete subvalvar aortic stenosis: management implications. J Am Coll Cardiol. 2001 Sep. 38(3):843-5. [Medline].

  17. Brauner R, Laks H, Drinkwater DC Jr, Shvarts O, Eghbali K, Galindo A. Benefits of early surgical repair in fixed subaortic stenosis. J Am Coll Cardiol. 1997 Dec. 30(7):1835-42. [Medline].

  18. de Agustin JA, Gomez de Diego JJ, Marcos-Alberca P, Macaya C, Perez de Isla L. Combined subaortic membrane and aortic valve stenosis: additive value of three-dimensional echocardiography. Eur Heart J Cardiovasc Imaging. 2013 Oct 18. [Medline].

  19. Singh GK, Shiota T, Cobanoglu A, et al. Diagnostic accuracy and role of intraoperative biplane transesophageal echocardiography in pediatric patients with left ventricle outflow tract lesions. J Am Soc Echocardiogr. 1998 Jan. 11(1):47-56. [Medline].

  20. Brown JW, Ruzmetov M, Vijay P, et al. Operative results and outcomes in children with Shone's anomaly. Ann Thorac Surg. 2005 Apr. 79(4):1358-65. [Medline].

  21. [Guideline] Bonow RO, Carabello BA, Kanu C, et al. ACC/AHA 2006 guidelines for the management of patients with valvular heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to revise the 1998 Guidelines for the Management of Patients With Valvular Heart Disease): developed in collaboration with the Society of Cardiovascular Anesthesiologists: endorsed by the Society for Cardiovascular Angiography and Interventions and the Society of Thoracic Surgeons. Circulation. 2006 Aug 1. 114(5):e84-231. [Medline].

  22. Guglin M, Kristof-Kuteyeva O. Congenital discrete subaortic stenosis in pregnancy: case report and literature review. J Heart Valve Dis. 2013 May. 22(3):439-44. [Medline].

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Echocardiogram of membranous subaortic stenosis. AO = aortic; LA = left atrium; LVOT = left ventricular outflow tract.
Tunnel-type of subaortic stenosis (subvalvular aortic stenosis [SAS]). MV = mitral valve.
 
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