Pediatric Right Bundle Branch Block Workup
- Author: Glenn T Wetzel, MD, PhD; Chief Editor: P Syamasundar Rao, MD more...
If myocarditis or cardiomyopathy seem to be reflected in the right bundle branch block (RBBB) pattern, consider troponin, creatine kinase (CK), erythrocyte sedimentation rate (ESR), and other laboratory tests for cardiomyopathy (eg, carnitine determination).
ECG findings in right bundle branch block (RBBB) reflect the underlying pathophysiology.
Transmission of the electrical impulse through the left bundle is normal, resulting in normal depolarization of the septum and left ventricle. This creates the initial R wave in lead V1 and the Q wave in V6.
The electrical impulse in the right bundle branch is delayed or not conducted. Therefore, the right ventricle depolarizes by means of cell-to-cell conduction that spreads from the interventricular septum and left ventricle to the right ventricle. This situation results in the characteristic ECG pattern shown in the image below.
Right bundle branch block has been noted to alternate with left bundle branch block and infra-Hisian block.
ECG findings necessary to confirm the diagnosis of right bundle branch block include the following:
For complete right bundle branch block, the duration of the QRS complex is prolonged for the patient's age. Maximum QRS durations are 0.07 seconds for newborns less than 6 days, 0.08 seconds for patients aged 1 week to 7 years, and 0.09 seconds for patients aged 7-15 years.
An rSR' or rR' pattern, with the initial r wave less than the R' or r', may be seen in leads V1-V3R (see the image below). The initial R wave represents septal activation, the S wave represents left ventricular activation, and the R' represents activation of the right ventricle from the septum and left ventricle.
The S wave, which represents right ventricular activation, is wide in leads I and V6 (see the image below).
The QRS axis may be normal, or right or left axis deviation may be present.
The T wave is almost always inverted in lead V1 and may be inverted in V2. In the other precordial leads and in the limb leads, the T wave is directed opposite to the terminal portion of the QRS complex.
Ambulatory ECG (ie, Holter monitoring) may be indicated in postoperative patients who are being periodically monitored or in patients with new right bundle branch block that has a poorly understood etiology and clinical effect.
Echocardiography or myocardial perfusion studies may be indicated if the right bundle branch block is new or if the patient may have coexisting cardiac problems that cannot be adequately assessed with routine ECG. For example, the standard criteria for ventricular hypertrophy or ischemia are relatively unhelpful in a patient with a preexisting intraventricular conduction defect.
Invasive cardiac catheterization and electrophysiologic testing may be necessary to evaluate patients at risk for heart block or ventricular tachycardia and to document cardiomyopathy, myocarditis, or coexisting hemodynamic abnormalities.
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