Pulmonary Artery Sling Clinical Presentation
- Author: Stuart Berger, MD; Chief Editor: Howard S Weber, MD, FSCAI more...
In patients with pulmonary artery sling, the history is predictable and usually not subtle. Most infants are affected within the first few weeks of life and present with stridor, respiratory distress, cyanosis, wheezing, and/or pneumonia.
Physical examination demonstrates respiratory distress with stridor, dyspnea, and wheezing. When tracheal obstruction is present, the infant may have constant retractions and tachypnea. If a congenital heart defect is associated, its typical physical findings can be identified.
The specific etiology of the pulmonary artery sling is unknown.
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