eMedicine Specialties > Pediatrics: Cardiac Disease and Critical Care Medicine > Cardiology
Single Ventricle: Multimedia
Updated: Jul 15, 2009
Multimedia
 | Media file 1: Cranially angulated frontal angiogram of an L-looped single left ventricle. Abbreviations are as follows: ao=aorta, mpa=main pulmonary artery, oc=outlet chamber (rudimentary right ventricle). |
 | Media file 2: Long axial oblique-equivalent subcostal echocardiogram of single left ventricle (vent) with narrow communication (unlabeled arrow) between left ventricle and outlet chamber (oc). Abbreviations are as follows: L=left, lav=left atrioventricular valve, P=posterior, rav=right atrioventricular valve, S=superior. |
 | Media file 3: Pulsed Doppler echocardiographic evaluation of the narrowing shown in Media file 2. On the left, the sample volume (split oval) is placed just distal to the narrow area. On the right, spectral analysis reveals a mixture of velocities, consistent with the presence of highly nonlaminar (turbulent) flow. |
 | Media file 4: Schematic diagram of a lateral tunnel Fontan. Although the example shown is from a double-outlet right ventricle with left ventricular hypoplasia, it shows the same intra-atrial reconstruction as would be done in a single, common-inlet, right ventricle with bilateral superior venae cavae. Blood from the venae cavae is routed directly to the pulmonary arteries. Pulmonary venous blood flows through the common atrioventricular valve into the right ventricle. Abbreviations are as follows: IVC=inferior vena cava, HV=hepatic vein, LPA=left pulmonary artery, LPVs=left pulmonary veins, LSVC=left superior vena cava, RPA=right pulmonary artery, RPVs=right pulmonary veins, RSVC=right superior vena cava, RV=right ventricle. |
 | Media file 5: Volume-unloading operations, such as the hemi-Fontan procedure, result in increases in wall thickness, as shown by subcostal echocardiography. Frontal views are seen in sections A, B, C and D. Sagittal views are seen in sections E, F, G and H. Pre–hemi-Fontan views are seen in A, B, E, and F. Post–hemi-Fontan views are seen in C, D, G, and H. End-diastole views are seen in A, C, E, and G. End-systole views are seen on B, D, F, and H. In all panels, a pair of open triangles point to markers 1 cm apart. |
 | Media file 6: Cardiac MRI. Frontal view of a 3-dimensional flow field in a patient who has undergone a lateral tunnel type of modified Fontan operation (A). This surgical palliation for patients with only one functional ventricle redirects venous blood from the superior vena cava (SVC) and inferior vena cava (IVC) directly into the right (RPA) and left (LPA) pulmonary arteries. Flow streamlines are shown in red. B. Frontal view of in plane velocity mapping. Right (R jug) and left (L jug) jugular vein flow towards the feet is signal-poor (black). Flow toward the head in the infrahepatic inferior vena cava (IVC) and intracardiac portion of the systemic venous pathway (svp) is signal-intense (white). Images courtesy of Dr. Mark A. Fogel, The Children's Hospital of Philadelphia. |
More on Single Ventricle |
| Overview: Single Ventricle |
| Differential Diagnoses & Workup: Single Ventricle |
| Treatment & Medication: Single Ventricle |
| Follow-up: Single Ventricle |
 Multimedia: Single Ventricle |
| References |
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References
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Further Reading
Keywords
single ventricle, single left ventricle, single right ventricle, tricuspid atresia, mitral atresia, double-inlet single ventricle, common-inlet single ventricle, hepatic dysfunction, biliary dysfunction, protein-losing enteropathy, subpulmonary stenosis, aortic arch obstruction, aortic arch hypoplasia, subaortic stenosis, cyanosis, peripheral perfusion, Fontan operation, hypoproteinemia, L-looped single left ventricle, transposition of the great arteries, D-looped single left ventricle, bulboventricular foramen, outlet foramen, bidirectional Glenn operation, hemi-Fontan operation, pulmonary artery distortion, pericardial effusion, pleural effusion, ascites, thrombus, sinus bradycardia, atrial tachyarrhythmias, varices, plastic bronchitis, thrombocytopenia, systemic collaterals, short stature, treatment, diagnosis
