eMedicine Specialties > Pediatrics: General Medicine > Gastroenterology

Imperforate Anus: Multimedia

Author: Nelson G Rosen, MD, FACS, FAAP, Assistant Professor of Surgery and Pediatrics, Albert Einstein College of Medicine; Attending Pediatric Surgeon and Director, Pediatric Trauma Center, Department of Pediatric General Surgery, Schneider Children's Hospital
Coauthor(s): Daniel A Beals, MD, Attending Staff, Cornerstone Pediatric Surgery
Contributor Information and Disclosures

Updated: Apr 19, 2007

Multimedia

Distal colostogram, posteroanterior view. The ini...
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Media file 1: Distal colostogram, posteroanterior view. The initial phase of augmented-pressure distal colostography aims to determine where the colostomy was placed in the colon and how much colon is available for pull-through, without taking down the colostomy.
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Distal colostogram, posteroanterior view. The ini...

Distal colostogram, posteroanterior view. The initial phase of augmented-pressure distal colostography aims to determine where the colostomy was placed in the colon and how much colon is available for pull-through, without taking down the colostomy.

Distal colostogram, lateral view. This image sho...
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Media file 2: Distal colostogram, lateral view. This image shows the second phase of distal colostography, in which the patient is placed in the lateral position. A radio-opaque marker is clearly visible in the lower right side of the image, marking the muscle complex on the skin. This image shows that the rectal pouch joins the urinary tract at the level of the bulbar urethra, a relatively common malformation in boys.
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Distal colostogram, lateral view. This image sho...

Distal colostogram, lateral view. This image shows the second phase of distal colostography, in which the patient is placed in the lateral position. A radio-opaque marker is clearly visible in the lower right side of the image, marking the muscle complex on the skin. This image shows that the rectal pouch joins the urinary tract at the level of the bulbar urethra, a relatively common malformation in boys.

Bucket-handle malformation. The appearance of a ...
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Media file 3: Bucket-handle malformation. The appearance of a band of skin overlying the sphincteric muscle complex is a common sign in a child born with imperforate anus and perineal fistula.
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Bucket-handle malformation. The appearance of a ...

Bucket-handle malformation. The appearance of a band of skin overlying the sphincteric muscle complex is a common sign in a child born with imperforate anus and perineal fistula.

String-of-pearls malformation. This image shows w...
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Media file 4: String-of-pearls malformation. This image shows white mucoid material within a perineal fistula. The fistula frequently extends anteriorly up the scrotum's median raphe.
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String-of-pearls malformation. This image shows w...

String-of-pearls malformation. This image shows white mucoid material within a perineal fistula. The fistula frequently extends anteriorly up the scrotum's median raphe.

Cloaca. This is the classic appearance of a girl ...
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Media file 5: Cloaca. This is the classic appearance of a girl with a cloacal malformation with a single perineal orifice. The genitals appear quite short, which is a finding consistent with cloaca.
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Cloaca. This is the classic appearance of a girl ...

Cloaca. This is the classic appearance of a girl with a cloacal malformation with a single perineal orifice. The genitals appear quite short, which is a finding consistent with cloaca.

Fourchette fistula. This malformation is somewhe...
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Media file 6: Fourchette fistula. This malformation is somewhere halfway between perineal fistula and vestibular fistula. The fistula has a wet vestibular mucosal lining on its anterior half, but the posterior half is dry perineal skin.
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Fourchette fistula. This malformation is somewhe...

Fourchette fistula. This malformation is somewhere halfway between perineal fistula and vestibular fistula. The fistula has a wet vestibular mucosal lining on its anterior half, but the posterior half is dry perineal skin.

More on Imperforate Anus

Overview: Imperforate Anus
Differential Diagnoses & Workup: Imperforate Anus
Treatment & Medication: Imperforate Anus
Follow-up: Imperforate Anus
Multimedia: Imperforate Anus
References
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References

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  24. Rosen NG, Hong A, Soffer S. Recto-vaginal fistula: a common diagnostic error with significant consequences in girls with anorectal malformations. J Pediatr Surg. 2002;37(7):961-5.

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Further Reading

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Keywords

imperforate anus, anorectal malformations, posterior sagittal anorectoplasty, PSARP, posterior sagittal anorectovaginourethroplasty, PSARVUP, cloacal duct, cloacal cavity, incomplete rupture of the anal membrane, anal atresia, anal stenosis, covered anus, rectourethral fistula, rectovestibular fistulas, long–common-channel cloaca, bladder-neck fistula, perineal fistula, vestibular fistula, fourchette fistula, vaginal fistula, persistent cloaca, tetralogy of Fallot, ventricular septal defects, transposition of the great arteries, hypoplastic left heart syndrome, tracheoesophageal abnormalities, duodenal obstruction, malrotation with Ladd bands, Hirschsprung disease, constipation, lumbosacral anomalies, spinal dysraphism, tethered spinal cord, sacral defect, presacral mass, hydronephrosis, vesicoureteric reflux, renal agenesis, renal dysplasia, cryptorchidism, bicornate uterus, uterus didelphys, vaginal septum, vaginal duplication, cloacal malformations, vaginal agenesis, ipsilateralabsentovary,ipsilateral absent kidney, anorectal anomaly,

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Contributor Information and Disclosures

Author

Nelson G Rosen, MD, FACS, FAAP, Assistant Professor of Surgery and Pediatrics, Albert Einstein College of Medicine; Attending Pediatric Surgeon and Director, Pediatric Trauma Center, Department of Pediatric General Surgery, Schneider Children's Hospital
Nelson G Rosen, MD, FACS, FAAP is a member of the following medical societies: American Academy of Pediatrics, American College of Surgeons, American Pediatric Surgical Association, American Trauma Society, Association of Military Surgeons of the US, Canadian Association of Pediatric Surgeons, and Eastern Association for the Surgery of Trauma
Disclosure: Nothing to disclose.

Coauthor(s)

Daniel A Beals, MD, Attending Staff, Cornerstone Pediatric Surgery
Daniel A Beals, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Physicians, American Pediatric Surgical Association, American Society for Bioethics and Humanities, Kentucky Medical Association, Society for Fetal Urology, Society of Critical Care Medicine, and Southeastern Surgical Congress
Disclosure: Nothing to disclose.

Medical Editor

Hisham Nazer, MB, BCh, FRCP, DCh, DTM&H, Professor of Pediatrics, Consultant in Pediatric Gastroenterology, Hepatology and Clinical Nutrition, Bushnaq Medical Centre, University of Jordan
Hisham Nazer, MB, BCh, FRCP, DCh, DTM&H is a member of the following medical societies: Royal College of Paediatrics and Child Health, Royal College of Physicians, Royal College of Surgeons in Ireland, Royal College of Surgeons of Edinburgh, and Royal Society of Tropical Medicine and Hygiene
Disclosure: Nothing to disclose.

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from broker recommendation; Avanir Pharma Stock Investment from broker recommendation

Managing Editor

Carmen Cuffari, MD, Associate Professor, Department of Pediatrics, Division of Gastroenterology/Nutrition, Johns Hopkins University School of Medicine
Carmen Cuffari, MD is a member of the following medical societies: American College of Gastroenterology, American Gastroenterological Association, North American Society for Pediatric Gastroenterology, Hepatology and Nutrition, and Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

CME Editor

Steven M Schwarz, MD, FAAP, FACN, AGAF, Professor of Pediatrics, State University of New York, Downstate Medical Center College of Medicine; Distinguished Lecturer, New York Medical College, School of Public Health
Steven M Schwarz, MD, FAAP, FACN, AGAF is a member of the following medical societies: American Academy of Pediatrics, American College of Nutrition, American College of Physician Executives, American Gastroenterological Association, American Pediatric Society, Gastroenterology Research Group, New York Academy of Medicine, North American Society for Pediatric Gastroenterology and Nutrition, and Society for Pediatric Research
Disclosure: TAP Pharmaceuticals Honoraria Speaking and teaching; Curemark, LLC Consulting fee Board membership

Chief Editor

Carmen Cuffari, MD, Associate Professor, Department of Pediatrics, Division of Gastroenterology/Nutrition, Johns Hopkins University School of Medicine
Carmen Cuffari, MD is a member of the following medical societies: American College of Gastroenterology, American Gastroenterological Association, North American Society for Pediatric Gastroenterology, Hepatology and Nutrition, and Royal College of Physicians and Surgeons of Canada
Disclosure: Nothing to disclose.

 
 
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