eMedicine Specialties > Pediatrics: Genetics and Metabolic Disease > Metabolic Diseases
Denys-Drash Syndrome: Multimedia
Updated: Apr 10, 2009
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![]() | Media file 1: Gross nephrectomy specimen shows a Wilms tumor pushing the normal renal parenchyma to the side. |
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References
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Further Reading
Keywords
Denys-Drash syndrome, Drash syndrome, DDS, Wilms tumor, intersex disorder, congenital nephropathy, end-stage renal disorder, ESRD, diffuse mesangial sclerosis, nephrotic syndrome, pseudohermaphroditism, gonadoblastoma, oliguria, generalized edema, ascites, hypertension, anemia, rickets, abdominal mass, penoscrotal hypospadias, cryptorchidism, enlarged clitoris with labial fusion, bifid scrotum with palpable gonads, micropenis


Multimedia: Denys-Drash Syndrome