Galactokinase Deficiency Treatment & Management
- Author: Karl S Roth, MD; Chief Editor: Maria Descartes, MD more...
Treatment may be provided on an outpatient basis.
Cataracts that do not regress or disappear with therapy may require hospitalization for surgical removal.
Cataracts may require surgical removal.
See the list below:
Diet is the foundation of therapy. Elimination of lactose and galactose sources suffices for definitive therapy.
Because soy formulas are typically poor calcium sources, ensure adequate calcium intake through dietary supplements.
Many lactose-free foods are known to contain free galactose; counsel from a skilled nutritionist may help a patient avoid these items.
Under kosher dietary law, all foods labeled kosher must also be identified as meat, dairy, or pareve (neither meat nor dairy). Thus, shopping for foods from the kosher meat and pareve food categories exclusively can simplify purchasing food.
No restriction is necessary.
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