eMedicine Specialties > Pediatrics: General Medicine > Nephrology

Polycystic Kidney Disease: Multimedia

Author: Priya Verghese, MD, Fellow in Pediatric Nephrology, Seattle Children's Hospital, University of Washington
Coauthor(s): Jordan M Symons, MD, Associate Professor of Pediatrics, University of Washington School of Medicine; Dialysis Medical Director, Department of Nephrology, Children's Hospital and Regional Medical Center; Henrique M Lederman, MD, PhD, Consulting Staff, Department of Radiology, LeBonheur Children's Medical Center and St Jude Children's Research Hospital; Professor of Radiology and Pediatric Radiology, Chief, Division of Diagnostic Imaging in Pediatrics, Federal University of Sao Paulo, Brazil; Peter J Hurh, Research Fellow, Department of Radiology, The Children's Hospital of Philadelphia; H Jorge Baluarte, MD, Medical Director, Renal Transplant Program, Division of Nephrology, Department of Pediatrics, The Children's Hospital of Philadelphia; Professor of Pediatrics, University of Pennsylvania
Contributor Information and Disclosures

Updated: Aug 13, 2008

Multimedia

Frontal excretory urogram of autosomal dominant p...
(Enlarge Image)
Media file 1: Frontal excretory urogram of autosomal dominant polycystic kidney disease (ADPKD) shows a spider-legs configuration of the collecting system secondary to compression due to cysts.
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Frontal excretory urogram of autosomal dominant p...

Frontal excretory urogram of autosomal dominant polycystic kidney disease (ADPKD) shows a spider-legs configuration of the collecting system secondary to compression due to cysts.

Lateral excretory urogram of autosomal dominant p...
(Enlarge Image)
Media file 2: Lateral excretory urogram of autosomal dominant polycystic kidney disease (ADPKD) shows a spider-legs configuration of the collecting system secondary to compression due to cysts.
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Lateral excretory urogram of autosomal dominant p...

Lateral excretory urogram of autosomal dominant polycystic kidney disease (ADPKD) shows a spider-legs configuration of the collecting system secondary to compression due to cysts.

Sonogram shows cysts with bilaterally enlarged ki...
(Enlarge Image)
Media file 3: Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).
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Sonogram shows cysts with bilaterally enlarged ki...

Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).

Sonogram shows cysts with bilaterally enlarged ki...
(Enlarge Image)
Media file 4: Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).
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Sonogram shows cysts with bilaterally enlarged ki...

Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).

Sonogram shows cysts with bilaterally enlarged ki...
(Enlarge Image)
Media file 5: Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).
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Sonogram shows cysts with bilaterally enlarged ki...

Sonogram shows cysts with bilaterally enlarged kidneys. These findings are compatible with a diagnosis of autosomal dominant polycystic kidney disease (ADPKD).

Pathologic specimen of end-stage autosomal domina...
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Media file 6: Pathologic specimen of end-stage autosomal dominant polycystic kidney disease (ADPKD) with deformed lobulated kidneys.
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Pathologic specimen of end-stage autosomal domina...

Pathologic specimen of end-stage autosomal dominant polycystic kidney disease (ADPKD) with deformed lobulated kidneys.

Sonogram shows enlargement of both kidneys, diffu...
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Media file 7: Sonogram shows enlargement of both kidneys, diffuse increased echogenicity, and loss of corticomedullary differentiation. These findings are compatible with a diagnosis of autosomal recessive polycystic kidney disease (ARPKD).
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Sonogram shows enlargement of both kidneys, diffu...

Sonogram shows enlargement of both kidneys, diffuse increased echogenicity, and loss of corticomedullary differentiation. These findings are compatible with a diagnosis of autosomal recessive polycystic kidney disease (ARPKD).

Excretory urogram shows minimal bilateral tubular...
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Media file 8: Excretory urogram shows minimal bilateral tubular changes caused by a mild form of autosomal recessive polycystic kidney disease (ARPKD).
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Excretory urogram shows minimal bilateral tubular...

Excretory urogram shows minimal bilateral tubular changes caused by a mild form of autosomal recessive polycystic kidney disease (ARPKD).

Excretory urogram shows enlarged kidneys with bil...
(Enlarge Image)
Media file 9: Excretory urogram shows enlarged kidneys with bilateral distortion of the collecting system (spider-legs configuration). These findings are compatible with a diagnosis of autosomal recessive polycystic kidney disease (ARPKD).
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Excretory urogram shows enlarged kidneys with bil...

Excretory urogram shows enlarged kidneys with bilateral distortion of the collecting system (spider-legs configuration). These findings are compatible with a diagnosis of autosomal recessive polycystic kidney disease (ARPKD).

Excretory urogram shows the typical mottled (spon...
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Media file 10: Excretory urogram shows the typical mottled (spongelike) contrast pattern in autosomal recessive polycystic kidney disease (ARPKD).
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Excretory urogram shows the typical mottled (spon...

Excretory urogram shows the typical mottled (spongelike) contrast pattern in autosomal recessive polycystic kidney disease (ARPKD).

Excretory urogram shows the typical mottled (spon...
(Enlarge Image)
Media file 11: Excretory urogram shows the typical mottled (spongelike) contrast pattern in autosomal recessive polycystic kidney disease (ARPKD).
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Excretory urogram shows the typical mottled (spon...

Excretory urogram shows the typical mottled (spongelike) contrast pattern in autosomal recessive polycystic kidney disease (ARPKD).

Excretory urogram shows the typical mottled (spon...
(Enlarge Image)
Media file 12: Excretory urogram shows the typical mottled (spongelike) contrast enhancement pattern in autosomal recessive polycystic kidney disease (ARPKD).
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Excretory urogram shows the typical mottled (spon...

Excretory urogram shows the typical mottled (spongelike) contrast enhancement pattern in autosomal recessive polycystic kidney disease (ARPKD).

More on Polycystic Kidney Disease

Overview: Polycystic Kidney Disease
Differential Diagnoses & Workup: Polycystic Kidney Disease
Treatment & Medication: Polycystic Kidney Disease
Follow-up: Polycystic Kidney Disease
Multimedia: Polycystic Kidney Disease
References
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Further Reading

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Keywords

polycystic kidney disease, PKD, cystic kidney disease, genetic cystic disease, autosomal dominant polycystic kidney disease, ADPKD, adult polycystic kidney disease, autosomal recessive polycystic kidney disease, ARPKD, infantile polycystic kidney disease, medullary cystic disease, obstructive cystic disease, multicystic dysplasia, cystic dysplasia, cysts associated with systemic disease, tubular cell hyperplasia, congenital hepatic fibrosis, oligohydramnios, pulmonary hypoplasia, chronic kidney disease, acute renal failure, ARF, end-stage renal disease, hepatosplenomegaly, urinary tract infection, chronic pyelonephritis, clubfoot, renal cysts, portal hypertension, mitral valve prolapse, endocardial fibroelastosis, hyperkalemia, hyperphosphatemia, metabolic acidosis

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Contributor Information and Disclosures

Author

Priya Verghese, MD, Fellow in Pediatric Nephrology, Seattle Children's Hospital, University of Washington
Priya Verghese, MD is a member of the following medical societies: American Society of Pediatric Nephrology
Disclosure: Nothing to disclose.

Coauthor(s)

Jordan M Symons, MD, Associate Professor of Pediatrics, University of Washington School of Medicine; Dialysis Medical Director, Department of Nephrology, Children's Hospital and Regional Medical Center
Jordan M Symons, MD is a member of the following medical societies: American Society of Nephrology, American Society of Pediatric Nephrology, and Renal Physicians Association
Disclosure: Nothing to disclose.

Henrique M Lederman, MD, PhD, Consulting Staff, Department of Radiology, LeBonheur Children's Medical Center and St Jude Children's Research Hospital; Professor of Radiology and Pediatric Radiology, Chief, Division of Diagnostic Imaging in Pediatrics, Federal University of Sao Paulo, Brazil
Henrique M Lederman, MD, PhD is a member of the following medical societies: Society for Pediatric Radiology
Disclosure: Nothing to disclose.

Peter J Hurh, Research Fellow, Department of Radiology, The Children's Hospital of Philadelphia
Disclosure: Nothing to disclose.

H Jorge Baluarte, MD, Medical Director, Renal Transplant Program, Division of Nephrology, Department of Pediatrics, The Children's Hospital of Philadelphia; Professor of Pediatrics, University of Pennsylvania
H Jorge Baluarte, MD is a member of the following medical societies: American Academy of Pediatrics, American Society of Nephrology, American Society of Pediatric Nephrology, American Society of Transplantation, and International Society of Nephrology
Disclosure: Nothing to disclose.

Medical Editor

Richard Neiberger, MD, PhD, Director of Pediatric Renal Stone Disease Clinic, Associate Professor, Department of Pediatrics, Division of Nephrology, University of Florida College of Medicine and Shands Hospital
Richard Neiberger, MD, PhD is a member of the following medical societies: American Academy of Pediatrics, American Federation for Medical Research, American Medical Association, American Society of Nephrology, American Society of Pediatric Nephrology, Christian Medical & Dental Society, Florida Medical Association, International Society for Peritoneal Dialysis, International Society of Nephrology, National Kidney Foundation, New York Academy of Sciences, Shock Society, Sigma Xi, Southern Medical Association, Southern Society for Pediatric Research, and Southwest Pediatric Nephrology Study Group
Disclosure: The Osler Institute Honoraria Speaking and teaching

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from financial planner; Avanir Pharma Stock Investment from financial planner ; WebMD Salary and stock Employment and investment from financial planner

Managing Editor

Luther Travis, MD, William W Glauser Professor of Pediatrics and Pediatric Nephrology, Department of Pediatrics, Divisions of Nephrology and Diabetes, University of Texas Medical Branch and Children's Hospital
Luther Travis, MD is a member of the following medical societies: Alpha Omega Alpha, American Federation for Medical Research, International Society of Nephrology, and Texas Pediatric Society
Disclosure: Nothing to disclose.

CME Editor

Howard Trachtman, MD, Program Director, Pediatrics Research, Schneider Children's Hospital, Department of Pediatrics, Division of Nephrology, Professor, Albert Einstein College of Medicine
Howard Trachtman, MD is a member of the following medical societies: American Society of Hypertension, American Society of Nephrology, American Society of Pediatric Nephrology, and Society for Pediatric Research
Disclosure: Nothing to disclose.

Chief Editor

Craig B Langman, MD, The Isaac A Abt, MD, Professor of Kidney Diseases, Feinberg School of Medicine, Northwestern University; Division Head of Kidney Diseases, Children's Memorial Hospital, Chicago
Craig B Langman, MD is a member of the following medical societies: American Academy of Pediatrics, American Society of Nephrology, and International Society of Nephrology
Disclosure: Amgen Grant/research funds None; Altus Pharmaceuticals Grant/research funds None; Genzyme Grant/research funds None; Merck Grant/research funds None; NIH Grant/research funds None

 
 
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