eMedicine Specialties > Pediatrics: Surgery > Otolaryngology

Otosclerosis: Follow-up

Author: Peter S Roland, MD, Professor, Department of Neurological Surgery, Professor and Chairman, Department of Otolaryngology-Head and Neck Surgery, Director of Clinical Center for Auditory, Vestibular and Facial Nerve Disorders, Chief of Pediatric Otology, University of Texas Southwestern Medical Center; Adjunct Professor of Communicative Disorders, School of Human Development.
Contributor Information and Disclosures

Updated: Oct 16, 2008

Follow-up

Further Inpatient Care

  • In patients with otosclerosis, audiography should be performed on an annual basis indefinitely.

Prognosis

  • Clinical progression of the disease is unpredictable. Bilateral involvement is typical, and, in most cases, conductive hearing loss progresses until the maximal 50-60 dB loss develops.
  • Sensorineural hearing loss (SNHL) can result in total deafness, but such severe progression is uncommon.

Patient Education

Miscellaneous

Medicolegal Pitfalls

  • No unusual or unexpected areas of medicolegal exposure in otosclerosis are recognized.
  • The most likely causes of action would be failure to diagnose or failure to inform parents of treatment alternatives. In the latter context, all patients with otosclerosis and their families must recognize that hearing aids work fairly well to remediate hearing loss and that surgery, although the preferred treatment, is not the only treatment
 


More on Otosclerosis

Overview: Otosclerosis
Differential Diagnoses & Workup: Otosclerosis
Treatment & Medication: Otosclerosis
Follow-up: Otosclerosis
References

References

  1. Gordon MA. The genetics of otosclerosis: a review. Am J Otol. Nov 1989;10(6):426-38. [Medline].

  2. Ealy M, Chen W, Ryu GY, et al. Gene expression analysis of human otosclerotic stapedial footplates. Hear Res. Jun 2008;240(1-2):80-6. [Medline].

  3. Shambaugh GE Jr, Causse J. Ten years experience with fluoride in otosclerotic (otospongiotic) patients. Ann Otol Rhinol Laryngol. Sep-Oct 1974;83(5):635-42. [Medline].

  4. Shambaugh GE Jr, Petrovic A. Effects of sodium fluoride on bone. Application to otosclerosis and other decalcifying bone diseases. JAMA. Jun 10 1968;204(11):969-73. [Medline].

  5. Causse JR, Causse JB, Bretlau P, et al. Etiology of otospongiotic sensorineural losses. Am J Otol. Mar 1989;10(2):99-107. [Medline].

  6. Dornhoffer JL, Bailey HA Jr, Graham SS. Long-term hearing results following stapedotomy. Am J Otol. Sep 1994;15(5):674-8. [Medline].

  7. Hannley MT. Audiologic characteristics of the patient with otosclerosis. Otolaryngol Clin North Am. Jun 1993;26(3):373-87. [Medline].

  8. Hinojosa R, Marion M. Otosclerosis and sensorineural hearing loss: a histopathologic study. Am J Otolaryngol. Sep-Oct 1987;8(5):296-307. [Medline].

  9. Hough JV, Dyer RK Jr. Stapedectomy. Causes of failure and revision surgery in otosclerosis. Otolaryngol Clin North Am. Jun 1993;26(3):453-70. [Medline].

  10. Iurato S, Ettorre GC, Onofri M, Davidson C. Very far-advanced otosclerosis. Am J Otol. Sep 1992;13(5):482-7. [Medline].

  11. Linthicum FH Jr. Histopathology of otosclerosis. Otolaryngol Clin North Am. Jun 1993;26(3):335-52. [Medline].

  12. Rama-Lopez J, Cervera-Paz FJ, Manrique M. Cochlear implantation of patients with far-advanced otosclerosis. Otol Neurotol. Feb 2006;27(2):153-8. [Medline].

  13. Rizer FM, Lippy WH. Evolution of techniques of stapedectomy from the total stapedectomy to the small fenestra stapedectomy. Otolaryngol Clin North Am. Jun 1993;26(3):443-51. [Medline].

  14. Roland PS, Meyerhof WL. Otosclerosis. In: Head and neck Surgery-Otolaryngology. Vol 2. 1998:2083-97.

  15. Willis R. Stapedectomy--past and present. Ann Acad Med Singapore. Sep 1991;20(5):680-5. [Medline].

  16. Zehnder AF, Kristiansen AG, Adams JC, et al. Osteoprotegrin knockout mice demonstrate abnormal remodeling of the otic capsule and progressive hearing loss. Laryngoscope. Feb 2006;116(2):201-6. [Medline].

Further Reading

Keywords

otosclerosis, hearing loss, conductive hearing loss, sensorineural hearing loss, SNHL, deafness, metabolic bone disease, otic capsule, ossicles, tinnitus, disequilibrium, vertigo, otosclerotic inner ear syndrome, secondary endolymphatic hydrops, Ménière syndrome, otitis media, aural atresia, tympanosclerosis, Paget disease, osteogenesis imperfecta

Contributor Information and Disclosures

Author

Peter S Roland, MD, Professor, Department of Neurological Surgery, Professor and Chairman, Department of Otolaryngology-Head and Neck Surgery, Director of Clinical Center for Auditory, Vestibular and Facial Nerve Disorders, Chief of Pediatric Otology, University of Texas Southwestern Medical Center; Adjunct Professor of Communicative Disorders, School of Human Development.
Peter S Roland, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Otolaryngic Allergy, American Academy of Otolaryngology-Head and Neck Surgery, American Auditory Society, American Laryngological Rhinological and Otological Society, American Neurotology Society, American Otological Society, North American Skull Base Society, and Society of University Otolaryngologists-Head and Neck Surgeons
Disclosure: Alcon labs Honoraria Speaking and teaching; GSK Honoraria Speaking and teaching; Advanced Bionics Honoraria Board membership; Cochlear corp Honoraria Board membership; Med El corp travel grants Speaking and teaching; Insight vision Consulting fee Consulting

Medical Editor

Orval Brown, MD, Director of Otolaryngology Clinic, Professor, Department of Otolaryngology-Head and Neck Surgery, University of Texas Southwestern Medical Center at Dallas
Orval Brown, MD is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American Academy of Pediatrics, American Bronchoesophagological Association, American College of Surgeons, American Medical Association, American Society of Pediatric Otolaryngology, Society for Ear, Nose and Throat Advances in Children, and Society of University Otolaryngologists-Head and Neck Surgeons
Disclosure: Nothing to disclose.

Pharmacy Editor

Mary L Windle, PharmD, Adjunct Assistant Professor, University of Nebraska Medical Center College of Pharmacy, Pharmacy Editor, eMedicine
Disclosure: Pfizer Inc Stock Investment from broker recommendation; Avanir Pharma Stock Investment from broker recommendation

Managing Editor

John E McClay, MD, Assistant Professor, Department of Otolaryngology, Division of Pediatric Otolaryngology, Children's Medical Center, University of Texas Southwestern Medical School
John E McClay, MD is a member of the following medical societies: American Academy of Otolaryngic Allergy, American Academy of Otolaryngology-Head and Neck Surgery, American College of Surgeons, and American Medical Association
Disclosure: Nothing to disclose.

CME Editor

Daniel Rauch, MD, FAAP, Director, Pediatric Hospitalist Program, Associate Professor, Department of Pediatrics, New York University School of Medicine
Daniel Rauch, MD, FAAP is a member of the following medical societies: Ambulatory Pediatric Association, American Academy of Pediatrics, and Society of Hospital Medicine
Disclosure: Baxter Honoraria Consulting; Pfizer Honoraria Consulting

Chief Editor

Glenn C Isaacson, MD, FACS, FAAP, Professor of Otolaryngology-Head and Neck Surgery and Pediatrics, Temple University School of Medicine
Glenn C Isaacson, MD, FACS, FAAP is a member of the following medical societies: American Academy of Otolaryngology-Head and Neck Surgery, American Academy of Pediatrics, American Bronchoesophagological Association, American College of Surgeons, American Laryngological Rhinological and Otological Society, American Society of Pediatric Otolaryngology, and Society of University Otolaryngologists-Head and Neck Surgeons
Disclosure: Covidien Honoraria Consulting

 
 
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