Medical Care
No medical care is required for benign lymphangioendothelioma (BLAE).
Surgical Care
Once the diagnosis is established, no treatment is necessary. Solitary nodules can be excised; occasionally, local recurrence is observed. If more extensive patches and plaques are cosmetically disturbing but too large to excise, they can be treated with a laser. However, because benign lymphangioendothelioma is relatively free of blood, the usual absorption characteristics that are importance in hemangiomas and vascular malformations are less important, and an individually tailored approach with test areas is recommended.
Consultations
Because of the rarity of BLAE, many dermatopathologists or surgical pathologists may seek additional evaluation of the specimen from other pathologists. Additionally, appropriate consultations as necessary for surgical treatment.
Complications
Complications are usually only those associated with surgery and laser treatment, such as scarring and pigmentary change.
Long-Term Monitoring
Because of the histologic confusion at times between BLAE, angiosarcoma, and Kaposi sarcoma, annual follow-up to assess for recurrence is recommended.
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Erythematous nodule with macular component at the periphery.
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Overview of a histologic section from a tumor depicting dilated vascular spaces interspersed between collagen fibers and a more central accumulation of many complex vascular spaces.
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High-power view showing dilated vascular channel with innocent endothelial cells.
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High-power view showing lymphatic endothelial cells in a hematoxylin and eosin–stained section.
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High-power view showing lymphatic endothelial cells stained positively with podoplanin.
